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<!--
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UID=871105
|
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ConceptID=C4025570
|
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-->
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<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Hypoplasia of lymphatic vessels</div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>871105</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C4025570</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Congenital Abnormality</dd></dl></div></div><table class="medgenTable"><tbody><tr><td>Synonym:</td>
|
||
<td>Underdeveloped lymphatic vessels</td></tr>
|
||
<tr><td colspan="2" class="small"> </td></tr><tr><td>HPO:</td>
|
||
<td><a target="_blank" title="Human Phenotype Ontology" href="https://hpo.jax.org/app/browse/term/HP:0003759">HP:0003759</a></td></tr>
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</tbody></table></div><div class="rprt-body jig-ncbiinpagenav" data-jigconfig="smoothScroll: false, gotoTopLink: true, gotoTopLinkText: '', gotoTopLinkAttrs: {'title': 'Go to the top of the page'},allHeadingLevels: ['h1'], topOfPageTOC: true, tocId: 'my-toc'"><div id="rprt-tabs-1" class="rprt-tab"><div id="tb-termsProp-1"><div class="leftCol mgCol"><div>
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<div class="portlet mgSection" id="ID_100">
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Definition">Definition</h1><a sid="100" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln">Congenital underdevelopment of lymph vessels. [from <a title="Human Phenotype Ontology" href="http://www.human-phenotype-ontology.org" class="defSource" target="_blank">HPO</a>]</div>
|
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</div>
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||
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<div class="portlet mgSection" id="ID_118">
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
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<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test, </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test, </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM, </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>, </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="chiclet_list"><span class="chiclet unavailable round" title="Clinical test">C</span><span class="chiclet unavailable round" title="Research Tests">R</span><span class="chiclet unavailable" title="OMIM">O</span><span class="chiclet unavailable" title="GeneReviews">G</span><span class="chiclet unavailable" title="ClinVar">V</span></span><span class="TLline">Hypoplasia of lymphatic vessels</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="TLline"><a href="/medgen/867443" ref="tree=MeSH" title="MedGen record for Phenotypic abnormality">Phenotypic abnormality</a></span><ul><li><span class="TLline"><a href="/medgen/867388" ref="tree=MeSH" title="MedGen record for Abnormality of the immune system">Abnormality of the immune system</a></span><ul><li><span class="TLline"><a href="/medgen/892707" ref="tree=MeSH" title="MedGen record for Abnormality of the lymphatic system">Abnormality of the lymphatic system</a></span><ul><li><span class="TLline"><a href="/medgen/867589" ref="tree=MeSH" title="MedGen record for Abnormal lymphatic vessel morphology">Abnormal lymphatic vessel morphology</a></span><ul><li><span class="matched_ds">Hypoplasia of lymphatic vessels</span></li></ul></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_112">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Conditions_with_this_feature">Conditions with this feature</h1><a sid="112" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln clinfeat">
|
||
<div class="divPopper rprt" id="rdis_113164"><div><strong>Yellow nail syndrome</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>113164</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C0221348</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Yellow nail syndrome (YNS) is classically considered to comprise a clinical triad of yellow nails, lymphedema, and respiratory tract involvement. Two of these symptoms are required for the diagnosis, since the complete triad is only observed in about one-third of patients. Onset is usually after puberty (Hoque et al., 2007).</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/113164">Condition Record</a></div></div>
|
||
<div class="divPopper rprt" id="rdis_309963"><div><strong>Hereditary lymphedema type I</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>309963</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information."><span class="highlight" style="background-color:">C1704423</span></a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Primary lymphedema is caused by anatomic or functional defects in the lymphatic system, resulting in chronic swelling of body parts. There may be accompanying nail and skin changes, such as nail dysplasia or papillomatosis. Onset is usually at birth or in early childhood but can occur later, and the severity is variable (summary by Gordon et al., 2013 and Balboa-Beltran et al., 2014). Genetic Heterogeneity of Lymphatic Malformation Primary lymphedema is genetically heterogeneous: see also LMPHM2 (611944), which maps to chromosome 6q16.2-q22.1; LMPHM3 (613480), caused by mutation in the GJC2 gene (608803) on chromosome 1q42; LMPHM4 (615907), caused by mutation in the VEGFC gene (601528) on chromosome 4q34; LMPHM5 (153200); LMPHM6 (616843), caused by mutation in the PIEZO1 gene (611184) on chromosome 16q24; LMPHM7 (617300), caused by mutation in the EPHB4 gene (600011) on chromosome 7q22; LMPHM8 (618773), caused by mutation in the CALCRL gene (114190) on chromosome 2q31; LMPHM9 (619319), caused by mutation in the CELSR1 gene (604523) on chromosome 22q13; LMPHM10 (610369), caused by mutation in the ANGPT2 gene (601922) on chromosome 8p23; LMPHM11 (619401), caused by mutation in the TIE1 gene (600222) on chromosome 1p34; LMPHM12 (620014), caused by mutation in the MDFIC gene (614511) on chromosome 7q31; LMPHM13 (620244), caused by mutation in the THSD1 gene (616821) on chromosome 13q14; and LMPHM14 (620602), caused by mutation in the ERG gene (165080) on chromosome 21q22. Lymphedema can also be a feature of syndromic disorders such as lymphedema-distichiasis syndrome (153400), which is caused by mutation in the FOXC2 gene (602402), and various forms of nonimmune hydrops fetalis (NIHF; see 236750).</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/309963">Condition Record</a></div></div>
|
||
<div class="divPopper rprt" id="rdis_1648463"><div><strong>Lymphedema praecox</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>1648463</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C4746631</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Primary lymphedema is caused by anatomic or functional defects in the lymphatic system, resulting in chronic swelling of body parts. There may be accompanying nail and skin changes, such as nail dysplasia or papillomatosis. Onset is usually at birth or in early childhood but can occur later, and the severity is variable (summary by Gordon et al., 2013 and Balboa-Beltran et al., 2014). For a discussion of the genetic heterogeneity of lymphocytic malformation, see 153100.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/1648463">Condition Record</a></div></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_309963" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Hereditary lymphedema type I</a></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_1648463" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Lymphedema praecox</a></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_113164" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Yellow nail syndrome</a></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_105">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/35430156">Management of a neonatal giant lymphatic malformations with dyspnea.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Chen H,
|
||
Ren C,
|
||
Zhang L,
|
||
Zhong Y</span><br />
|
||
<span class="medgenPMjournal">Asian J Surg</span>
|
||
2022 Oct;45(10):1910-1911.
|
||
Epub 2022 Apr 13
|
||
doi: 10.1016/j.asjsur.2022.03.135.
|
||
<span class="bold">PMID: </span><a href="/pubmed/35430156" target="_blank">35430156</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27097138">Evidence-Based Management of Vascular Malformations.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Morgan P,
|
||
Keller R,
|
||
Patel K</span><br />
|
||
<span class="medgenPMjournal">Facial Plast Surg</span>
|
||
2016 Apr;32(2):162-76.
|
||
Epub 2016 Apr 20
|
||
doi: 10.1055/s-0036-1581141.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27097138" target="_blank">27097138</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/21742796">Normalization of the vasculature for treatment of cancer and other diseases.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Goel S,
|
||
Duda DG,
|
||
Xu L,
|
||
Munn LL,
|
||
Boucher Y,
|
||
Fukumura D,
|
||
Jain RK</span><br />
|
||
<span class="medgenPMjournal">Physiol Rev</span>
|
||
2011 Jul;91(3):1071-121.
|
||
doi: 10.1152/physrev.00038.2010.
|
||
<span class="bold">PMID: </span><a href="/pubmed/21742796" target="_blank">21742796</a><a href="/pmc/articles/PMC3258432" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(hypoplasia%20of%20lymphatic%20vessels)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (34)</a></div></div>
|
||
</div>
|
||
<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
|
||
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
|
||
<div class="portlet mgSection" id="ID_103">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/39445428">Radiation-Induced Macrovessel/Microvessel Disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Abe JI,
|
||
Allen BG,
|
||
Beyer AM,
|
||
Lewandowski D,
|
||
Mapuskar KA,
|
||
Subramanian V,
|
||
Tamplin MR,
|
||
Grumbach IM</span><br />
|
||
<span class="medgenPMjournal">Arterioscler Thromb Vasc Biol</span>
|
||
2024 Dec;44(12):2407-2415.
|
||
Epub 2024 Oct 24
|
||
doi: 10.1161/ATVBAHA.124.319866.
|
||
<span class="bold">PMID: </span><a href="/pubmed/39445428" target="_blank">39445428</a><a href="/pmc/articles/PMC11842029" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/35778409">MR lymphangiography of lymphatic abnormalities in children and adults with Noonan syndrome.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Pieper CC,
|
||
Wagenpfeil J,
|
||
Henkel A,
|
||
Geiger S,
|
||
Köster T,
|
||
Hoss K,
|
||
Luetkens JA,
|
||
Hart C,
|
||
Attenberger UI,
|
||
Müller A</span><br />
|
||
<span class="medgenPMjournal">Sci Rep</span>
|
||
2022 Jul 1;12(1):11164.
|
||
doi: 10.1038/s41598-022-13806-w.
|
||
<span class="bold">PMID: </span><a href="/pubmed/35778409" target="_blank">35778409</a><a href="/pmc/articles/PMC9249771" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/34166069">Vascular and Lymphatic Malformations: Perspectives From Human and Vertebrate Studies.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Janardhan HP,
|
||
Saheera S,
|
||
Jung R,
|
||
Trivedi CM</span><br />
|
||
<span class="medgenPMjournal">Circ Res</span>
|
||
2021 Jun 25;129(1):131-135.
|
||
Epub 2021 Jun 24
|
||
doi: 10.1161/CIRCRESAHA.121.319587.
|
||
<span class="bold">PMID: </span><a href="/pubmed/34166069" target="_blank">34166069</a><a href="/pmc/articles/PMC8238353" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/33504714">Visualization of Lymphatic Vessels Using Photoacoustic Imaging.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Kajita H,
|
||
Suzuki Y,
|
||
Sakuma H,
|
||
Imanishi N,
|
||
Tsuji T,
|
||
Jinzaki M,
|
||
Aiso S,
|
||
Kishi K</span><br />
|
||
<span class="medgenPMjournal">Keio J Med</span>
|
||
2021 Dec 25;70(4):82-92.
|
||
Epub 2021 Jan 28
|
||
doi: 10.2302/kjm.2020-0010-OA.
|
||
<span class="bold">PMID: </span><a href="/pubmed/33504714" target="_blank">33504714</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/33493408">Lymphatic and Mixed Malformations.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Hathaway BA,
|
||
Radu S,
|
||
Wilson J,
|
||
Nauta AC</span><br />
|
||
<span class="medgenPMjournal">Lymphat Res Biol</span>
|
||
2021 Feb;19(1):41-50.
|
||
Epub 2021 Jan 25
|
||
doi: 10.1089/lrb.2020.0100.
|
||
<span class="bold">PMID: </span><a href="/pubmed/33493408" target="_blank">33493408</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hypoplasia%20of%20lymphatic%20vessels%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (163)</a></div><h3 class="subhead">Diagnosis</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/32471546">Imaging of Vascular Malformations.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Hussein A,
|
||
Malguria N</span><br />
|
||
<span class="medgenPMjournal">Radiol Clin North Am</span>
|
||
2020 Jul;58(4):815-830.
|
||
Epub 2020 Apr 23
|
||
doi: 10.1016/j.rcl.2020.02.003.
|
||
<span class="bold">PMID: </span><a href="/pubmed/32471546" target="_blank">32471546</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27514587">Plastic Bronchitis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Rubin BK</span><br />
|
||
<span class="medgenPMjournal">Clin Chest Med</span>
|
||
2016 Sep;37(3):405-8.
|
||
Epub 2016 Jun 15
|
||
doi: 10.1016/j.ccm.2016.04.003.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27514587" target="_blank">27514587</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/17325083">Slow-flow vascular malformations.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Wirth GA,
|
||
Sundine MJ</span><br />
|
||
<span class="medgenPMjournal">Clin Pediatr (Phila)</span>
|
||
2007 Mar;46(2):109-20.
|
||
doi: 10.1177/0009922806289788.
|
||
<span class="bold">PMID: </span><a href="/pubmed/17325083" target="_blank">17325083</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/15609924">Lymphatic malformations.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Smith RJ</span><br />
|
||
<span class="medgenPMjournal">Lymphat Res Biol</span>
|
||
2004;2(1):25-31.
|
||
doi: 10.1089/1539685041690436.
|
||
<span class="bold">PMID: </span><a href="/pubmed/15609924" target="_blank">15609924</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/14206637">FETAL HYDROTHORAX.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">BORNHURST RA,
|
||
CARSKY EW</span><br />
|
||
<span class="medgenPMjournal">Radiology</span>
|
||
1964 Sep;83:476-9.
|
||
doi: 10.1148/83.3.476.
|
||
<span class="bold">PMID: </span><a href="/pubmed/14206637" target="_blank">14206637</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hypoplasia%20of%20lymphatic%20vessels%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (256)</a></div><h3 class="subhead">Therapy</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/39445428">Radiation-Induced Macrovessel/Microvessel Disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Abe JI,
|
||
Allen BG,
|
||
Beyer AM,
|
||
Lewandowski D,
|
||
Mapuskar KA,
|
||
Subramanian V,
|
||
Tamplin MR,
|
||
Grumbach IM</span><br />
|
||
<span class="medgenPMjournal">Arterioscler Thromb Vasc Biol</span>
|
||
2024 Dec;44(12):2407-2415.
|
||
Epub 2024 Oct 24
|
||
doi: 10.1161/ATVBAHA.124.319866.
|
||
<span class="bold">PMID: </span><a href="/pubmed/39445428" target="_blank">39445428</a><a href="/pmc/articles/PMC11842029" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/34166070">Genetic Basis and Therapies for Vascular Anomalies.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Queisser A,
|
||
Seront E,
|
||
Boon LM,
|
||
Vikkula M</span><br />
|
||
<span class="medgenPMjournal">Circ Res</span>
|
||
2021 Jun 25;129(1):155-173.
|
||
Epub 2021 Jun 24
|
||
doi: 10.1161/CIRCRESAHA.121.318145.
|
||
<span class="bold">PMID: </span><a href="/pubmed/34166070" target="_blank">34166070</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27514587">Plastic Bronchitis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Rubin BK</span><br />
|
||
<span class="medgenPMjournal">Clin Chest Med</span>
|
||
2016 Sep;37(3):405-8.
|
||
Epub 2016 Jun 15
|
||
doi: 10.1016/j.ccm.2016.04.003.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27514587" target="_blank">27514587</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/21742796">Normalization of the vasculature for treatment of cancer and other diseases.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Goel S,
|
||
Duda DG,
|
||
Xu L,
|
||
Munn LL,
|
||
Boucher Y,
|
||
Fukumura D,
|
||
Jain RK</span><br />
|
||
<span class="medgenPMjournal">Physiol Rev</span>
|
||
2011 Jul;91(3):1071-121.
|
||
doi: 10.1152/physrev.00038.2010.
|
||
<span class="bold">PMID: </span><a href="/pubmed/21742796" target="_blank">21742796</a><a href="/pmc/articles/PMC3258432" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/15609924">Lymphatic malformations.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Smith RJ</span><br />
|
||
<span class="medgenPMjournal">Lymphat Res Biol</span>
|
||
2004;2(1):25-31.
|
||
doi: 10.1089/1539685041690436.
|
||
<span class="bold">PMID: </span><a href="/pubmed/15609924" target="_blank">15609924</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hypoplasia%20of%20lymphatic%20vessels%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (110)</a></div><h3 class="subhead">Prognosis</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/38814187">Sequential MRI Evaluation of Lymphatic Abnormalities over the Course of Fontan Completion.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Kelly B,
|
||
Mohanakumar S,
|
||
Ford B,
|
||
Smith CL,
|
||
Pinto E,
|
||
Biko DM,
|
||
Hjortdal VE,
|
||
Dori Y</span><br />
|
||
<span class="medgenPMjournal">Radiol Cardiothorac Imaging</span>
|
||
2024 Jun;6(3):e230315.
|
||
doi: 10.1148/ryct.230315.
|
||
<span class="bold">PMID: </span><a href="/pubmed/38814187" target="_blank">38814187</a><a href="/pmc/articles/PMC11211943" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/38513796">Magnetic resonance lymphangiography: Establishing normal.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Mills M,
|
||
Brezgyte G,
|
||
Ho B,
|
||
Pearce J,
|
||
Gordon K,
|
||
Mortimer PS,
|
||
Ostergaard P,
|
||
Howe FA</span><br />
|
||
<span class="medgenPMjournal">J Vasc Surg Venous Lymphat Disord</span>
|
||
2024 Jul;12(4):101870.
|
||
Epub 2024 Mar 20
|
||
doi: 10.1016/j.jvsv.2024.101870.
|
||
<span class="bold">PMID: </span><a href="/pubmed/38513796" target="_blank">38513796</a><a href="/pmc/articles/PMC11413519" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/21543977">Role of the lymphatic system in the pathogenesis of Crohn's disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">von der Weid PY,
|
||
Rehal S,
|
||
Ferraz JG</span><br />
|
||
<span class="medgenPMjournal">Curr Opin Gastroenterol</span>
|
||
2011 Jul;27(4):335-41.
|
||
doi: 10.1097/MOG.0b013e3283476e8f.
|
||
<span class="bold">PMID: </span><a href="/pubmed/21543977" target="_blank">21543977</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/19172338">Congenital pulmonary lymphangiectasis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Xiao ZY,
|
||
Tao Y,
|
||
Tang XY,
|
||
Chen GJ,
|
||
Guo L</span><br />
|
||
<span class="medgenPMjournal">World J Pediatr</span>
|
||
2009 Feb;5(1):68-70.
|
||
Epub 2009 Jan 27
|
||
doi: 10.1007/s12519-009-0014-5.
|
||
<span class="bold">PMID: </span><a href="/pubmed/19172338" target="_blank">19172338</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/8037546">Primary chylopericardium.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Akamatsu H,
|
||
Amano J,
|
||
Sakamoto T,
|
||
Suzuki A</span><br />
|
||
<span class="medgenPMjournal">Ann Thorac Surg</span>
|
||
1994 Jul;58(1):262-6.
|
||
doi: 10.1016/0003-4975(94)91124-x.
|
||
<span class="bold">PMID: </span><a href="/pubmed/8037546" target="_blank">8037546</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hypoplasia%20of%20lymphatic%20vessels%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (93)</a></div><h3 class="subhead">Clinical prediction guides</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/39445428">Radiation-Induced Macrovessel/Microvessel Disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Abe JI,
|
||
Allen BG,
|
||
Beyer AM,
|
||
Lewandowski D,
|
||
Mapuskar KA,
|
||
Subramanian V,
|
||
Tamplin MR,
|
||
Grumbach IM</span><br />
|
||
<span class="medgenPMjournal">Arterioscler Thromb Vasc Biol</span>
|
||
2024 Dec;44(12):2407-2415.
|
||
Epub 2024 Oct 24
|
||
doi: 10.1161/ATVBAHA.124.319866.
|
||
<span class="bold">PMID: </span><a href="/pubmed/39445428" target="_blank">39445428</a><a href="/pmc/articles/PMC11842029" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/35163775">The Role of the Lymphatic System in the Pathogenesis and Treatment of Inflammatory Bowel Disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Nikolakis D,
|
||
de Voogd FAE,
|
||
Pruijt MJ,
|
||
Grootjans J,
|
||
van de Sande MG,
|
||
D'Haens GR</span><br />
|
||
<span class="medgenPMjournal">Int J Mol Sci</span>
|
||
2022 Feb 6;23(3)
|
||
doi: 10.3390/ijms23031854.
|
||
<span class="bold">PMID: </span><a href="/pubmed/35163775" target="_blank">35163775</a><a href="/pmc/articles/PMC8836364" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/34753699">Assessment of PI3K/AKT and MAPK/ERK pathways activation in oral lymphatic malformations.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Gomes IP,
|
||
Guimarães LM,
|
||
Pereira TDSF,
|
||
Braga NP,
|
||
Martins MD,
|
||
Gomez RS,
|
||
Gomes CC</span><br />
|
||
<span class="medgenPMjournal">Oral Surg Oral Med Oral Pathol Oral Radiol</span>
|
||
2022 Feb;133(2):216-220.
|
||
Epub 2021 Aug 30
|
||
doi: 10.1016/j.oooo.2021.08.018.
|
||
<span class="bold">PMID: </span><a href="/pubmed/34753699" target="_blank">34753699</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/33053612">Tubal flushing for subfertility.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Wang R,
|
||
Watson A,
|
||
Johnson N,
|
||
Cheung K,
|
||
Fitzgerald C,
|
||
Mol BWJ,
|
||
Mohiyiddeen L</span><br />
|
||
<span class="medgenPMjournal">Cochrane Database Syst Rev</span>
|
||
2020 Oct 15;10(10):CD003718.
|
||
doi: 10.1002/14651858.CD003718.pub5.
|
||
<span class="bold">PMID: </span><a href="/pubmed/33053612" target="_blank">33053612</a><a href="/pmc/articles/PMC9508794" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/30937582">Non-contrast MR lymphography of the lymphatic system of the liver.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Arrivé L,
|
||
Monnier-Cholley L,
|
||
Cazzagon N,
|
||
Wendum D,
|
||
Chambenois E,
|
||
El Mouhadi S</span><br />
|
||
<span class="medgenPMjournal">Eur Radiol</span>
|
||
2019 Nov;29(11):5879-5888.
|
||
Epub 2019 Apr 1
|
||
doi: 10.1007/s00330-019-06151-6.
|
||
<span class="bold">PMID: </span><a href="/pubmed/30937582" target="_blank">30937582</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hypoplasia%20of%20lymphatic%20vessels%22%20AND%20Clinical%20prediction%20guides%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (115)</a></div></div>
|
||
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|
||
|
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<div class="portlet mgSection" id="ID_104">
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_systematic_reviews">Recent systematic reviews</h1><a sid="104" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln">
|
||
<div class="nl"><a target="_blank" href="/pubmed/38951201">Sclerotherapy vs. surgical excision for lymphatic malformations of the head and neck: a systematic review and meta-analysis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Alqutub A,
|
||
Baamir NJ,
|
||
Mofti Z,
|
||
Zawawi F,
|
||
Al-Khatib T</span><br />
|
||
<span class="medgenPMjournal">Eur Arch Otorhinolaryngol</span>
|
||
2024 Nov;281(11):5571-5617.
|
||
Epub 2024 Jul 1
|
||
doi: 10.1007/s00405-024-08793-9.
|
||
<span class="bold">PMID: </span><a href="/pubmed/38951201" target="_blank">38951201</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/35852876">Sirolimus in the Treatment of Microcystic Lymphatic Malformations: A Systematic Review.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Teng JMC,
|
||
Hammill A,
|
||
Martini J,
|
||
Treat J</span><br />
|
||
<span class="medgenPMjournal">Lymphat Res Biol</span>
|
||
2023 Apr;21(2):101-110.
|
||
Epub 2022 Jul 18
|
||
doi: 10.1089/lrb.2021.0103.
|
||
<span class="bold">PMID: </span><a href="/pubmed/35852876" target="_blank">35852876</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/33710683">Use of magnetic resonance imaging lymphangiography for preoperative planning in lymphedema surgery: A systematic review.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Forte AJ,
|
||
Boczar D,
|
||
Huayllani MT,
|
||
Avila FR,
|
||
Guliyeva G,
|
||
Lu X,
|
||
Mash WR,
|
||
Kung TA</span><br />
|
||
<span class="medgenPMjournal">Microsurgery</span>
|
||
2021 May;41(4):384-390.
|
||
Epub 2021 Mar 12
|
||
doi: 10.1002/micr.30731.
|
||
<span class="bold">PMID: </span><a href="/pubmed/33710683" target="_blank">33710683</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/33053612">Tubal flushing for subfertility.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Wang R,
|
||
Watson A,
|
||
Johnson N,
|
||
Cheung K,
|
||
Fitzgerald C,
|
||
Mol BWJ,
|
||
Mohiyiddeen L</span><br />
|
||
<span class="medgenPMjournal">Cochrane Database Syst Rev</span>
|
||
2020 Oct 15;10(10):CD003718.
|
||
doi: 10.1002/14651858.CD003718.pub5.
|
||
<span class="bold">PMID: </span><a href="/pubmed/33053612" target="_blank">33053612</a><a href="/pmc/articles/PMC9508794" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/28429627">Compression therapy for congenital low-flow vascular malformations of the extremities: A systematic review.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Langbroek GB,
|
||
Horbach SE,
|
||
van der Vleuten CJ,
|
||
Ubbink DT,
|
||
van der Horst CM</span><br />
|
||
<span class="medgenPMjournal">Phlebology</span>
|
||
2018 Feb;33(1):5-13.
|
||
Epub 2016 Dec 19
|
||
doi: 10.1177/0268355516684694.
|
||
<span class="bold">PMID: </span><a href="/pubmed/28429627" target="_blank">28429627</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hypoplasia%20of%20lymphatic%20vessels%22%20AND%20systematic%5Bsb%5D%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (6)</a></div></div>
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<h2 class="offscreen_noflow">Supplemental Content</h2>
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<div class="portlet_content ln"><ul><li><a href="https://clinicaltrials.gov/search?cond=Hypoplasia%20of%20lymphatic%20vessels" target="_blank">ClinicalTrials.gov</a></li></ul></div>
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<div class="portlet_content ln"><ul class="a_poppers"><li><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(hypoplasia%20of%20lymphatic%20vessels)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">PubMed</a><div class="help-popup">See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div></li><li><a target="_blank" href="/books/?term=((%22clinical%20guidelines%22%5BResource%20Type%5D)%20OR%20%22practice%20guideline%22%5BPublication%20Type%5D)%20AND%20(%22Hypoplasia%20of%20lymphatic%20vessels%22)">Bookshelf</a><div class="help-popup">See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div></li></ul></div>
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<a href="/pubmed?term=Hypoplasia%20of%20lymphatic%20vessels%20AND%20humans[mesh]%20AND%20review[publication%20type]" ref="ncbi_uid=&discoId=gtr_reviews&linkpos=2&linkpostotal=2" target="_blank">Reviews in PubMed</a>
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<a class="htb ralinkpopperctrl" ref="log$=activity&linkpos=1" href="/portal/utils/pageresolver.fcgi?recordid=67d4b6982f30673f7b64a1cd">Hypoplasia of lymphatic vessels</a>
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