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<meta name="keywords" content="C1800706, cryptogenic fibrosing alveolitides, cryptogenic fibrosing alveolitis, disease or syndrome, dysplasia, fibrocystic pulmonary, fibrocystic pulmonary dysplasia, fibrocystic pulmonary dysplasias, fibrosing alveolitides, cryptogenic, fibrosing alveolitis, cryptogenic, idiopathic fibrosing alveolitis, idiopathic fibrosing alveolitis, chronic form, idiopathic pulmonary fibroses, idiopathic pulmonary fibrosis, ipf, ipf - idiopathic pulmonary fibrosis, pulmonary dysplasia, fibrocystic, pulmonary fibroses, idiopathic, pulmonary fibrosis, idiopathic, autosomal dominant, autosomal recessive, birth defects, chromosomal disease, chromosome, clinical features, clinical findings, clinical genetics, clinical recommendations, clinvar, congenital chromosomal disease, consumer genetic resources, cytogenetic location, disease characteristics, disease definitions, disease descriptions, disease ontology, disease synonyms, disease vocabulary, dysmorphology, entrez, familial disease, gene, gene-disease relationship, genereviews, genetic disease, genetic disorder, genetic terminology, genetic testing registry, genetics home reference, genomic disease, gtr, hereditary disease, heritable disease, hpo, human phenotype ontology, inherited disease, management guidelines, maternal inheritance, medgen, medical genetics, medical subject headings, mesh, mitochondrial inheritance, mode of inheritance, national center for biotechnology information, national institutes of health, national library of medicine, ncbi, nih, nlm, omim, ordo, orphanet, paternal inheritance, phenome, position statements, professional practice guidelines, rare disease, reference sequence, refseq, snomed ct, syndrome, undiagnosed diseases, x-linked recessive" /><meta name="description" content="Idiopathic pulmonary fibrosis is a chronic, progressive lung disease. This condition causes scar tissue (fibrosis) to build up in the lungs, which makes the lungs unable to transport oxygen into the bloodstream effectively. The disease usually affects people between the ages of 50 and 70. Idiopathic pulmonary fibrosis belongs to a group of conditions called interstitial lung diseases (also known as ILD), which describes lung diseases that involve inflammation or scarring in the lung.\n\nThe most common signs and symptoms of idiopathic pulmonary fibrosis are shortness of breath and a persistent dry, hacking cough. Many affected individuals also experience a loss of appetite and gradual weight loss. Some people with idiopathic pulmonary fibrosis develop widened and rounded tips of the fingers and toes (clubbing) resulting from a shortage of oxygen. These features are relatively nonspecific; not everyone with these health problems has idiopathic pulmonary fibrosis. Other respiratory diseases, some of which are less serious, can cause similar signs and symptoms.\n\nIn people with idiopathic pulmonary fibrosis, scarring of the lungs increases over time until the lungs can no longer provide enough oxygen to the body's organs and tissues. Some people with idiopathic pulmonary fibrosis develop other serious lung conditions, including lung cancer, blood clots in the lungs (pulmonary emboli), pneumonia, or high blood pressure in the blood vessels that supply the lungs (pulmonary hypertension). Most affected individuals survive 3 to 5 years after their diagnosis. However, the course of the disease is highly variable; some affected people become seriously ill within a few months, while others may live with the disease for a decade or longer.\n\nIn most cases, idiopathic pulmonary fibrosis occurs in only one person in a family. These cases are described as sporadic. However, a small percentage of people with this disease have at least one other affected family member. When idiopathic pulmonary fibrosis occurs in multiple members of the same family, it is known as familial pulmonary fibrosis." /><meta name="robots" content="index,nofollow,noarchive" />
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<!--
UID=321462
ConceptID=C1800706
-->
<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Idiopathic Pulmonary Fibrosis<span class="h1sub">(IPF)</span></div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>321462</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information."><span class="highlight" style="background-color:">C1800706</span></a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div><table class="medgenTable"><tbody><tr><td>Synonyms:</td>
<td>idiopathic fibrosing alveolitis; Idiopathic fibrosing alveolitis, chronic form</td></tr>
<tr><td><span class="bold">SNOMED CT: </span></td>
<td>Idiopathic fibrosing alveolitis (700250006); Cryptogenic fibrosing alveolitis (700250006); Idiopathic pulmonary fibrosis (700250006); IPF - idiopathic pulmonary fibrosis (700250006)</td></tr>
<tr><td colspan="2" class="small"> </td></tr><tr><td>OMIM<span class="superscript">®</span>:</td>
<td><a href="https://omim.org/entry/178500" target="_blank">178500</a></td></tr>
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<div class="portlet mgSection" id="ID_100">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Definition">Definition</h1><a sid="100" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln">Idiopathic pulmonary fibrosis is a chronic, progressive lung disease. This condition causes scar tissue (fibrosis) to build up in the lungs, which makes the lungs unable to transport oxygen into the bloodstream effectively. The disease usually affects people between the ages of 50 and 70. Idiopathic pulmonary fibrosis belongs to a group of conditions called interstitial lung diseases (also known as ILD), which describes lung diseases that involve inflammation or scarring in the lung.<br /><br />The most common signs and symptoms of idiopathic pulmonary fibrosis are shortness of breath and a persistent dry, hacking cough. Many affected individuals also experience a loss of appetite and gradual weight loss. Some people with idiopathic pulmonary fibrosis develop widened and rounded tips of the fingers and toes (clubbing) resulting from a shortage of oxygen. These features are relatively nonspecific; not everyone with these health problems has idiopathic pulmonary fibrosis. Other respiratory diseases, some of which are less serious, can cause similar signs and symptoms.<br /><br />In people with idiopathic pulmonary fibrosis, scarring of the lungs increases over time until the lungs can no longer provide enough oxygen to the body's organs and tissues. Some people with idiopathic pulmonary fibrosis develop other serious lung conditions, including lung cancer, blood clots in the lungs (pulmonary emboli), pneumonia, or high blood pressure in the blood vessels that supply the lungs (pulmonary hypertension). Most affected individuals survive 3 to 5 years after their diagnosis. However, the course of the disease is highly variable; some affected people become seriously ill within a few months, while others may live with the disease for a decade or longer.<br /><br />In most cases, idiopathic pulmonary fibrosis occurs in only one person in a family. These cases are described as sporadic. However, a small percentage of people with this disease have at least one other affected family member. When idiopathic pulmonary fibrosis occurs in multiple members of the same family, it is known as familial pulmonary fibrosis. [from <a title="MedlinePlus Genetics" href="https://medlineplus.gov/genetics/" class="defSource" target="_blank">MedlinePlus Genetics</a>]</div>
</div>
<div class="portlet mgSection" id="ID_118">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test,  </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test,  </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM,  </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>,  </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar  </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="chiclet_list"><span class="chiclet Ccolor round" title="Clinical test"><a target="_blank" href="/gtr/tests/?term=C1800706[DISCUI]&amp;test_type=Clinical" ref="ncbi_uid=321462">C</a></span><span class="chiclet unavailable round" title="Research Tests">R</span><span class="chiclet Ocolor" title="OMIM"><a ref="ncbi_uid=321462" target="_blank" href="/omim/178500">O</a></span><span class="chiclet unavailable" title="GeneReviews">G</span><span class="chiclet Vcolor" title="ClinVar"><a target="_blank" href="/clinvar?LinkName=medgen_clinvar&amp;from_uid=321462" ref="ncbi_uid=321462">V</a></span></span><span class="TLline">Idiopathic Pulmonary Fibrosis</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="matched_ds">Idiopathic Pulmonary Fibrosis</span><ul><li><span class="TLline"><a href="/medgen/389939" ref="tree=MeSH" title="MedGen record for Idiopathic interstitial pneumonia">Idiopathic interstitial pneumonia</a></span><ul><li><span class="matched_ds">Idiopathic Pulmonary Fibrosis</span><ul><li><span class="TLline"><a href="/medgen/389939" ref="tree=MeSH" title="MedGen record for Idiopathic interstitial pneumonia">Idiopathic interstitial pneumonia</a></span><ul><li><span class="matched_ds">Idiopathic Pulmonary Fibrosis</span><ul><li><span class="TLline"><a href="/medgen/389939" ref="tree=MeSH" title="MedGen record for Idiopathic interstitial pneumonia">Idiopathic interstitial pneumonia</a></span><ul><li><span class="matched_ds">Idiopathic Pulmonary Fibrosis</span><ul><li><span class="TLline"><a href="/medgen/39340" ref="tree=MeSH" title="MedGen record for Acute interstitial pneumonia">Acute interstitial pneumonia</a></span></li><li><span class="TLline"><a href="/medgen/389939" ref="tree=MeSH" title="MedGen record for Idiopathic interstitial pneumonia">Idiopathic interstitial pneumonia</a></span><ul><li><span class="TLline"><a href="/medgen/116663" ref="tree=MeSH" title="MedGen record for Bronchiolitis obliterans organizing pneumonia">Bronchiolitis obliterans organizing pneumonia</a></span></li><li><span class="TLline"><a href="/medgen/838971" ref="tree=MeSH" title="MedGen record for Combined pulmonary fibrosis-emphysema syndrome">Combined pulmonary fibrosis-emphysema syndrome</a></span></li><li><span class="TLline"><a href="/medgen/65962" ref="tree=MeSH" title="MedGen record for Desquamative interstitial pneumonia">Desquamative interstitial pneumonia</a></span></li><li><span class="TLline"><a href="/medgen/1798890" ref="tree=MeSH" title="MedGen record for Idiopathic pleuroparenchymal fibroelastosis">Idiopathic pleuroparenchymal fibroelastosis</a></span></li><li><span class="TLline"><a href="/medgen/1794136" ref="tree=MeSH" title="MedGen record for Interstitial lung disease 2">Interstitial lung disease 2</a></span></li><li><span class="TLline"><a href="/medgen/82682" ref="tree=MeSH" title="MedGen record for Lymphoid interstitial pneumonia">Lymphoid interstitial pneumonia</a></span></li><li><span class="TLline"><a href="/medgen/220936" ref="tree=MeSH" title="MedGen record for Non-specific interstitial pneumonia">Non-specific interstitial pneumonia</a></span><ul><li><span class="TLline"><a href="/medgen/1782036" ref="tree=MeSH" title="MedGen record for Cellular non-specific interstitial pneumonia">Cellular non-specific interstitial pneumonia</a></span></li><li><span class="TLline"><a href="/medgen/1786141" ref="tree=MeSH" title="MedGen record for Fibrotic non-specific interstitial pneumonia">Fibrotic non-specific interstitial pneumonia</a></span></li></ul></li><li><span class="TLline"><a href="/medgen/1672485" ref="tree=MeSH" title="MedGen record for Respiratory bronchiolitis-interstitial lung disease syndrome">Respiratory bronchiolitis-interstitial lung disease syndrome</a></span></li><li><span class="TLline"><a href="/medgen/1662563" ref="tree=MeSH" title="MedGen record for Usual interstitial pneumonia">Usual interstitial pneumonia</a></span></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
</div>
<div class="portlet mgSection" id="ID_105">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
<div class="nl"><a target="_blank" href="/pubmed/35486072">Idiopathic Pulmonary Fibrosis (an Update) and Progressive Pulmonary Fibrosis in Adults: An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Raghu G,
Remy-Jardin M,
Richeldi L,
Thomson CC,
Inoue Y,
Johkoh T,
Kreuter M,
Lynch DA,
Maher TM,
Martinez FJ,
Molina-Molina M,
Myers JL,
Nicholson AG,
Ryerson CJ,
Strek ME,
Troy LK,
Wijsenbeek M,
Mammen MJ,
Hossain T,
Bissell BD,
Herman DD,
Hon SM,
Kheir F,
Khor YH,
Macrea M,
Antoniou KM,
Bouros D,
Buendia-Roldan I,
Caro F,
Crestani B,
Ho L,
Morisset J,
Olson AL,
Podolanczuk A,
Poletti V,
Selman M,
Ewing T,
Jones S,
Knight SL,
Ghazipura M,
Wilson KC</span><br />
<span class="medgenPMjournal">Am J Respir Crit Care Med</span>
2022 May 1;205(9):e18-e47.
doi: 10.1164/rccm.202202-0399ST.
<span class="bold">PMID: </span><a href="/pubmed/35486072" target="_blank">35486072</a><a href="/pmc/articles/PMC9851481" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/35001525">Idiopathic pulmonary fibrosis: Current and future treatment.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Glass DS,
Grossfeld D,
Renna HA,
Agarwala P,
Spiegler P,
DeLeon J,
Reiss AB</span><br />
<span class="medgenPMjournal">Clin Respir J</span>
2022 Feb;16(2):84-96.
Epub 2022 Jan 10
doi: 10.1111/crj.13466.
<span class="bold">PMID: </span><a href="/pubmed/35001525" target="_blank">35001525</a><a href="/pmc/articles/PMC9060042" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/29154106">Diagnostic criteria for idiopathic pulmonary fibrosis: a Fleischner Society White Paper.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Lynch DA,
Sverzellati N,
Travis WD,
Brown KK,
Colby TV,
Galvin JR,
Goldin JG,
Hansell DM,
Inoue Y,
Johkoh T,
Nicholson AG,
Knight SL,
Raoof S,
Richeldi L,
Ryerson CJ,
Ryu JH,
Wells AU</span><br />
<span class="medgenPMjournal">Lancet Respir Med</span>
2018 Feb;6(2):138-153.
Epub 2017 Nov 15
doi: 10.1016/S2213-2600(17)30433-2.
<span class="bold">PMID: </span><a href="/pubmed/29154106" target="_blank">29154106</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(%22idiopathic%20pulmonary%20fibrosis%22%5Btiab%3A~0%5D)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (627)</a></div></div>
</div>
<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
<div class="portlet mgSection" id="ID_103">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
<div class="nl"><a target="_blank" href="/pubmed/35659420">Idiopathic pulmonary fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">León-Román F,
Valenzuela C,
Molina-Molina M</span><br />
<span class="medgenPMjournal">Med Clin (Barc)</span>
2022 Aug 26;159(4):189-194.
Epub 2022 Jun 1
doi: 10.1016/j.medcli.2022.02.020.
<span class="bold">PMID: </span><a href="/pubmed/35659420" target="_blank">35659420</a></div>
<div class="nl"><a target="_blank" href="/pubmed/35354649">Impact of antifibrotic therapy on lung cancer development in idiopathic pulmonary fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Naoi H,
Suzuki Y,
Mori K,
Aono Y,
Kono M,
Hasegawa H,
Yokomura K,
Inoue Y,
Hozumi H,
Karayama M,
Furuhashi K,
Enomoto N,
Fujisawa T,
Nakamura Y,
Inui N,
Nakamura H,
Suda T</span><br />
<span class="medgenPMjournal">Thorax</span>
2022 Jul;77(7):727-730.
Epub 2022 Mar 30
doi: 10.1136/thoraxjnl-2021-218281.
<span class="bold">PMID: </span><a href="/pubmed/35354649" target="_blank">35354649</a></div>
<div class="nl"><a target="_blank" href="/pubmed/29742380">Idiopathic Pulmonary Fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Lederer DJ,
Martinez FJ</span><br />
<span class="medgenPMjournal">N Engl J Med</span>
2018 May 10;378(19):1811-1823.
doi: 10.1056/NEJMra1705751.
<span class="bold">PMID: </span><a href="/pubmed/29742380" target="_blank">29742380</a></div>
<div class="nl"><a target="_blank" href="/pubmed/29471816">Idiopathic pulmonary fibrosis: pathogenesis and management.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Sgalla G,
Iovene B,
Calvello M,
Ori M,
Varone F,
Richeldi L</span><br />
<span class="medgenPMjournal">Respir Res</span>
2018 Feb 22;19(1):32.
doi: 10.1186/s12931-018-0730-2.
<span class="bold">PMID: </span><a href="/pubmed/29471816" target="_blank">29471816</a><a href="/pmc/articles/PMC5824456" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/27299520">Acute Exacerbation of Idiopathic Pulmonary Fibrosis. An International Working Group Report.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Collard HR,
Ryerson CJ,
Corte TJ,
Jenkins G,
Kondoh Y,
Lederer DJ,
Lee JS,
Maher TM,
Wells AU,
Antoniou KM,
Behr J,
Brown KK,
Cottin V,
Flaherty KR,
Fukuoka J,
Hansell DM,
Johkoh T,
Kaminski N,
Kim DS,
Kolb M,
Lynch DA,
Myers JL,
Raghu G,
Richeldi L,
Taniguchi H,
Martinez FJ</span><br />
<span class="medgenPMjournal">Am J Respir Crit Care Med</span>
2016 Aug 1;194(3):265-75.
doi: 10.1164/rccm.201604-0801CI.
<span class="bold">PMID: </span><a href="/pubmed/27299520" target="_blank">27299520</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Idiopathic%20Pulmonary%20Fibrosis%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (4300)</a></div><h3 class="subhead">Diagnosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/37556670">Idiopathic pulmonary fibrosis: current diagnosis and treatment.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Amaral AF,
Colares PFB,
Kairalla RA</span><br />
<span class="medgenPMjournal">J Bras Pneumol</span>
2023;49(4):e20230085.
Epub 2023 Aug 7
doi: 10.36416/1806-3756/e20230085.
<span class="bold">PMID: </span><a href="/pubmed/37556670" target="_blank">37556670</a><a href="/pmc/articles/PMC10578906" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/36737162">Idiopathic pulmonary fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Benegas Urteaga M,
Ramírez Ruz J,
Sánchez González M</span><br />
<span class="medgenPMjournal">Radiologia (Engl Ed)</span>
2022 Dec;64 Suppl 3:227-239.
doi: 10.1016/j.rxeng.2022.10.009.
<span class="bold">PMID: </span><a href="/pubmed/36737162" target="_blank">36737162</a></div>
<div class="nl"><a target="_blank" href="/pubmed/35001525">Idiopathic pulmonary fibrosis: Current and future treatment.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Glass DS,
Grossfeld D,
Renna HA,
Agarwala P,
Spiegler P,
DeLeon J,
Reiss AB</span><br />
<span class="medgenPMjournal">Clin Respir J</span>
2022 Feb;16(2):84-96.
Epub 2022 Jan 10
doi: 10.1111/crj.13466.
<span class="bold">PMID: </span><a href="/pubmed/35001525" target="_blank">35001525</a><a href="/pmc/articles/PMC9060042" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/29742380">Idiopathic Pulmonary Fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Lederer DJ,
Martinez FJ</span><br />
<span class="medgenPMjournal">N Engl J Med</span>
2018 May 10;378(19):1811-1823.
doi: 10.1056/NEJMra1705751.
<span class="bold">PMID: </span><a href="/pubmed/29742380" target="_blank">29742380</a></div>
<div class="nl"><a target="_blank" href="/pubmed/28365056">Idiopathic pulmonary fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Richeldi L,
Collard HR,
Jones MG</span><br />
<span class="medgenPMjournal">Lancet</span>
2017 May 13;389(10082):1941-1952.
Epub 2017 Mar 30
doi: 10.1016/S0140-6736(17)30866-8.
<span class="bold">PMID: </span><a href="/pubmed/28365056" target="_blank">28365056</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Idiopathic%20Pulmonary%20Fibrosis%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (3901)</a></div><h3 class="subhead">Therapy</h3>
<div class="nl"><a target="_blank" href="/pubmed/35001525">Idiopathic pulmonary fibrosis: Current and future treatment.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Glass DS,
Grossfeld D,
Renna HA,
Agarwala P,
Spiegler P,
DeLeon J,
Reiss AB</span><br />
<span class="medgenPMjournal">Clin Respir J</span>
2022 Feb;16(2):84-96.
Epub 2022 Jan 10
doi: 10.1111/crj.13466.
<span class="bold">PMID: </span><a href="/pubmed/35001525" target="_blank">35001525</a><a href="/pmc/articles/PMC9060042" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/31996266">Progression of fibrosing interstitial lung disease.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Wong AW,
Ryerson CJ,
Guler SA</span><br />
<span class="medgenPMjournal">Respir Res</span>
2020 Jan 29;21(1):32.
doi: 10.1186/s12931-020-1296-3.
<span class="bold">PMID: </span><a href="/pubmed/31996266" target="_blank">31996266</a><a href="/pmc/articles/PMC6988233" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30704705">Inflammation and immunity in IPF pathogenesis and treatment.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Heukels P,
Moor CC,
von der Thüsen JH,
Wijsenbeek MS,
Kool M</span><br />
<span class="medgenPMjournal">Respir Med</span>
2019 Feb;147:79-91.
Epub 2019 Jan 9
doi: 10.1016/j.rmed.2018.12.015.
<span class="bold">PMID: </span><a href="/pubmed/30704705" target="_blank">30704705</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30616998">Senolytics in idiopathic pulmonary fibrosis: Results from a first-in-human, open-label, pilot study.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Justice JN,
Nambiar AM,
Tchkonia T,
LeBrasseur NK,
Pascual R,
Hashmi SK,
Prata L,
Masternak MM,
Kritchevsky SB,
Musi N,
Kirkland JL</span><br />
<span class="medgenPMjournal">EBioMedicine</span>
2019 Feb;40:554-563.
Epub 2019 Jan 5
doi: 10.1016/j.ebiom.2018.12.052.
<span class="bold">PMID: </span><a href="/pubmed/30616998" target="_blank">30616998</a><a href="/pmc/articles/PMC6412088" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/25745043">Mode of action of nintedanib in the treatment of idiopathic pulmonary fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Wollin L,
Wex E,
Pautsch A,
Schnapp G,
Hostettler KE,
Stowasser S,
Kolb M</span><br />
<span class="medgenPMjournal">Eur Respir J</span>
2015 May;45(5):1434-45.
Epub 2015 Mar 5
doi: 10.1183/09031936.00174914.
<span class="bold">PMID: </span><a href="/pubmed/25745043" target="_blank">25745043</a><a href="/pmc/articles/PMC4416110" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Idiopathic%20Pulmonary%20Fibrosis%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (3011)</a></div><h3 class="subhead">Prognosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/35354649">Impact of antifibrotic therapy on lung cancer development in idiopathic pulmonary fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Naoi H,
Suzuki Y,
Mori K,
Aono Y,
Kono M,
Hasegawa H,
Yokomura K,
Inoue Y,
Hozumi H,
Karayama M,
Furuhashi K,
Enomoto N,
Fujisawa T,
Nakamura Y,
Inui N,
Nakamura H,
Suda T</span><br />
<span class="medgenPMjournal">Thorax</span>
2022 Jul;77(7):727-730.
Epub 2022 Mar 30
doi: 10.1136/thoraxjnl-2021-218281.
<span class="bold">PMID: </span><a href="/pubmed/35354649" target="_blank">35354649</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34895203">Efficacy of antifibrotic drugs, nintedanib and pirfenidone, in treatment of progressive pulmonary fibrosis in both idiopathic pulmonary fibrosis (IPF) and non-IPF: a systematic review and meta-analysis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Finnerty JP,
Ponnuswamy A,
Dutta P,
Abdelaziz A,
Kamil H</span><br />
<span class="medgenPMjournal">BMC Pulm Med</span>
2021 Dec 11;21(1):411.
doi: 10.1186/s12890-021-01783-1.
<span class="bold">PMID: </span><a href="/pubmed/34895203" target="_blank">34895203</a><a href="/pmc/articles/PMC8666028" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34233665">Global incidence and prevalence of idiopathic pulmonary fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Maher TM,
Bendstrup E,
Dron L,
Langley J,
Smith G,
Khalid JM,
Patel H,
Kreuter M</span><br />
<span class="medgenPMjournal">Respir Res</span>
2021 Jul 7;22(1):197.
doi: 10.1186/s12931-021-01791-z.
<span class="bold">PMID: </span><a href="/pubmed/34233665" target="_blank">34233665</a><a href="/pmc/articles/PMC8261998" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/31689414">Six-Minute Walk Test: Clinical Role, Technique, Coding, and Reimbursement.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Agarwala P,
Salzman SH</span><br />
<span class="medgenPMjournal">Chest</span>
2020 Mar;157(3):603-611.
Epub 2019 Nov 2
doi: 10.1016/j.chest.2019.10.014.
<span class="bold">PMID: </span><a href="/pubmed/31689414" target="_blank">31689414</a><a href="/pmc/articles/PMC7609960" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/25976683">Global incidence and mortality of idiopathic pulmonary fibrosis: a systematic review.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Hutchinson J,
Fogarty A,
Hubbard R,
McKeever T</span><br />
<span class="medgenPMjournal">Eur Respir J</span>
2015 Sep;46(3):795-806.
Epub 2015 May 14
doi: 10.1183/09031936.00185114.
<span class="bold">PMID: </span><a href="/pubmed/25976683" target="_blank">25976683</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Idiopathic%20Pulmonary%20Fibrosis%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (3665)</a></div><h3 class="subhead">Clinical prediction guides</h3>
<div class="nl"><a target="_blank" href="/pubmed/34675050">Biomarker signatures for progressive idiopathic pulmonary fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Clynick B,
Corte TJ,
Jo HE,
Stewart I,
Glaspole IN,
Grainge C,
Maher TM,
Navaratnam V,
Hubbard R,
Hopkins PMA,
Reynolds PN,
Chapman S,
Zappala C,
Keir GJ,
Cooper WA,
Mahar AM,
Ellis S,
Goh NS,
De Jong E,
Cha L,
Tan DBA,
Leigh L,
Oldmeadow C,
Walters EH,
Jenkins RG,
Moodley Y</span><br />
<span class="medgenPMjournal">Eur Respir J</span>
2022 Mar;59(3)
Epub 2022 Mar 31
doi: 10.1183/13993003.01181-2021.
<span class="bold">PMID: </span><a href="/pubmed/34675050" target="_blank">34675050</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30578335">Presentation, diagnosis and clinical course of the spectrum of progressive-fibrosing interstitial lung diseases.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Cottin V,
Hirani NA,
Hotchkin DL,
Nambiar AM,
Ogura T,
Otaola M,
Skowasch D,
Park JS,
Poonyagariyagorn HK,
Wuyts W,
Wells AU</span><br />
<span class="medgenPMjournal">Eur Respir Rev</span>
2018 Dec 31;27(150)
Epub 2018 Dec 21
doi: 10.1183/16000617.0076-2018.
<span class="bold">PMID: </span><a href="/pubmed/30578335" target="_blank">30578335</a><a href="/pmc/articles/PMC9489068" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/24591661">Interstitial lung disease.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Antoniou KM,
Margaritopoulos GA,
Tomassetti S,
Bonella F,
Costabel U,
Poletti V</span><br />
<span class="medgenPMjournal">Eur Respir Rev</span>
2014 Mar 1;23(131):40-54.
doi: 10.1183/09059180.00009113.
<span class="bold">PMID: </span><a href="/pubmed/24591661" target="_blank">24591661</a><a href="/pmc/articles/PMC9487254" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/23728863">Idiopathic pulmonary fibrosis: current challenges and future perspectives.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Richeldi L</span><br />
<span class="medgenPMjournal">Eur Respir Rev</span>
2013 Jun 1;22(128):103-5.
doi: 10.1183/09059180.00001413.
<span class="bold">PMID: </span><a href="/pubmed/23728863" target="_blank">23728863</a><a href="/pmc/articles/PMC9487390" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/22586007">A multidimensional index and staging system for idiopathic pulmonary fibrosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Ley B,
Ryerson CJ,
Vittinghoff E,
Ryu JH,
Tomassetti S,
Lee JS,
Poletti V,
Buccioli M,
Elicker BM,
Jones KD,
King TE Jr,
Collard HR</span><br />
<span class="medgenPMjournal">Ann Intern Med</span>
2012 May 15;156(10):684-91.
doi: 10.7326/0003-4819-156-10-201205150-00004.
<span class="bold">PMID: </span><a href="/pubmed/22586007" target="_blank">22586007</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Idiopathic%20Pulmonary%20Fibrosis%22%20AND%20Clinical%20prediction%20guides%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (3583)</a></div></div>
</div>
<div class="portlet mgSection" id="ID_104">
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<div class="nl"><a target="_blank" href="/pubmed/36476129">The Human Respiratory Microbiome: Current Understandings and Future Directions.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Zhao L,
Luo JL,
Ali MK,
Spiekerkoetter E,
Nicolls MR</span><br />
<span class="medgenPMjournal">Am J Respir Cell Mol Biol</span>
2023 Mar;68(3):245-255.
doi: 10.1165/rcmb.2022-0208TR.
<span class="bold">PMID: </span><a href="/pubmed/36476129" target="_blank">36476129</a><a href="/pmc/articles/PMC9989478" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/35145039">Medical treatments for idiopathic pulmonary fibrosis: a systematic review and network meta-analysis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Pitre T,
Mah J,
Helmeczi W,
Khalid MF,
Cui S,
Zhang M,
Husnudinov R,
Su J,
Banfield L,
Guy B,
Coyne J,
Scallan C,
Kolb MR,
Jones A,
Zeraatkar D</span><br />
<span class="medgenPMjournal">Thorax</span>
2022 Dec;77(12):1243-1250.
Epub 2022 Feb 10
doi: 10.1136/thoraxjnl-2021-217976.
<span class="bold">PMID: </span><a href="/pubmed/35145039" target="_blank">35145039</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34895203">Efficacy of antifibrotic drugs, nintedanib and pirfenidone, in treatment of progressive pulmonary fibrosis in both idiopathic pulmonary fibrosis (IPF) and non-IPF: a systematic review and meta-analysis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Finnerty JP,
Ponnuswamy A,
Dutta P,
Abdelaziz A,
Kamil H</span><br />
<span class="medgenPMjournal">BMC Pulm Med</span>
2021 Dec 11;21(1):411.
doi: 10.1186/s12890-021-01783-1.
<span class="bold">PMID: </span><a href="/pubmed/34895203" target="_blank">34895203</a><a href="/pmc/articles/PMC8666028" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34559419">Pulmonary rehabilitation for interstitial lung disease.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Dowman L,
Hill CJ,
May A,
Holland AE</span><br />
<span class="medgenPMjournal">Cochrane Database Syst Rev</span>
2021 Feb 1;2(2):CD006322.
doi: 10.1002/14651858.CD006322.pub4.
<span class="bold">PMID: </span><a href="/pubmed/34559419" target="_blank">34559419</a><a href="/pmc/articles/PMC8094410" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/25976683">Global incidence and mortality of idiopathic pulmonary fibrosis: a systematic review.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Hutchinson J,
Fogarty A,
Hubbard R,
McKeever T</span><br />
<span class="medgenPMjournal">Eur Respir J</span>
2015 Sep;46(3):795-806.
Epub 2015 May 14
doi: 10.1183/09031936.00185114.
<span class="bold">PMID: </span><a href="/pubmed/25976683" target="_blank">25976683</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Idiopathic%20Pulmonary%20Fibrosis%22%20AND%20systematic%5Bsb%5D%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (168)</a></div></div>
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<div class="portlet_content ln"><ul><li><a href="/gtr/tests?term=C1800706%5bDISCUI%5d&amp;filter=method%3A2%5F7" target="_blank">Sequence analysis of the entire coding region (2)</a></li>
<li class="portletSeeAll portletSeeAllPad"><total><a href="/gtr/tests?term=C1800706%5bDISCUI%5d" target="_blank">See all (2)</a></total></li>
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<div class="portlet_content ln"><ul><li><a href="https://clinicaltrials.gov/search?cond=Idiopathic%20Pulmonary%20Fibrosis" target="_blank">ClinicalTrials.gov</a></li></ul></div>
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<div class="portlet_content ln"><ul class="a_poppers"><li><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(%22idiopathic%20pulmonary%20fibrosis%22%5Btiab%3A~0%5D)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">PubMed</a><div class="help-popup">See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div></li><li><a target="_blank" href="/books/?term=((%22clinical%20guidelines%22%5BResource%20Type%5D)%20OR%20%22practice%20guideline%22%5BPublication%20Type%5D)%20AND%20(%22Idiopathic%20Pulmonary%20Fibrosis%22)">Bookshelf</a><div class="help-popup">See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div></li></ul></div>
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