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<meta name="keywords" content="C0020542, finding, hypertension, pulmonary, pathologic function, pht - pulmonary hypertension, pulmonary hypertension, autosomal dominant, autosomal recessive, birth defects, chromosomal disease, chromosome, clinical features, clinical findings, clinical genetics, clinical recommendations, clinvar, congenital chromosomal disease, consumer genetic resources, cytogenetic location, disease characteristics, disease definitions, disease descriptions, disease ontology, disease synonyms, disease vocabulary, dysmorphology, entrez, familial disease, gene, gene-disease relationship, genereviews, genetic disease, genetic disorder, genetic terminology, genetic testing registry, genetics home reference, genomic disease, gtr, hereditary disease, heritable disease, hpo, human phenotype ontology, inherited disease, management guidelines, maternal inheritance, medgen, medical genetics, medical subject headings, mesh, mitochondrial inheritance, mode of inheritance, national center for biotechnology information, national institutes of health, national library of medicine, ncbi, nih, nlm, omim, ordo, orphanet, paternal inheritance, phenome, position statements, professional practice guidelines, rare disease, reference sequence, refseq, snomed ct, syndrome, undiagnosed diseases, x-linked recessive" /><meta name="description" content="Increased pressure within the pulmonary circulation due to lung or heart disorder." /><meta name="robots" content="index,nofollow,noarchive" />
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<!--
UID=9376
ConceptID=C0020542
-->
<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Pulmonary hypertension</div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>9376</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information."><span class="highlight" style="background-color:">C0020542</span></a></dd><dt><span class="dotprefix"></span></dt><dd>Finding; Pathologic Function</dd></dl></div></div><table class="medgenTable"><tbody><tr><td>Synonyms:</td>
<td>Hypertension, Pulmonary; Pulmonary Hypertension</td></tr>
<tr><td><span class="bold">SNOMED CT: </span></td>
<td>Pulmonary hypertension (70995007); PHT - Pulmonary hypertension (70995007)</td></tr>
<tr><td colspan="2" class="small"> </td></tr><tr><td>Monarch Initiative:</td>
<td><a href="https://monarchinitiative.org/disease/MONDO:0005149" target="_blank">MONDO:0005149</a></td></tr>
</tbody></table></div><div class="rprt-body jig-ncbiinpagenav" data-jigconfig="smoothScroll: false, gotoTopLink: true, gotoTopLinkText: '', gotoTopLinkAttrs: {'title': 'Go to the top of the page'},allHeadingLevels: ['h1'], topOfPageTOC: true, tocId: 'my-toc'"><div id="rprt-tabs-1" class="rprt-tab"><div id="tb-termsProp-1"><div class="leftCol mgCol"><div>
<div class="portlet mgSection" id="ID_100">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Definition">Definition</h1><a sid="100" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln">Increased pressure within the pulmonary circulation due to lung or heart disorder. [from <a title="NCI Thesaurus" href="http://ncit.nci.nih.gov" class="defSource" target="_blank">NCI</a>]</div>
</div>
<div class="portlet mgSection" id="ID_118">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test,  </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test,  </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM,  </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>,  </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar  </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="TLline">Pulmonary hypertension</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="TLline"><a href="/medgen/19750" ref="tree=MeSH" title="MedGen record for Disease, Respiratory Tract">Disease, Respiratory Tract</a></span><ul><li><span class="TLline"><a href="/medgen/7399" ref="tree=MeSH" title="MedGen record for Disorder of lung">Disorder of lung</a></span><ul><li><span class="matched_ds">Pulmonary hypertension</span><ul><li><span class="TLline"><a href="/medgen/473476" ref="tree=MeSH" title="MedGen record for Associated pulmonary arterial hypertension">Associated pulmonary arterial hypertension</a></span></li><li><span class="TLline"><a href="/medgen/90953" ref="tree=MeSH" title="MedGen record for Heritable pulmonary arterial hypertension">Heritable pulmonary arterial hypertension</a></span><ul><li><span class="TLline"><a href="/medgen/1643124" ref="tree=MeSH" title="MedGen record for Pulmonary hypertension, primary, 1">Pulmonary hypertension, primary, 1</a></span><ul><li><span class="TLline"><a href="/medgen/942109" ref="tree=MeSH" title="MedGen record for Pulmonary hypertension, primary, fenfluramine or dexfenfluramine-associated">Pulmonary hypertension, primary, fenfluramine or dexfenfluramine-associated</a></span></li></ul></li><li><span class="TLline"><a href="/medgen/854709" ref="tree=MeSH" title="MedGen record for Pulmonary hypertension, primary, 2">Pulmonary hypertension, primary, 2</a></span></li><li><span class="TLline"><a href="/medgen/815522" ref="tree=MeSH" title="MedGen record for Pulmonary hypertension, primary, 3">Pulmonary hypertension, primary, 3</a></span></li><li><span class="TLline"><a href="/medgen/815528" ref="tree=MeSH" title="MedGen record for Pulmonary hypertension, primary, 4">Pulmonary hypertension, primary, 4</a></span></li></ul></li><li><span class="TLline"><a href="/medgen/468368" ref="tree=MeSH" title="MedGen record for Idiopathic pulmonary arterial hypertension">Idiopathic pulmonary arterial hypertension</a></span><ul><li><span class="TLline"><a href="/medgen/1825946" ref="tree=MeSH" title="MedGen record for Idiopathic and/or familial pulmonary arterial hypertension">Idiopathic and/or familial pulmonary arterial hypertension</a></span><ul><li><span class="TLline"><a href="/medgen/1802382" ref="tree=MeSH" title="MedGen record for Pulmonary hypertension, primary, autosomal recessive">Pulmonary hypertension, primary, autosomal recessive</a></span></li></ul></li></ul></li><li><span class="TLline"><a href="/medgen/45824" ref="tree=MeSH" title="MedGen record for Persistent fetal circulation">Persistent fetal circulation</a></span><ul><li><span class="TLline"><a href="/medgen/755478" ref="tree=MeSH" title="MedGen record for Alveolar capillary dysplasia with pulmonary venous misalignment">Alveolar capillary dysplasia with pulmonary venous misalignment</a></span></li></ul></li><li><span class="TLline"><a href="/medgen/425404" ref="tree=MeSH" title="MedGen record for Pulmonary arterial hypertension">Pulmonary arterial hypertension</a></span><ul><li><span class="TLline"><a href="/medgen/1783495" ref="tree=MeSH" title="MedGen record for Pulmonary arterial hypertension with lack of acute response to NO challenge">Pulmonary arterial hypertension with lack of acute response to NO challenge</a></span></li><li><span class="TLline"><a href="/medgen/1782938" ref="tree=MeSH" title="MedGen record for Pulmonary arterial hypertension with positive acute response to NO challenge">Pulmonary arterial hypertension with positive acute response to NO challenge</a></span></li></ul></li><li><span class="TLline"><a href="/medgen/538962" ref="tree=MeSH" title="MedGen record for Secondary pulmonary hypertension">Secondary pulmonary hypertension</a></span></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
</div>
<div class="portlet mgSection" id="ID_105">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
<div class="nl"><a target="_blank" href="/pubmed/36017548">2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Humbert M,
Kovacs G,
Hoeper MM,
Badagliacca R,
Berger RMF,
Brida M,
Carlsen J,
Coats AJS,
Escribano-Subias P,
Ferrari P,
Ferreira DS,
Ghofrani HA,
Giannakoulas G,
Kiely DG,
Mayer E,
Meszaros G,
Nagavci B,
Olsson KM,
Pepke-Zaba J,
Quint JK,
Rådegran G,
Simonneau G,
Sitbon O,
Tonia T,
Toshner M,
Vachiery JL,
Vonk Noordegraaf A,
Delcroix M,
Rosenkranz S;
ESC/ERS Scientific Document Group</span><br />
<span class="medgenPMjournal">Eur Heart J</span>
2022 Oct 11;43(38):3618-3731.
doi: 10.1093/eurheartj/ehac237.
<span class="bold">PMID: </span><a href="/pubmed/36017548" target="_blank">36017548</a></div>
<div class="nl"><a target="_blank" href="/pubmed/35412560">Diagnosis and Treatment of Pulmonary Arterial Hypertension: A Review.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Ruopp NF,
Cockrill BA</span><br />
<span class="medgenPMjournal">JAMA</span>
2022 Apr 12;327(14):1379-1391.
doi: 10.1001/jama.2022.4402.
<span class="bold">PMID: </span><a href="/pubmed/35412560" target="_blank">35412560</a></div>
<div class="nl"><a target="_blank" href="/pubmed/29540357">Pulmonary arterial hypertension: pathogenesis and clinical management.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Thenappan T,
Ormiston ML,
Ryan JJ,
Archer SL</span><br />
<span class="medgenPMjournal">BMJ</span>
2018 Mar 14;360:j5492.
doi: 10.1136/bmj.j5492.
<span class="bold">PMID: </span><a href="/pubmed/29540357" target="_blank">29540357</a><a href="/pmc/articles/PMC6889979" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(%22pulmonary%20hypertension%22%5Btiab%3A~0%5D)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (1887)</a></div></div>
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<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
<div class="portlet mgSection" id="ID_103">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
<div class="nl"><a target="_blank" href="/pubmed/38177157">Pulmonary hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Mocumbi A,
Humbert M,
Saxena A,
Jing ZC,
Sliwa K,
Thienemann F,
Archer SL,
Stewart S</span><br />
<span class="medgenPMjournal">Nat Rev Dis Primers</span>
2024 Jan 4;10(1):1.
doi: 10.1038/s41572-023-00486-7.
<span class="bold">PMID: </span><a href="/pubmed/38177157" target="_blank">38177157</a></div>
<div class="nl"><a target="_blank" href="/pubmed/36990148">Evaluation and Management of Chronic Thromboembolic Pulmonary Hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Yang J,
Madani MM,
Mahmud E,
Kim NH</span><br />
<span class="medgenPMjournal">Chest</span>
2023 Aug;164(2):490-502.
Epub 2023 Mar 28
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<span class="bold">PMID: </span><a href="/pubmed/36990148" target="_blank">36990148</a><a href="/pmc/articles/PMC10410247" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/36017548">2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Humbert M,
Kovacs G,
Hoeper MM,
Badagliacca R,
Berger RMF,
Brida M,
Carlsen J,
Coats AJS,
Escribano-Subias P,
Ferrari P,
Ferreira DS,
Ghofrani HA,
Giannakoulas G,
Kiely DG,
Mayer E,
Meszaros G,
Nagavci B,
Olsson KM,
Pepke-Zaba J,
Quint JK,
Rådegran G,
Simonneau G,
Sitbon O,
Tonia T,
Toshner M,
Vachiery JL,
Vonk Noordegraaf A,
Delcroix M,
Rosenkranz S;
ESC/ERS Scientific Document Group</span><br />
<span class="medgenPMjournal">Eur Heart J</span>
2022 Oct 11;43(38):3618-3731.
doi: 10.1093/eurheartj/ehac237.
<span class="bold">PMID: </span><a href="/pubmed/36017548" target="_blank">36017548</a></div>
<div class="nl"><a target="_blank" href="/pubmed/33844574">Pulmonary Hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Poch D,
Mandel J</span><br />
<span class="medgenPMjournal">Ann Intern Med</span>
2021 Apr;174(4):ITC49-ITC64.
Epub 2021 Apr 13
doi: 10.7326/AITC202104200.
<span class="bold">PMID: </span><a href="/pubmed/33844574" target="_blank">33844574</a></div>
<div class="nl"><a target="_blank" href="/pubmed/26975810">A global view of pulmonary hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Hoeper MM,
Humbert M,
Souza R,
Idrees M,
Kawut SM,
Sliwa-Hahnle K,
Jing ZC,
Gibbs JS</span><br />
<span class="medgenPMjournal">Lancet Respir Med</span>
2016 Apr;4(4):306-22.
Epub 2016 Mar 12
doi: 10.1016/S2213-2600(15)00543-3.
<span class="bold">PMID: </span><a href="/pubmed/26975810" target="_blank">26975810</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Pulmonary%20hypertension%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (16425)</a></div><h3 class="subhead">Diagnosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/38689108">Pediatric Pulmonary Hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Morales-Demori R,
Coleman R,
Mallory GB</span><br />
<span class="medgenPMjournal">Pediatr Rev</span>
2024 May 1;45(5):251-259.
doi: 10.1542/pir.2023-006010.
<span class="bold">PMID: </span><a href="/pubmed/38689108" target="_blank">38689108</a></div>
<div class="nl"><a target="_blank" href="/pubmed/38177157">Pulmonary hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Mocumbi A,
Humbert M,
Saxena A,
Jing ZC,
Sliwa K,
Thienemann F,
Archer SL,
Stewart S</span><br />
<span class="medgenPMjournal">Nat Rev Dis Primers</span>
2024 Jan 4;10(1):1.
doi: 10.1038/s41572-023-00486-7.
<span class="bold">PMID: </span><a href="/pubmed/38177157" target="_blank">38177157</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34546299">Pulmonary Hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Walter K</span><br />
<span class="medgenPMjournal">JAMA</span>
2021 Sep 21;326(11):1116.
doi: 10.1001/jama.2021.11054.
<span class="bold">PMID: </span><a href="/pubmed/34546299" target="_blank">34546299</a></div>
<div class="nl"><a target="_blank" href="/pubmed/33844574">Pulmonary Hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Poch D,
Mandel J</span><br />
<span class="medgenPMjournal">Ann Intern Med</span>
2021 Apr;174(4):ITC49-ITC64.
Epub 2021 Apr 13
doi: 10.7326/AITC202104200.
<span class="bold">PMID: </span><a href="/pubmed/33844574" target="_blank">33844574</a></div>
<div class="nl"><a target="_blank" href="/pubmed/28241922">Pulmonary Hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Hoeper MM,
Ghofrani HA,
Grünig E,
Klose H,
Olschewski H,
Rosenkranz S</span><br />
<span class="medgenPMjournal">Dtsch Arztebl Int</span>
2017 Feb 3;114(5):73-84.
doi: 10.3238/arztebl.2017.0073.
<span class="bold">PMID: </span><a href="/pubmed/28241922" target="_blank">28241922</a><a href="/pmc/articles/PMC5331483" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Pulmonary%20hypertension%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (14602)</a></div><h3 class="subhead">Therapy</h3>
<div class="nl"><a target="_blank" href="/pubmed/39209478">Pulmonary hypertension associated with left heart disease.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Maron BA,
Bortman G,
De Marco T,
Huston JH,
Lang IM,
Rosenkranz SH,
Vachiéry JL,
Tedford RJ</span><br />
<span class="medgenPMjournal">Eur Respir J</span>
2024 Oct;64(4)
Epub 2024 Oct 31
doi: 10.1183/13993003.01344-2024.
<span class="bold">PMID: </span><a href="/pubmed/39209478" target="_blank">39209478</a><a href="/pmc/articles/PMC11525340" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/39209469">Pulmonary hypertension associated with lung diseases.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Shlobin OA,
Adir Y,
Barbera JA,
Cottin V,
Harari S,
Jutant EM,
Pepke-Zaba J,
Ghofrani HA,
Channick R</span><br />
<span class="medgenPMjournal">Eur Respir J</span>
2024 Oct;64(4)
Epub 2024 Oct 31
doi: 10.1183/13993003.01200-2024.
<span class="bold">PMID: </span><a href="/pubmed/39209469" target="_blank">39209469</a><a href="/pmc/articles/PMC11525344" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30545974">Pulmonary hypertension due to left heart disease.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Vachiéry JL,
Tedford RJ,
Rosenkranz S,
Palazzini M,
Lang I,
Guazzi M,
Coghlan G,
Chazova I,
De Marco T</span><br />
<span class="medgenPMjournal">Eur Respir J</span>
2019 Jan;53(1)
Epub 2019 Jan 24
doi: 10.1183/13993003.01897-2018.
<span class="bold">PMID: </span><a href="/pubmed/30545974" target="_blank">30545974</a><a href="/pmc/articles/PMC6351334" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/29032565">Pulmonary Hypertension Complicating Connective Tissue Disease.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Volkmann ER,
Chung A,
Saggar R,
Belperio JA,
Lynch JP 3rd</span><br />
<span class="medgenPMjournal">Semin Respir Crit Care Med</span>
2017 Oct;38(5):619-635.
Epub 2017 Oct 15
doi: 10.1055/s-0037-1606203.
<span class="bold">PMID: </span><a href="/pubmed/29032565" target="_blank">29032565</a></div>
<div class="nl"><a target="_blank" href="/pubmed/12410094">Scleroderma in children.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Foeldvari I</span><br />
<span class="medgenPMjournal">Curr Opin Rheumatol</span>
2002 Nov;14(6):699-703.
doi: 10.1097/00002281-200211000-00012.
<span class="bold">PMID: </span><a href="/pubmed/12410094" target="_blank">12410094</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Pulmonary%20hypertension%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (12092)</a></div><h3 class="subhead">Prognosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/33082079">Idiopathic pulmonary arterial hypertension phenotypes determined by cluster analysis from the COMPERA registry.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Hoeper MM,
Pausch C,
Grünig E,
Klose H,
Staehler G,
Huscher D,
Pittrow D,
Olsson KM,
Vizza CD,
Gall H,
Benjamin N,
Distler O,
Opitz C,
Gibbs JSR,
Delcroix M,
Ghofrani HA,
Rosenkranz S,
Ewert R,
Kaemmerer H,
Lange TJ,
Kabitz HJ,
Skowasch D,
Skride A,
Jureviciene E,
Paleviciute E,
Miliauskas S,
Claussen M,
Behr J,
Milger K,
Halank M,
Wilkens H,
Wirtz H,
Pfeuffer-Jovic E,
Harbaum L,
Scholtz W,
Dumitrescu D,
Bruch L,
Coghlan G,
Neurohr C,
Tsangaris I,
Gorenflo M,
Scelsi L,
Vonk-Noordegraaf A,
Ulrich S,
Held M</span><br />
<span class="medgenPMjournal">J Heart Lung Transplant</span>
2020 Dec;39(12):1435-1444.
Epub 2020 Sep 30
doi: 10.1016/j.healun.2020.09.011.
<span class="bold">PMID: </span><a href="/pubmed/33082079" target="_blank">33082079</a></div>
<div class="nl"><a target="_blank" href="/pubmed/29502796">Pulmonary hypertension in congenital diaphragmatic hernia patients: Prognostic markers and long-term outcomes.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Wong M,
Reyes J,
Lapidus-Krol E,
Chiang M,
Humpl T,
Al-Faraj M,
Ryan G,
Chiu PPL</span><br />
<span class="medgenPMjournal">J Pediatr Surg</span>
2018 May;53(5):918-924.
Epub 2018 Feb 7
doi: 10.1016/j.jpedsurg.2018.02.015.
<span class="bold">PMID: </span><a href="/pubmed/29502796" target="_blank">29502796</a></div>
<div class="nl"><a target="_blank" href="/pubmed/26066077">Five-Year outcomes of patients enrolled in the REVEAL Registry.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Farber HW,
Miller DP,
Poms AD,
Badesch DB,
Frost AE,
Muros-Le Rouzic E,
Romero AJ,
Benton WW,
Elliott CG,
McGoon MD,
Benza RL</span><br />
<span class="medgenPMjournal">Chest</span>
2015 Oct;148(4):1043-54.
doi: 10.1378/chest.15-0300.
<span class="bold">PMID: </span><a href="/pubmed/26066077" target="_blank">26066077</a></div>
<div class="nl"><a target="_blank" href="/pubmed/23102885">Moderate pulmonary embolism treated with thrombolysis (from the "MOPETT" Trial).</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Sharifi M,
Bay C,
Skrocki L,
Rahimi F,
Mehdipour M;
“MOPETT” Investigators</span><br />
<span class="medgenPMjournal">Am J Cardiol</span>
2013 Jan 15;111(2):273-7.
Epub 2012 Oct 24
doi: 10.1016/j.amjcard.2012.09.027.
<span class="bold">PMID: </span><a href="/pubmed/23102885" target="_blank">23102885</a></div>
<div class="nl"><a target="_blank" href="/pubmed/1863023">Survival in patients with primary pulmonary hypertension. Results from a national prospective registry.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">D'Alonzo GE,
Barst RJ,
Ayres SM,
Bergofsky EH,
Brundage BH,
Detre KM,
Fishman AP,
Goldring RM,
Groves BM,
Kernis JT</span><br />
<span class="medgenPMjournal">Ann Intern Med</span>
1991 Sep 1;115(5):343-9.
doi: 10.7326/0003-4819-115-5-343.
<span class="bold">PMID: </span><a href="/pubmed/1863023" target="_blank">1863023</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Pulmonary%20hypertension%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (12136)</a></div><h3 class="subhead">Clinical prediction guides</h3>
<div class="nl"><a target="_blank" href="/pubmed/31335403">Update on Congenital Diaphragmatic Hernia.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Chatterjee D,
Ing RJ,
Gien J</span><br />
<span class="medgenPMjournal">Anesth Analg</span>
2020 Sep;131(3):808-821.
doi: 10.1213/ANE.0000000000004324.
<span class="bold">PMID: </span><a href="/pubmed/31335403" target="_blank">31335403</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30878436">Imaging Risk in Multisystem Inflammatory Diseases.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Ikonomidis I,
Makavos G,
Katsimbri P,
Boumpas DT,
Parissis J,
Iliodromitis E</span><br />
<span class="medgenPMjournal">JACC Cardiovasc Imaging</span>
2019 Dec;12(12):2517-2537.
Epub 2019 Mar 13
doi: 10.1016/j.jcmg.2018.06.033.
<span class="bold">PMID: </span><a href="/pubmed/30878436" target="_blank">30878436</a></div>
<div class="nl"><a target="_blank" href="/pubmed/28935040">Cardiopulmonary Exercise Testing: What Is its Value?</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Guazzi M,
Bandera F,
Ozemek C,
Systrom D,
Arena R</span><br />
<span class="medgenPMjournal">J Am Coll Cardiol</span>
2017 Sep 26;70(13):1618-1636.
doi: 10.1016/j.jacc.2017.08.012.
<span class="bold">PMID: </span><a href="/pubmed/28935040" target="_blank">28935040</a></div>
<div class="nl"><a target="_blank" href="/pubmed/27679806">Contemporary diagnosis and management of pulmonary hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Cannon JE,
Pepke-Zaba J</span><br />
<span class="medgenPMjournal">Heart</span>
2016 Oct 15;102(20):1680-91.
doi: 10.1136/heartjnl-2015-307996.
<span class="bold">PMID: </span><a href="/pubmed/27679806" target="_blank">27679806</a></div>
<div class="nl"><a target="_blank" href="/pubmed/24855320">Diagnosis and treatment of pulmonary hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Haeck ML,
Vliegen HW</span><br />
<span class="medgenPMjournal">Heart</span>
2015 Feb;101(4):311-9.
Epub 2014 May 22
doi: 10.1136/heartjnl-2011-301386.
<span class="bold">PMID: </span><a href="/pubmed/24855320" target="_blank">24855320</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Pulmonary%20hypertension%22%20AND%20Clinical%20prediction%20guides%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (9776)</a></div></div>
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<div class="nl"><a target="_blank" href="/pubmed/36947725">Exercise-based rehabilitation programmes for pulmonary hypertension.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Morris NR,
Kermeen FD,
Jones AW,
Lee JY,
Holland AE</span><br />
<span class="medgenPMjournal">Cochrane Database Syst Rev</span>
2023 Mar 22;3(3):CD011285.
doi: 10.1002/14651858.CD011285.pub3.
<span class="bold">PMID: </span><a href="/pubmed/36947725" target="_blank">36947725</a><a href="/pmc/articles/PMC10032353" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/36853497">Benefits and Risks of Antidepressant Drugs During Pregnancy: A Systematic Review of Meta-analyses.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Desaunay P,
Eude LG,
Dreyfus M,
Alexandre C,
Fedrizzi S,
Alexandre J,
Uguz F,
Guénolé F</span><br />
<span class="medgenPMjournal">Paediatr Drugs</span>
2023 May;25(3):247-265.
Epub 2023 Feb 28
doi: 10.1007/s40272-023-00561-2.
<span class="bold">PMID: </span><a href="/pubmed/36853497" target="_blank">36853497</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34292294">Dengue and the heart.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Araiza-Garaygordobil D,
García-Martínez CE,
Burgos LM,
Saldarriaga C,
Liblik K,
Mendoza I,
Martinez-Selles M,
Scatularo CE,
Farina JM,
Baranchuk A;
Neglected Tropical Diseases and other Infectious Diseases affecting the Heart (the NETHeart) project</span><br />
<span class="medgenPMjournal">Cardiovasc J Afr</span>
2021 Sep-Oct 23;32(5):276-283.
Epub 2021 Jul 20
doi: 10.5830/CVJA-2021-033.
<span class="bold">PMID: </span><a href="/pubmed/34292294" target="_blank">34292294</a><a href="/pmc/articles/PMC8756038" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/28495379">Transthoracic Echocardiography for Diagnosing Pulmonary Embolism: A Systematic Review and Meta-Analysis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Fields JM,
Davis J,
Girson L,
Au A,
Potts J,
Morgan CJ,
Vetter I,
Riesenberg LA</span><br />
<span class="medgenPMjournal">J Am Soc Echocardiogr</span>
2017 Jul;30(7):714-723.e4.
Epub 2017 May 9
doi: 10.1016/j.echo.2017.03.004.
<span class="bold">PMID: </span><a href="/pubmed/28495379" target="_blank">28495379</a></div>
<div class="nl"><a target="_blank" href="/pubmed/27941129">Update of EULAR recommendations for the treatment of systemic sclerosis.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Kowal-Bielecka O,
Fransen J,
Avouac J,
Becker M,
Kulak A,
Allanore Y,
Distler O,
Clements P,
Cutolo M,
Czirjak L,
Damjanov N,
Del Galdo F,
Denton CP,
Distler JHW,
Foeldvari I,
Figelstone K,
Frerix M,
Furst DE,
Guiducci S,
Hunzelmann N,
Khanna D,
Matucci-Cerinic M,
Herrick AL,
van den Hoogen F,
van Laar JM,
Riemekasten G,
Silver R,
Smith V,
Sulli A,
Tarner I,
Tyndall A,
Welling J,
Wigley F,
Valentini G,
Walker UA,
Zulian F,
Müller-Ladner U;
EUSTAR Coauthors</span><br />
<span class="medgenPMjournal">Ann Rheum Dis</span>
2017 Aug;76(8):1327-1339.
Epub 2016 Nov 9
doi: 10.1136/annrheumdis-2016-209909.
<span class="bold">PMID: </span><a href="/pubmed/27941129" target="_blank">27941129</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Pulmonary%20hypertension%22%20AND%20systematic%5Bsb%5D%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (504)</a></div></div>
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