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<!--
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||
UID=9827
|
||
ConceptID=C0024214
|
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-->
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<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Lymphangiectasis</div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>9827</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C0024214</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div><table class="medgenTable"><tbody><tr><td>Synonym:</td>
|
||
<td>lymphangiectasia</td></tr>
|
||
<tr><td><span class="bold">SNOMED CT: </span></td>
|
||
<td>Lymphangiectasis (48087001); Lymphangiectasia (48087001)</td></tr>
|
||
<tr><td colspan="2" class="small"> </td></tr><tr><td>HPO:</td>
|
||
<td><a target="_blank" title="Human Phenotype Ontology" href="https://hpo.jax.org/app/browse/term/HP:0031842">HP:0031842</a></td></tr>
|
||
<tr><td>Monarch Initiative:</td>
|
||
<td><a href="https://monarchinitiative.org/disease/MONDO:0006840" target="_blank">MONDO:0006840</a></td></tr>
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</tbody></table></div><div class="rprt-body jig-ncbiinpagenav" data-jigconfig="smoothScroll: false, gotoTopLink: true, gotoTopLinkText: '', gotoTopLinkAttrs: {'title': 'Go to the top of the page'},allHeadingLevels: ['h1'], topOfPageTOC: true, tocId: 'my-toc'"><div id="rprt-tabs-1" class="rprt-tab"><div id="tb-termsProp-1"><div class="leftCol mgCol"><div>
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||
<div class="portlet_content ln">Dilation of the lymphatic vessels, the basic process that may result in the formation of a lymphangioma. [from <a title="Human Phenotype Ontology" href="http://www.human-phenotype-ontology.org" class="defSource" target="_blank">HPO</a>]</div>
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
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<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test, </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test, </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM, </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>, </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="chiclet_list"><span class="chiclet unavailable round" title="Clinical test">C</span><span class="chiclet unavailable round" title="Research Tests">R</span><span class="chiclet unavailable" title="OMIM">O</span><span class="chiclet unavailable" title="GeneReviews">G</span><span class="chiclet unavailable" title="ClinVar">V</span></span><span class="TLline">Lymphangiectasis</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="TLline"><a href="/medgen/867443" ref="tree=MeSH" title="MedGen record for Phenotypic abnormality">Phenotypic abnormality</a></span><ul><li><span class="TLline"><a href="/medgen/867388" ref="tree=MeSH" title="MedGen record for Abnormality of the immune system">Abnormality of the immune system</a></span><ul><li><span class="TLline"><a href="/medgen/892707" ref="tree=MeSH" title="MedGen record for Abnormality of the lymphatic system">Abnormality of the lymphatic system</a></span><ul><li><span class="TLline"><a href="/medgen/867589" ref="tree=MeSH" title="MedGen record for Abnormal lymphatic vessel morphology">Abnormal lymphatic vessel morphology</a></span><ul><li><span class="matched_ds">Lymphangiectasis</span><ul><li><span class="TLline"><a href="/medgen/340355" ref="tree=MeSH" title="MedGen record for Congenital pulmonary lymphangiectasia">Congenital pulmonary lymphangiectasia</a></span></li><li><span class="TLline"><a href="/medgen/9828" ref="tree=MeSH" title="MedGen record for Intestinal lymphangiectasia">Intestinal lymphangiectasia</a></span><ul><li><span class="TLline"><a href="/medgen/444009" ref="tree=MeSH" title="MedGen record for Primary intestinal lymphangiectasia">Primary intestinal lymphangiectasia</a></span></li><li><span class="TLline"><a href="/medgen/19522" ref="tree=MeSH" title="MedGen record for Protein-losing enteropathy">Protein-losing enteropathy</a></span></li><li><span class="TLline"><a href="/medgen/908114" ref="tree=MeSH" title="MedGen record for Secondary intestinal lymphangiectasia">Secondary intestinal lymphangiectasia</a></span></li></ul></li><li><span class="TLline"><a href="/medgen/344668" ref="tree=MeSH" title="MedGen record for Pancreatic lymphangiectasis">Pancreatic lymphangiectasis</a></span></li><li><span class="TLline"><a href="/medgen/341077" ref="tree=MeSH" title="MedGen record for Pericardial lymphangiectasia">Pericardial lymphangiectasia</a></span></li><li><span class="TLline"><a href="/medgen/343483" ref="tree=MeSH" title="MedGen record for Pleural lymphangiectasia">Pleural lymphangiectasia</a></span></li><li><span class="TLline"><a href="/medgen/340882" ref="tree=MeSH" title="MedGen record for Pulmonary lymphangiectasia">Pulmonary lymphangiectasia</a></span></li><li><span class="TLline"><a href="/medgen/383841" ref="tree=MeSH" title="MedGen record for Thyroid lymphangiectasia">Thyroid lymphangiectasia</a></span></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_112">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Conditions_with_this_feature">Conditions with this feature</h1><a sid="112" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln clinfeat">
|
||
<div class="divPopper rprt" id="rdis_108454"><div><strong>Costello syndrome</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>108454</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C0587248</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">While the majority of individuals with HRAS-related Costello syndrome (Costello syndrome) share characteristic findings affecting multiple organ systems, the phenotypic spectrum is wide, ranging from a mild or attenuated phenotype to a severe phenotype with early-lethal complications. Costello syndrome is typically characterized by failure to thrive in infancy as a result of severe postnatal feeding difficulties; short stature; developmental delay or intellectual disability; coarse facial features (full lips, large mouth, full nasal tip); curly or sparse, fine hair; loose, soft skin with deep palmar and plantar creases; papillomata of the face and perianal region; diffuse hypotonia and joint laxity with ulnar deviation of the wrists and fingers; tight Achilles tendons; and cardiac involvement including cardiac hypertrophy (usually hypertrophic cardiomyopathy), congenital heart defects (usually valvular pulmonic stenosis), and arrhythmia (usually supraventricular tachycardia, especially abnormal atrial rhythm / multifocal atrial tachycardia or ectopic atrial tachycardia). Relative or absolute macrocephaly is typical, and postnatal cerebellar overgrowth can result in the development of a Chiari I malformation with associated anomalies including hydrocephalus or syringomyelia. Individuals with Costello syndrome have an approximately 15% lifetime risk for malignant tumors including rhabdomyosarcoma and neuroblastoma in young children and transitional cell carcinoma of the bladder in adolescents and young adults.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/108454">Condition Record</a></div></div>
|
||
<div class="divPopper rprt" id="rdis_400692"><div><strong>MPI-congenital disorder of glycosylation</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>400692</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C1865145</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Congenital disorders of glycosylation (CDGs) are a genetically heterogeneous group of autosomal recessive disorders caused by enzymatic defects in the synthesis and processing of asparagine (N)-linked glycans or oligosaccharides on glycoproteins. Type I CDGs comprise defects in the assembly of the dolichol lipid-linked oligosaccharide (LLO) chain and its transfer to the nascent protein. These disorders can be identified by a characteristic abnormal isoelectric focusing profile of plasma transferrin (Leroy, 2006). For a discussion of the classification of CDGs, see CDG1A (212065). CDG Ib is clinically distinct from most other CDGs by the lack of significant central nervous system involvement. The predominant symptoms are chronic diarrhea with failure to thrive and protein-losing enteropathy with coagulopathy. Some patients develop hepatic fibrosis. CDG Ib is also different from other CDGs in that it can be treated effectively with oral mannose supplementation, but can be fatal if untreated (Marquardt and Denecke, 2003). Thus, CDG Ib should be considered in the differential diagnosis of patients with unexplained hypoglycemia, chronic diarrhea, liver disease, or coagulopathy in order to allow early diagnosis and effective therapy (Vuillaumier-Barrot et al., 2002) Freeze and Aebi (1999) reviewed CDG Ib and CDG Ic (603147). Marques-da-Silva et al. (2017) systematically reviewed the literature concerning liver involvement in CDG.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/400692">Condition Record</a></div></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_108454" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Costello syndrome</a></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_400692" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">MPI-congenital disorder of glycosylation</a></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_105">
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||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/33407260">Individual approach for treatment of primary intestinal lymphangiectasia in children: single-center experience and review of the literature.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Kwon Y,
|
||
Kim ES,
|
||
Choe YH,
|
||
Kim MJ</span><br />
|
||
<span class="medgenPMjournal">BMC Pediatr</span>
|
||
2021 Jan 7;21(1):21.
|
||
doi: 10.1186/s12887-020-02447-5.
|
||
<span class="bold">PMID: </span><a href="/pubmed/33407260" target="_blank">33407260</a><a href="/pmc/articles/PMC7789338" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/31893385">Predictors of iron-deficiency anemia in primary care older adults: a real-world European multi-country longitudinal study.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Vetrano DL,
|
||
Zucchelli A,
|
||
Marconi E,
|
||
Levi M,
|
||
Pegoraro V,
|
||
Cataldo N,
|
||
Heiman F,
|
||
Cricelli C,
|
||
Lapi F</span><br />
|
||
<span class="medgenPMjournal">Aging Clin Exp Res</span>
|
||
2020 Nov;32(11):2211-2216.
|
||
Epub 2020 Jan 1
|
||
doi: 10.1007/s40520-019-01454-6.
|
||
<span class="bold">PMID: </span><a href="/pubmed/31893385" target="_blank">31893385</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/4978356">Treatment of protein losing enteropathy due to idiopathic intestinal lymphangiectasis by parenteral nutrition.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Wagner A</span><br />
|
||
<span class="medgenPMjournal">Digestion</span>
|
||
1969;2(3):167-71.
|
||
doi: 10.1159/000196934.
|
||
<span class="bold">PMID: </span><a href="/pubmed/4978356" target="_blank">4978356</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(%22lymphangiectasis%22%5Btiab%3A~0%5D)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (5)</a></div></div>
|
||
</div>
|
||
<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
|
||
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
|
||
<div class="portlet mgSection" id="ID_103">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/38038236">Use of octreotide for the treatment of protein-losing enteropathy in dogs: Retrospective study of 18 cases.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Jablonski SA,
|
||
Mazepa ASW,
|
||
Tolbert MK</span><br />
|
||
<span class="medgenPMjournal">J Vet Intern Med</span>
|
||
2024 Jan-Feb;38(1):145-151.
|
||
Epub 2023 Dec 1
|
||
doi: 10.1111/jvim.16966.
|
||
<span class="bold">PMID: </span><a href="/pubmed/38038236" target="_blank">38038236</a><a href="/pmc/articles/PMC10800202" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/30543193">A story of oedemas.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Cordier C,
|
||
Spyckerelle C,
|
||
Forzy G</span><br />
|
||
<span class="medgenPMjournal">Ann Biol Clin (Paris)</span>
|
||
2018 Dec 1;76(6):681-685.
|
||
doi: 10.1684/abc.2018.1398.
|
||
<span class="bold">PMID: </span><a href="/pubmed/30543193" target="_blank">30543193</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27514588">Nonmalignant Adult Thoracic Lymphatic Disorders.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Itkin M,
|
||
McCormack FX</span><br />
|
||
<span class="medgenPMjournal">Clin Chest Med</span>
|
||
2016 Sep;37(3):409-20.
|
||
doi: 10.1016/j.ccm.2016.04.004.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27514588" target="_blank">27514588</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27246594">Thoracic involvement in generalised lymphatic anomaly (or lymphangiomatosis).</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Luisi F,
|
||
Torre O,
|
||
Harari S</span><br />
|
||
<span class="medgenPMjournal">Eur Respir Rev</span>
|
||
2016 Jun;25(140):170-7.
|
||
doi: 10.1183/16000617.0018-2016.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27246594" target="_blank">27246594</a><a href="/pmc/articles/PMC9487238" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/472852">Congenital pulmonary lymphangiectasis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Lloyd ES,
|
||
Press HC Jr</span><br />
|
||
<span class="medgenPMjournal">South Med J</span>
|
||
1979 Sep;72(9):1205-6.
|
||
doi: 10.1097/00007611-197909000-00036.
|
||
<span class="bold">PMID: </span><a href="/pubmed/472852" target="_blank">472852</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Lymphangiectasis%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (131)</a></div><h3 class="subhead">Diagnosis</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/38291682">Secondary Intestinal Lymphangiectasia.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Hoskins B,
|
||
Song W,
|
||
Guerrerio AL</span><br />
|
||
<span class="medgenPMjournal">J Pediatr Gastroenterol Nutr</span>
|
||
2024 Jan;78(1):166.
|
||
Epub 2023 Sep 6
|
||
doi: 10.1097/MPG.0000000000003936.
|
||
<span class="bold">PMID: </span><a href="/pubmed/38291682" target="_blank">38291682</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/38038236">Use of octreotide for the treatment of protein-losing enteropathy in dogs: Retrospective study of 18 cases.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Jablonski SA,
|
||
Mazepa ASW,
|
||
Tolbert MK</span><br />
|
||
<span class="medgenPMjournal">J Vet Intern Med</span>
|
||
2024 Jan-Feb;38(1):145-151.
|
||
Epub 2023 Dec 1
|
||
doi: 10.1111/jvim.16966.
|
||
<span class="bold">PMID: </span><a href="/pubmed/38038236" target="_blank">38038236</a><a href="/pmc/articles/PMC10800202" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/29232763">Lymphangiectasia.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Swann PG,
|
||
Han T</span><br />
|
||
<span class="medgenPMjournal">Clin Exp Optom</span>
|
||
2018 May;101(3):418-419.
|
||
Epub 2017 Dec 12
|
||
doi: 10.1111/cxo.12647.
|
||
<span class="bold">PMID: </span><a href="/pubmed/29232763" target="_blank">29232763</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27514588">Nonmalignant Adult Thoracic Lymphatic Disorders.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Itkin M,
|
||
McCormack FX</span><br />
|
||
<span class="medgenPMjournal">Clin Chest Med</span>
|
||
2016 Sep;37(3):409-20.
|
||
doi: 10.1016/j.ccm.2016.04.004.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27514588" target="_blank">27514588</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/22196284">Pulmonary lymphangiomatosis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Satria MN,
|
||
Pacheco-Rodriguez G,
|
||
Moss J</span><br />
|
||
<span class="medgenPMjournal">Lymphat Res Biol</span>
|
||
2011;9(4):191-3.
|
||
doi: 10.1089/lrb.2011.0023.
|
||
<span class="bold">PMID: </span><a href="/pubmed/22196284" target="_blank">22196284</a><a href="/pmc/articles/PMC3246407" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Lymphangiectasis%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (527)</a></div><h3 class="subhead">Therapy</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/38038236">Use of octreotide for the treatment of protein-losing enteropathy in dogs: Retrospective study of 18 cases.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Jablonski SA,
|
||
Mazepa ASW,
|
||
Tolbert MK</span><br />
|
||
<span class="medgenPMjournal">J Vet Intern Med</span>
|
||
2024 Jan-Feb;38(1):145-151.
|
||
Epub 2023 Dec 1
|
||
doi: 10.1111/jvim.16966.
|
||
<span class="bold">PMID: </span><a href="/pubmed/38038236" target="_blank">38038236</a><a href="/pmc/articles/PMC10800202" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/37855839">Lymphangiectasia Hemorrhagica Conjunctivae Regression with Bleomycin Sclerotherapy on Anterior-Segment Optical Coherence Tomography.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Tripathy D</span><br />
|
||
<span class="medgenPMjournal">JAMA Ophthalmol</span>
|
||
2023 Oct 1;141(10):e231878.
|
||
Epub 2023 Oct 19
|
||
doi: 10.1001/jamaophthalmol.2023.1878.
|
||
<span class="bold">PMID: </span><a href="/pubmed/37855839" target="_blank">37855839</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/26718572">Eculizumab-related progressive multifocal leukoencephalopathy.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Gómez-Cibeira E,
|
||
Ivanovic-Barbeito Y,
|
||
Gutiérrez-Martínez E,
|
||
Morales E,
|
||
Abradelo M,
|
||
Hilario A,
|
||
Ramos A,
|
||
Ruiz-Morales J,
|
||
Villarejo-Galende A</span><br />
|
||
<span class="medgenPMjournal">Neurology</span>
|
||
2016 Jan 26;86(4):399-400.
|
||
Epub 2015 Dec 30
|
||
doi: 10.1212/WNL.0000000000002312.
|
||
<span class="bold">PMID: </span><a href="/pubmed/26718572" target="_blank">26718572</a><a href="/pmc/articles/PMC4776092" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/19179873">Intestinal lymphangiectasia.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Hauser B,
|
||
Moreels T,
|
||
Urbain D,
|
||
Van Marck V,
|
||
Pletincx M,
|
||
Devreker T,
|
||
Vandenplas Y</span><br />
|
||
<span class="medgenPMjournal">J Pediatr Gastroenterol Nutr</span>
|
||
2009 Feb;48(2):125.
|
||
doi: 10.1097/MPG.0b013e318192418e.
|
||
<span class="bold">PMID: </span><a href="/pubmed/19179873" target="_blank">19179873</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/4888638">Unusual pulmonary diseases.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Knelson JH,
|
||
De Lemos RA,
|
||
Avery ME</span><br />
|
||
<span class="medgenPMjournal">Dis Mon</span>
|
||
1969 Mar:1-44.
|
||
doi: 10.1016/s0011-5029(69)80014-3.
|
||
<span class="bold">PMID: </span><a href="/pubmed/4888638" target="_blank">4888638</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Lymphangiectasis%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (148)</a></div><h3 class="subhead">Prognosis</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/30543193">A story of oedemas.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Cordier C,
|
||
Spyckerelle C,
|
||
Forzy G</span><br />
|
||
<span class="medgenPMjournal">Ann Biol Clin (Paris)</span>
|
||
2018 Dec 1;76(6):681-685.
|
||
doi: 10.1684/abc.2018.1398.
|
||
<span class="bold">PMID: </span><a href="/pubmed/30543193" target="_blank">30543193</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/28258976">Congenital pulmonary lymphangiectasia.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Yuan SM</span><br />
|
||
<span class="medgenPMjournal">J Perinat Med</span>
|
||
2017 Dec 20;45(9):1023-1030.
|
||
doi: 10.1515/jpm-2016-0407.
|
||
<span class="bold">PMID: </span><a href="/pubmed/28258976" target="_blank">28258976</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27246594">Thoracic involvement in generalised lymphatic anomaly (or lymphangiomatosis).</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Luisi F,
|
||
Torre O,
|
||
Harari S</span><br />
|
||
<span class="medgenPMjournal">Eur Respir Rev</span>
|
||
2016 Jun;25(140):170-7.
|
||
doi: 10.1183/16000617.0018-2016.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27246594" target="_blank">27246594</a><a href="/pmc/articles/PMC9487238" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/15334508">Pulmonary lymphangiectasia: diagnosis and clinical course.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Esther CR Jr,
|
||
Barker PM</span><br />
|
||
<span class="medgenPMjournal">Pediatr Pulmonol</span>
|
||
2004 Oct;38(4):308-13.
|
||
doi: 10.1002/ppul.20100.
|
||
<span class="bold">PMID: </span><a href="/pubmed/15334508" target="_blank">15334508</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/10712360">Thoracic lymphangiomas, lymphangiectasis, lymphangiomatosis, and lymphatic dysplasia syndrome.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Faul JL,
|
||
Berry GJ,
|
||
Colby TV,
|
||
Ruoss SJ,
|
||
Walter MB,
|
||
Rosen GD,
|
||
Raffin TA</span><br />
|
||
<span class="medgenPMjournal">Am J Respir Crit Care Med</span>
|
||
2000 Mar;161(3 Pt 1):1037-46.
|
||
doi: 10.1164/ajrccm.161.3.9904056.
|
||
<span class="bold">PMID: </span><a href="/pubmed/10712360" target="_blank">10712360</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Lymphangiectasis%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (152)</a></div><h3 class="subhead">Clinical prediction guides</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/30565236">CHAPLE syndrome uncovers the primary role of complement in a familial form of Waldmann's disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Ozen A</span><br />
|
||
<span class="medgenPMjournal">Immunol Rev</span>
|
||
2019 Jan;287(1):20-32.
|
||
doi: 10.1111/imr.12715.
|
||
<span class="bold">PMID: </span><a href="/pubmed/30565236" target="_blank">30565236</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/30701863">Primary lymphangiectasia of the gastrointestinal tract.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Esedov EM,
|
||
Abasova AS,
|
||
Akhmedova FD,
|
||
Musaeva LN</span><br />
|
||
<span class="medgenPMjournal">Ter Arkh</span>
|
||
2018 Apr 19;90(3):96-98.
|
||
doi: 10.26442/terarkh201890396-98.
|
||
<span class="bold">PMID: </span><a href="/pubmed/30701863" target="_blank">30701863</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27246594">Thoracic involvement in generalised lymphatic anomaly (or lymphangiomatosis).</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Luisi F,
|
||
Torre O,
|
||
Harari S</span><br />
|
||
<span class="medgenPMjournal">Eur Respir Rev</span>
|
||
2016 Jun;25(140):170-7.
|
||
doi: 10.1183/16000617.0018-2016.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27246594" target="_blank">27246594</a><a href="/pmc/articles/PMC9487238" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/17684071">Renal lymphangiectasia.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Ashraf K,
|
||
Raza SS,
|
||
Ashraf O,
|
||
Memon W,
|
||
Memon A,
|
||
Zubairi TA</span><br />
|
||
<span class="medgenPMjournal">Br J Radiol</span>
|
||
2007 Jun;80(954):e117-8.
|
||
doi: 10.1259/bjr/16931054.
|
||
<span class="bold">PMID: </span><a href="/pubmed/17684071" target="_blank">17684071</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/24294">Congenital testicular lymphangiectasis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Nistal M,
|
||
Paniagua R</span><br />
|
||
<span class="medgenPMjournal">Virchows Arch A Pathol Anat Histol</span>
|
||
1977 Dec 29;377(1):79-84.
|
||
doi: 10.1007/BF00432700.
|
||
<span class="bold">PMID: </span><a href="/pubmed/24294" target="_blank">24294</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Lymphangiectasis%22%20AND%20Clinical%20prediction%20guides%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (91)</a></div></div>
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<div class="nl"><a target="_blank" href="/pubmed/35570283">Hypomagnesemia in intestinal lymphangiectasia: a case report and review of the literature.</a></div>
|
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<div class="portlet_content ln"><span class="medgenPMauthor">Feng H,
|
||
Zou L,
|
||
Zhai X,
|
||
Zhang S,
|
||
Li J</span><br />
|
||
<span class="medgenPMjournal">BMC Gastroenterol</span>
|
||
2022 May 15;22(1):246.
|
||
doi: 10.1186/s12876-022-02318-6.
|
||
<span class="bold">PMID: </span><a href="/pubmed/35570283" target="_blank">35570283</a><a href="/pmc/articles/PMC9107688" target="_blank" class="PubMedFree">Free PMC Article</a></div>
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