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<!--
|
||
UID=87493
|
||
ConceptID=C0344987
|
||
-->
|
||
<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Bicuspid pulmonary valve</div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>87493</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C0344987</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Congenital Abnormality</dd></dl></div></div><table class="medgenTable"><tbody><tr><td><span class="bold">SNOMED CT: </span></td>
|
||
<td>Bicuspid pulmonary valve (253599005)</td></tr>
|
||
<tr><td colspan="2" class="small"> </td></tr><tr><td>HPO:</td>
|
||
<td><a target="_blank" title="Human Phenotype Ontology" href="https://hpo.jax.org/app/browse/term/HP:0005182">HP:0005182</a></td></tr>
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</tbody></table></div><div class="rprt-body jig-ncbiinpagenav" data-jigconfig="smoothScroll: false, gotoTopLink: true, gotoTopLinkText: '', gotoTopLinkAttrs: {'title': 'Go to the top of the page'},allHeadingLevels: ['h1'], topOfPageTOC: true, tocId: 'my-toc'"><div id="rprt-tabs-1" class="rprt-tab"><div id="tb-termsProp-1"><div class="leftCol mgCol"><div>
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<div class="portlet mgSection" id="ID_100">
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Definition">Definition</h1><a sid="100" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln">The presence of a bicuspid pulmonary valve. [from <a title="Human Phenotype Ontology" href="http://www.human-phenotype-ontology.org" class="defSource" target="_blank">HPO</a>]</div>
|
||
</div>
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|
||
<div class="portlet mgSection" id="ID_118">
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test, </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test, </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM, </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>, </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="chiclet_list"><span class="chiclet unavailable round" title="Clinical test">C</span><span class="chiclet unavailable round" title="Research Tests">R</span><span class="chiclet unavailable" title="OMIM">O</span><span class="chiclet unavailable" title="GeneReviews">G</span><span class="chiclet unavailable" title="ClinVar">V</span></span><span class="TLline">Bicuspid pulmonary valve</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="TLline"><a href="/medgen/116727" ref="tree=MeSH" title="MedGen record for Abnormality of the cardiovascular system">Abnormality of the cardiovascular system</a></span><ul><li><span class="TLline"><a href="/medgen/892473" ref="tree=MeSH" title="MedGen record for Abnormal cardiovascular system morphology">Abnormal cardiovascular system morphology</a></span><ul><li><span class="TLline"><a href="/medgen/6748" ref="tree=MeSH" title="MedGen record for Abnormal heart morphology">Abnormal heart morphology</a></span><ul><li><span class="TLline"><a href="/medgen/892837" ref="tree=MeSH" title="MedGen record for Abnormal heart valve morphology">Abnormal heart valve morphology</a></span><ul><li><span class="TLline"><a href="/medgen/488998" ref="tree=MeSH" title="MedGen record for Abnormal pulmonary valve morphology">Abnormal pulmonary valve morphology</a></span><ul><li><span class="TLline"><a href="/medgen/1623853" ref="tree=MeSH" title="MedGen record for Abnormal pulmonary valve cusp morphology">Abnormal pulmonary valve cusp morphology</a></span><ul><li><span class="matched_ds">Bicuspid pulmonary valve</span></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_112">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Conditions_with_this_feature">Conditions with this feature</h1><a sid="112" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln clinfeat">
|
||
<div class="divPopper rprt" id="rdis_382398"><div><strong>Loeys-Dietz syndrome 2</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>382398</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information."><span class="highlight" style="background-color:">C2674574</span></a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Loeys-Dietz syndrome (LDS) is characterized by vascular findings (cerebral, thoracic, and abdominal arterial aneurysms and/or dissections), skeletal manifestations (pectus excavatum or pectus carinatum, scoliosis, joint laxity, arachnodactyly, talipes equinovarus, and cervical spine malformation and/or instability), craniofacial features (hypertelorism, strabismus, bifid uvula / cleft palate, and craniosynostosis that can involve any sutures), and cutaneous findings (velvety and translucent skin, easy bruising, and dystrophic scars). Individuals with LDS are predisposed to widespread and aggressive arterial aneurysms and pregnancy-related complications including uterine rupture and death. Individuals with LDS can show a strong predisposition for allergic/inflammatory disease including asthma, eczema, and reactions to food or environmental allergens. There is also an increased incidence of gastrointestinal inflammation including eosinophilic esophagitis and gastritis or inflammatory bowel disease. Wide variation in the distribution and severity of clinical features can be seen in individuals with LDS, even among affected individuals within a family who have the same pathogenic variant.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/382398">Condition Record</a></div></div>
|
||
<div class="divPopper rprt" id="rdis_1646567"><div><strong>Loeys-Dietz syndrome 1</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>1646567</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C4551955</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Loeys-Dietz syndrome (LDS) is characterized by vascular findings (cerebral, thoracic, and abdominal arterial aneurysms and/or dissections), skeletal manifestations (pectus excavatum or pectus carinatum, scoliosis, joint laxity, arachnodactyly, talipes equinovarus, and cervical spine malformation and/or instability), craniofacial features (hypertelorism, strabismus, bifid uvula / cleft palate, and craniosynostosis that can involve any sutures), and cutaneous findings (velvety and translucent skin, easy bruising, and dystrophic scars). Individuals with LDS are predisposed to widespread and aggressive arterial aneurysms and pregnancy-related complications including uterine rupture and death. Individuals with LDS can show a strong predisposition for allergic/inflammatory disease including asthma, eczema, and reactions to food or environmental allergens. There is also an increased incidence of gastrointestinal inflammation including eosinophilic esophagitis and gastritis or inflammatory bowel disease. Wide variation in the distribution and severity of clinical features can be seen in individuals with LDS, even among affected individuals within a family who have the same pathogenic variant.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/1646567">Condition Record</a></div></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_1646567" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Loeys-Dietz syndrome 1</a></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_382398" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Loeys-Dietz syndrome 2</a></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_105">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/39212775">Endocarditis in Adult Congenital Heart Disease Patients: Prevention, Recognition, and Management.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Carvajal V,
|
||
Reyes FB,
|
||
Gonzalez D,
|
||
Schwartz M,
|
||
Whiltlow A,
|
||
Alegria JR</span><br />
|
||
<span class="medgenPMjournal">Curr Cardiol Rep</span>
|
||
2024 Sep;26(9):1031-1045.
|
||
Epub 2024 Aug 30
|
||
doi: 10.1007/s11886-024-02103-9.
|
||
<span class="bold">PMID: </span><a href="/pubmed/39212775" target="_blank">39212775</a><a href="/pmc/articles/PMC11379749" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/25441004">Current readings: long-term management of patients undergoing successful pediatric cardiac surgery.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">DiBardino DJ,
|
||
Jacobs JP</span><br />
|
||
<span class="medgenPMjournal">Semin Thorac Cardiovasc Surg</span>
|
||
2014 Summer;26(2):132-44.
|
||
Epub 2014 Aug 7
|
||
doi: 10.1053/j.semtcvs.2014.08.002.
|
||
<span class="bold">PMID: </span><a href="/pubmed/25441004" target="_blank">25441004</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/15285212">The Howard Gilman Foundation Lecture. Where have we come from and where are we going? Valve management past, present and future.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Perloff JK</span><br />
|
||
<span class="medgenPMjournal">Adv Cardiol</span>
|
||
2004;41:1-8.
|
||
doi: 10.1159/000079778.
|
||
<span class="bold">PMID: </span><a href="/pubmed/15285212" target="_blank">15285212</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(bicuspid%20pulmonary%20valve)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (9)</a></div></div>
|
||
</div>
|
||
<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
|
||
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
|
||
<div class="portlet mgSection" id="ID_103">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/37666352">Long-term Outcomes of Polytetrafluoroethylene Bicuspid Pulmonary Valve Replacement.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Kim ER,
|
||
Lee C,
|
||
Lee CH,
|
||
Cho SH</span><br />
|
||
<span class="medgenPMjournal">Ann Thorac Surg</span>
|
||
2024 Mar;117(3):535-541.
|
||
Epub 2023 Sep 4
|
||
doi: 10.1016/j.athoracsur.2023.08.019.
|
||
<span class="bold">PMID: </span><a href="/pubmed/37666352" target="_blank">37666352</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/35356973">The impact of a bicuspid pulmonary valve in the aortic position after arterial switch for transposition of the great arteries on neoaortic root dimension and function: a propensity score matched analysis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Jeon B,
|
||
Choi ES,
|
||
Kwon BS,
|
||
Yun TJ,
|
||
Cha SG,
|
||
Baek JS,
|
||
Yu JJ,
|
||
Park CS</span><br />
|
||
<span class="medgenPMjournal">Interact Cardiovasc Thorac Surg</span>
|
||
2022 Jun 1;34(6):1106-1112.
|
||
doi: 10.1093/icvts/ivac073.
|
||
<span class="bold">PMID: </span><a href="/pubmed/35356973" target="_blank">35356973</a><a href="/pmc/articles/PMC9159441" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/34482704">Native Bicuspid Pulmonary Valve in D-Loop Transposition of the Great Arteries: Outcomes of the Neo-Aortic Valve Function and Root Dilation After Arterial Switch Operation.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Irwin M,
|
||
Binney G,
|
||
Gauvreau K,
|
||
Emani S,
|
||
Blume ED,
|
||
Brown DW</span><br />
|
||
<span class="medgenPMjournal">J Am Heart Assoc</span>
|
||
2021 Sep 21;10(18):e021599.
|
||
Epub 2021 Sep 6
|
||
doi: 10.1161/JAHA.121.021599.
|
||
<span class="bold">PMID: </span><a href="/pubmed/34482704" target="_blank">34482704</a><a href="/pmc/articles/PMC8649553" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27083247">Polytetrafluoroethylene Bicuspid Pulmonary Valve Replacement: A 5-Year Experience in 119 Patients With Congenital Heart Disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Lee C,
|
||
Lee CH,
|
||
Kwak JG</span><br />
|
||
<span class="medgenPMjournal">Ann Thorac Surg</span>
|
||
2016 Jul;102(1):163-9.
|
||
Epub 2016 Apr 12
|
||
doi: 10.1016/j.athoracsur.2016.01.056.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27083247" target="_blank">27083247</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/21757366">Bicuspid pulmonary valve in transposition of the great arteries: impact on outcome.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Angeli E,
|
||
Gerelli S,
|
||
Beyler C,
|
||
Lamerain M,
|
||
Rochas B,
|
||
Bonnet D,
|
||
Vouhé P,
|
||
Raisky O</span><br />
|
||
<span class="medgenPMjournal">Eur J Cardiothorac Surg</span>
|
||
2012 Feb;41(2):248-55.
|
||
Epub 2011 Dec 12
|
||
doi: 10.1016/j.ejcts.2011.03.063.
|
||
<span class="bold">PMID: </span><a href="/pubmed/21757366" target="_blank">21757366</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Bicuspid%20pulmonary%20valve%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (20)</a></div><h3 class="subhead">Diagnosis</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/32350197">Pulmonary Artery Aneurysm Associated with Bicuspid Pulmonary Valve.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Izumida S,
|
||
Kawano H,
|
||
Tsuneto A,
|
||
Doi Y,
|
||
Maemura K</span><br />
|
||
<span class="medgenPMjournal">Intern Med</span>
|
||
2020 Aug 1;59(15):1867-1871.
|
||
Epub 2020 Apr 30
|
||
doi: 10.2169/internalmedicine.4415-20.
|
||
<span class="bold">PMID: </span><a href="/pubmed/32350197" target="_blank">32350197</a><a href="/pmc/articles/PMC7474982" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27083247">Polytetrafluoroethylene Bicuspid Pulmonary Valve Replacement: A 5-Year Experience in 119 Patients With Congenital Heart Disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Lee C,
|
||
Lee CH,
|
||
Kwak JG</span><br />
|
||
<span class="medgenPMjournal">Ann Thorac Surg</span>
|
||
2016 Jul;102(1):163-9.
|
||
Epub 2016 Apr 12
|
||
doi: 10.1016/j.athoracsur.2016.01.056.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27083247" target="_blank">27083247</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/25625455">Multimodality imaging of isolated bicuspid pulmonary valve leading to pulmonary stenosis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Öztürk C,
|
||
Demirkol S,
|
||
Aparcı M,
|
||
Sarı S,
|
||
Bozlar U,
|
||
Çelik T,
|
||
İyisoy A</span><br />
|
||
<span class="medgenPMjournal">Anatol J Cardiol</span>
|
||
2015 Jan 21;15(2):E5.
|
||
doi: 10.5152/akd.2015.5929.
|
||
<span class="bold">PMID: </span><a href="/pubmed/25625455" target="_blank">25625455</a><a href="/pmc/articles/PMC5337025" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/24771732">Prosthetic reconstruction of bicuspid pulmonary valve in tetralogy of Fallot.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Sasikumar N,
|
||
Ramanan S,
|
||
Rema KM,
|
||
Kumar RS,
|
||
Subramanyan R,
|
||
Cherian KM</span><br />
|
||
<span class="medgenPMjournal">Asian Cardiovasc Thorac Ann</span>
|
||
2014 May;22(4):436-41.
|
||
Epub 2013 Nov 13
|
||
doi: 10.1177/0218492313496416.
|
||
<span class="bold">PMID: </span><a href="/pubmed/24771732" target="_blank">24771732</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/6837541">Isolated congenital hypoplastic bicuspid pulmonary valve. Report of a case associated with seizure disorder in a 27-year-old man.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Okoye MI,
|
||
Mueller WF Jr,
|
||
Congdon DE,
|
||
Dewitt BL,
|
||
Blight CO,
|
||
Lau JM</span><br />
|
||
<span class="medgenPMjournal">Am J Forensic Med Pathol</span>
|
||
1983 Mar;4(1):79-83.
|
||
doi: 10.1097/00000433-198303000-00009.
|
||
<span class="bold">PMID: </span><a href="/pubmed/6837541" target="_blank">6837541</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Bicuspid%20pulmonary%20valve%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (24)</a></div><h3 class="subhead">Therapy</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/34482704">Native Bicuspid Pulmonary Valve in D-Loop Transposition of the Great Arteries: Outcomes of the Neo-Aortic Valve Function and Root Dilation After Arterial Switch Operation.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Irwin M,
|
||
Binney G,
|
||
Gauvreau K,
|
||
Emani S,
|
||
Blume ED,
|
||
Brown DW</span><br />
|
||
<span class="medgenPMjournal">J Am Heart Assoc</span>
|
||
2021 Sep 21;10(18):e021599.
|
||
Epub 2021 Sep 6
|
||
doi: 10.1161/JAHA.121.021599.
|
||
<span class="bold">PMID: </span><a href="/pubmed/34482704" target="_blank">34482704</a><a href="/pmc/articles/PMC8649553" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/31292191">Progression of aortic root dilatation and aortic valve regurgitation after the arterial switch operation.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">van der Palen RLF,
|
||
van der Bom T,
|
||
Dekker A,
|
||
Tsonaka R,
|
||
van Geloven N,
|
||
Kuipers IM,
|
||
Konings TC,
|
||
Rammeloo LAJ,
|
||
Ten Harkel ADJ,
|
||
Jongbloed MRM,
|
||
Koolbergen DR,
|
||
Mulder BJM,
|
||
Hazekamp MG,
|
||
Blom NA</span><br />
|
||
<span class="medgenPMjournal">Heart</span>
|
||
2019 Nov;105(22):1732-1740.
|
||
Epub 2019 Jul 10
|
||
doi: 10.1136/heartjnl-2019-315157.
|
||
<span class="bold">PMID: </span><a href="/pubmed/31292191" target="_blank">31292191</a><a href="/pmc/articles/PMC6855793" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/24771732">Prosthetic reconstruction of bicuspid pulmonary valve in tetralogy of Fallot.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Sasikumar N,
|
||
Ramanan S,
|
||
Rema KM,
|
||
Kumar RS,
|
||
Subramanyan R,
|
||
Cherian KM</span><br />
|
||
<span class="medgenPMjournal">Asian Cardiovasc Thorac Ann</span>
|
||
2014 May;22(4):436-41.
|
||
Epub 2013 Nov 13
|
||
doi: 10.1177/0218492313496416.
|
||
<span class="bold">PMID: </span><a href="/pubmed/24771732" target="_blank">24771732</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/18154805">Neoaortic bicuspid valve in arterial switch operation: mid-term follow-up.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Khan SM,
|
||
Sallehuddin AB,
|
||
Al-Bulbul ZR,
|
||
Al-Halees ZY</span><br />
|
||
<span class="medgenPMjournal">Ann Thorac Surg</span>
|
||
2008 Jan;85(1):179-84.
|
||
doi: 10.1016/j.athoracsur.2007.07.012.
|
||
<span class="bold">PMID: </span><a href="/pubmed/18154805" target="_blank">18154805</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/16181883">Tetralogy of Fallot: results of a pulmonary valve-sparing strategy.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Stewart RD,
|
||
Backer CL,
|
||
Young L,
|
||
Mavroudis C</span><br />
|
||
<span class="medgenPMjournal">Ann Thorac Surg</span>
|
||
2005 Oct;80(4):1431-8; discussion 1438-9.
|
||
doi: 10.1016/j.athoracsur.2005.04.016.
|
||
<span class="bold">PMID: </span><a href="/pubmed/16181883" target="_blank">16181883</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Bicuspid%20pulmonary%20valve%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (7)</a></div><h3 class="subhead">Prognosis</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/37666352">Long-term Outcomes of Polytetrafluoroethylene Bicuspid Pulmonary Valve Replacement.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Kim ER,
|
||
Lee C,
|
||
Lee CH,
|
||
Cho SH</span><br />
|
||
<span class="medgenPMjournal">Ann Thorac Surg</span>
|
||
2024 Mar;117(3):535-541.
|
||
Epub 2023 Sep 4
|
||
doi: 10.1016/j.athoracsur.2023.08.019.
|
||
<span class="bold">PMID: </span><a href="/pubmed/37666352" target="_blank">37666352</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/35356973">The impact of a bicuspid pulmonary valve in the aortic position after arterial switch for transposition of the great arteries on neoaortic root dimension and function: a propensity score matched analysis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Jeon B,
|
||
Choi ES,
|
||
Kwon BS,
|
||
Yun TJ,
|
||
Cha SG,
|
||
Baek JS,
|
||
Yu JJ,
|
||
Park CS</span><br />
|
||
<span class="medgenPMjournal">Interact Cardiovasc Thorac Surg</span>
|
||
2022 Jun 1;34(6):1106-1112.
|
||
doi: 10.1093/icvts/ivac073.
|
||
<span class="bold">PMID: </span><a href="/pubmed/35356973" target="_blank">35356973</a><a href="/pmc/articles/PMC9159441" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/29340729">Pulmonary Valve Morphology in Patients with Bicuspid Aortic Valves.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Koenraadt WMC,
|
||
Bartelings MM,
|
||
Gittenberger-de Groot AC,
|
||
Bökenkamp R,
|
||
DeRuiter MC,
|
||
Schalij MJ,
|
||
Jongbloed MRM</span><br />
|
||
<span class="medgenPMjournal">Pediatr Cardiol</span>
|
||
2018 Apr;39(4):690-694.
|
||
Epub 2018 Jan 16
|
||
doi: 10.1007/s00246-018-1807-x.
|
||
<span class="bold">PMID: </span><a href="/pubmed/29340729" target="_blank">29340729</a><a href="/pmc/articles/PMC5895682" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/27083247">Polytetrafluoroethylene Bicuspid Pulmonary Valve Replacement: A 5-Year Experience in 119 Patients With Congenital Heart Disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Lee C,
|
||
Lee CH,
|
||
Kwak JG</span><br />
|
||
<span class="medgenPMjournal">Ann Thorac Surg</span>
|
||
2016 Jul;102(1):163-9.
|
||
Epub 2016 Apr 12
|
||
doi: 10.1016/j.athoracsur.2016.01.056.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27083247" target="_blank">27083247</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/24771732">Prosthetic reconstruction of bicuspid pulmonary valve in tetralogy of Fallot.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Sasikumar N,
|
||
Ramanan S,
|
||
Rema KM,
|
||
Kumar RS,
|
||
Subramanyan R,
|
||
Cherian KM</span><br />
|
||
<span class="medgenPMjournal">Asian Cardiovasc Thorac Ann</span>
|
||
2014 May;22(4):436-41.
|
||
Epub 2013 Nov 13
|
||
doi: 10.1177/0218492313496416.
|
||
<span class="bold">PMID: </span><a href="/pubmed/24771732" target="_blank">24771732</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Bicuspid%20pulmonary%20valve%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (19)</a></div><h3 class="subhead">Clinical prediction guides</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/35356973">The impact of a bicuspid pulmonary valve in the aortic position after arterial switch for transposition of the great arteries on neoaortic root dimension and function: a propensity score matched analysis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Jeon B,
|
||
Choi ES,
|
||
Kwon BS,
|
||
Yun TJ,
|
||
Cha SG,
|
||
Baek JS,
|
||
Yu JJ,
|
||
Park CS</span><br />
|
||
<span class="medgenPMjournal">Interact Cardiovasc Thorac Surg</span>
|
||
2022 Jun 1;34(6):1106-1112.
|
||
doi: 10.1093/icvts/ivac073.
|
||
<span class="bold">PMID: </span><a href="/pubmed/35356973" target="_blank">35356973</a><a href="/pmc/articles/PMC9159441" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/30770571">Criss-cross heart with double-outlet right ventricle, subpulmonary ventricular septal defect, and bicuspid pulmonary valve.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Ren S,
|
||
Ma C,
|
||
Li S</span><br />
|
||
<span class="medgenPMjournal">J Clin Ultrasound</span>
|
||
2019 Jun;47(5):315-318.
|
||
Epub 2019 Feb 15
|
||
doi: 10.1002/jcu.22700.
|
||
<span class="bold">PMID: </span><a href="/pubmed/30770571" target="_blank">30770571</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/29340729">Pulmonary Valve Morphology in Patients with Bicuspid Aortic Valves.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Koenraadt WMC,
|
||
Bartelings MM,
|
||
Gittenberger-de Groot AC,
|
||
Bökenkamp R,
|
||
DeRuiter MC,
|
||
Schalij MJ,
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||
Jongbloed MRM</span><br />
|
||
<span class="medgenPMjournal">Pediatr Cardiol</span>
|
||
2018 Apr;39(4):690-694.
|
||
Epub 2018 Jan 16
|
||
doi: 10.1007/s00246-018-1807-x.
|
||
<span class="bold">PMID: </span><a href="/pubmed/29340729" target="_blank">29340729</a><a href="/pmc/articles/PMC5895682" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/28881023">Double-outlet left ventricle with a bicuspid pulmonary valve and aortic coarctation.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Sun F,
|
||
Fan M,
|
||
Huang L,
|
||
Ren W,
|
||
Li D</span><br />
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||
<span class="medgenPMjournal">J Clin Ultrasound</span>
|
||
2018 May;46(4):265-268.
|
||
Epub 2017 Sep 7
|
||
doi: 10.1002/jcu.22520.
|
||
<span class="bold">PMID: </span><a href="/pubmed/28881023" target="_blank">28881023</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/21757366">Bicuspid pulmonary valve in transposition of the great arteries: impact on outcome.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Angeli E,
|
||
Gerelli S,
|
||
Beyler C,
|
||
Lamerain M,
|
||
Rochas B,
|
||
Bonnet D,
|
||
Vouhé P,
|
||
Raisky O</span><br />
|
||
<span class="medgenPMjournal">Eur J Cardiothorac Surg</span>
|
||
2012 Feb;41(2):248-55.
|
||
Epub 2011 Dec 12
|
||
doi: 10.1016/j.ejcts.2011.03.063.
|
||
<span class="bold">PMID: </span><a href="/pubmed/21757366" target="_blank">21757366</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Bicuspid%20pulmonary%20valve%22%20AND%20Clinical%20prediction%20guides%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (15)</a></div></div>
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