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<meta name="keywords" content="C0392482, absence of interatrial septum, common atrium, congenital abnormality, congenital absence of atrial septum, cor triloculare biventriculare, single atrium, autosomal dominant, autosomal recessive, birth defects, chromosomal disease, chromosome, clinical features, clinical findings, clinical genetics, clinical recommendations, clinvar, congenital chromosomal disease, consumer genetic resources, cytogenetic location, disease characteristics, disease definitions, disease descriptions, disease ontology, disease synonyms, disease vocabulary, dysmorphology, entrez, familial disease, gene, gene-disease relationship, genereviews, genetic disease, genetic disorder, genetic terminology, genetic testing registry, genetics home reference, genomic disease, gtr, hereditary disease, heritable disease, hpo, human phenotype ontology, inherited disease, management guidelines, maternal inheritance, medgen, medical genetics, medical subject headings, mesh, mitochondrial inheritance, mode of inheritance, national center for biotechnology information, national institutes of health, national library of medicine, ncbi, nih, nlm, omim, ordo, orphanet, paternal inheritance, phenome, position statements, professional practice guidelines, rare disease, reference sequence, refseq, snomed ct, syndrome, undiagnosed diseases, x-linked recessive" /><meta name="description" content="Complete absence of the interatrial septum with common atrioventricular valve and two atrioventricular connections." /><meta name="robots" content="index,nofollow,noarchive" />
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<!--
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<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Common atrium</div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>488886</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C0392482</a></dd><dt><span class="dotprefix"></span></dt><dd>Congenital Abnormality</dd></dl></div></div><table class="medgenTable"><tbody><tr><td>Synonyms:</td>
<td>Absence of interatrial septum; Single atrium</td></tr>
<tr><td><span class="bold">SNOMED CT: </span></td>
<td>Congenital absence of atrial septum (253276007); Common atrium (253276007); Cor triloculare biventriculare (253276007)</td></tr>
<tr><td colspan="2" class="small"> </td></tr><tr><td>HPO:</td>
<td><a target="_blank" title="Human Phenotype Ontology" href="https://hpo.jax.org/app/browse/term/HP:0011565">HP:0011565</a></td></tr>
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Definition">Definition</h1><a sid="100" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln">Complete absence of the interatrial septum with common atrioventricular valve and two atrioventricular connections. [from <a title="Human Phenotype Ontology" href="http://www.human-phenotype-ontology.org" class="defSource" target="_blank">HPO</a>]</div>
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<div class="portlet mgSection" id="ID_118">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test,  </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test,  </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM,  </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>,  </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar  </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="TLline">Common atrium</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="TLline"><a href="/medgen/232130" ref="tree=MeSH" title="MedGen record for Disorder by Site">Disorder by Site</a></span><ul><li><span class="TLline"><a href="/medgen/2848" ref="tree=MeSH" title="MedGen record for Disorder of cardiovascular system">Disorder of cardiovascular system</a></span><ul><li><span class="TLline"><a href="/medgen/116727" ref="tree=MeSH" title="MedGen record for Abnormality of the cardiovascular system">Abnormality of the cardiovascular system</a></span><ul><li><span class="TLline"><a href="/medgen/892473" ref="tree=MeSH" title="MedGen record for Abnormal cardiovascular system morphology">Abnormal cardiovascular system morphology</a></span><ul><li><span class="TLline"><a href="/medgen/6748" ref="tree=MeSH" title="MedGen record for Abnormal heart morphology">Abnormal heart morphology</a></span><ul><li><span class="TLline"><a href="/medgen/870789" ref="tree=MeSH" title="MedGen record for Abnormal cardiac atrium morphology">Abnormal cardiac atrium morphology</a></span><ul><li><span class="matched_ds">Common atrium</span></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
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<div class="portlet mgSection" id="ID_112">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Conditions_with_this_feature">Conditions with this feature</h1><a sid="112" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln clinfeat">
<div class="divPopper rprt" id="rdis_8584"><div><strong>Ellis-van Creveld syndrome</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>8584</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C0013903</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Ellis-van Creveld (EVC) syndrome is characterized by postaxial polydactyly of the hands, disproportionate short stature with short limbs, dystrophic and/or hypoplastic nails, dental and oral manifestations, congenital heart disease, and radiologic abnormalities (narrow chest, short ribs, short tubular bones, bulbous ends of the proximal ulnae and distal radii, carpal and metacarpal fusions, cone-shaped epiphyses of phalanges, small iliac crests, acetabular spur projections [trident ilia], and lateral slanting of the tibial plateau). Other less common and more variable features include postaxial polydactyly of the feet, upper lip defect, and developmental delay.</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/8584">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_120524"><div><strong>Holt-Oram syndrome</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>120524</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information."><span class="highlight" style="background-color:">C0265264</span></a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Holt-Oram syndrome (HOS) is characterized by upper-limb defects, congenital heart malformation, and cardiac conduction disease. Upper-limb malformations may be unilateral, bilateral/symmetric, or bilateral/asymmetric and can range from triphalangeal or absent thumb(s) to phocomelia. Other upper-limb malformations can include unequal arm length caused by aplasia or hypoplasia of the radius, fusion or anomalous development of the carpal and thenar bones, abnormal forearm pronation and supination, abnormal opposition of the thumb, sloping shoulders, and restriction of shoulder joint movement. An abnormal carpal bone is present in all affected individuals and may be the only evidence of disease. A congenital heart malformation is present in 75% of individuals with HOS and most commonly involves the septum. Atrial septal defect and ventricular septal defect can vary in number, size, and location. Complex congenital heart malformations can also occur in individuals with HOS. Individuals with HOS with or without a congenital heart malformation are at risk for cardiac conduction disease. While individuals may present at birth with sinus bradycardia and first-degree atrioventricular (AV) block, AV block can progress unpredictably to a higher grade including complete heart block with and without atrial fibrillation.</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/120524">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_373234"><div><strong>Meacham syndrome</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>373234</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C1837026</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">WT1 disorder is characterized by congenital/infantile or childhood onset of steroid-resistant nephrotic syndrome (SRNS), a progressive glomerulopathy that does not respond to standard steroid therapy. Additional common findings can include disorders of testicular development (with or without abnormalities of the external genitalia and/or müllerian structures) and Wilms tumor. Less common findings are congenital anomalies of the kidney and urinary tract (CAKUT) and gonadoblastoma. While various combinations of renal and other findings associated with a WT1 pathogenic variant were designated as certain syndromes in the past, those designations are now recognized to be part of a phenotypic continuum and are no longer clinically helpful.</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/373234">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_336609"><div><strong>Heterotaxy, visceral, 1, X-linked</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>336609</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C1844020</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Heterotaxy&#13; Heterotaxy ('heter' meaning 'other' and 'taxy' meaning 'arrangement'), or situs ambiguus, is a developmental condition characterized by randomization of the placement of visceral organs, including the heart, lungs, liver, spleen, and stomach. The organs are oriented randomly with respect to the left-right axis and with respect to one another (Srivastava, 1997). Heterotaxy is a clinically and genetically heterogeneous disorder.&#13; Multiple Types of Congenital Heart Defects&#13; Congenital heart defects (CHTD) are among the most common congenital defects, occurring with an incidence of 8/1,000 live births. The etiology of CHTD is complex, with contributions from environmental exposure, chromosomal abnormalities, and gene defects. Some patients with CHTD also have cardiac arrhythmias, which may be due to the anatomic defect itself or to surgical interventions (summary by van de Meerakker et al., 2011).&#13; Reviews&#13; Obler et al. (2008) reviewed published cases of double-outlet right ventricle and discussed etiology and associations.&#13; Genetic Heterogeneity of Visceral Heterotaxy&#13; See also HTX2 (605376), caused by mutation in the CFC1 gene (605194) on chromosome 2q21; HTX3 (606325), which maps to chromosome 6q21; HTX4 (613751), caused by mutation in the ACVR2B gene (602730) on chromosome 3p22; HTX5 (270100), caused by mutation in the NODAL gene (601265) on chromosome 10q22; HTX6 (614779), caused by mutation in the CCDC11 gene (614759) on chromosome 18q21; HTX7 (616749), caused by mutation in the MMP21 gene (608416) on chromosome 10q26; HTX8 (617205), caused by mutation in the PKD1L1 gene (609721) on chromosome 7p12; HTX9 (618948), caused by mutation in the MNS1 gene (610766) on chromosome 15q21; HTX10 (619607), caused by mutation in the CFAP52 gene (609804) on chromosome 17p13; HTX11 (619608), caused by mutation in the CFAP45 gene (605152) on chromosome 1q23; HTX12 (619702), caused by mutation in the CIROP gene (619703) on chromosome 14q11; HTX13 (621079), caused by mutation in the DAND5 gene (609068) on chromosome 19p13; and HTX14 (621080), caused by mutation in the CIROZ gene (619700) on chromosome 1p36.&#13; Genetic Heterogeneity of Multiple Types of Congenital Heart Defects&#13; An X-linked form of CHTD, CHTD1, is caused by mutation in the ZIC3 gene on chromosome Xq26. CHTD2 (614980) is caused by mutation in the TAB2 gene (605101) on chromosome 6q25. A form of nonsyndromic congenital heart defects associated with cardiac rhythm and conduction disturbances (CHTD3; 614954) has been mapped to chromosome 9q31. CHTD4 (615779) is caused by mutation in the NR2F2 gene (107773) on chromosome 15q26. CHTD5 (617912) is caused by mutation in the GATA5 gene (611496) on chromosome 20q13. CHTD6 (613854) is caused by mutation in the GDF1 gene (602880) on chromosome 19p13. CHTD7 (618780) is caused by mutation in the FLT4 gene (136352) on chromosome 5q35. CHTD8 (619657) is caused by mutation in the SMAD2 gene (601366) on chromosome 18q21. CHTD9 (620294) is caused by mutation in the PLXND1 gene (604282) on chromosome 3q22.</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/336609">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_436265"><div><strong>Faciocardiomelic syndrome</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>436265</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C2674798</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove nowrap">See: <a href="/medgen/436265">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_462407"><div><strong>Heterotaxy, visceral, 4, autosomal</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>462407</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C3151057</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Heterotaxy ('heter' meaning 'other' and 'taxy' meaning 'arrangement'), or situs ambiguus, is a developmental condition characterized by randomization of the placement of visceral organs, including the heart, lungs, liver, spleen, and stomach. The organs are oriented randomly with respect to the left-right axis and with respect to one another (Srivastava, 1997). Heterotaxy is a clinically and genetically heterogeneous disorder.&#13; For a discussion of the genetic heterogeneity of visceral heterotaxy, see HTX1 (306955).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/462407">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_465274"><div><strong>Right atrial isomerism</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>465274</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C3178806</a></dd><dt><span class="dotprefix"></span></dt><dd>Congenital Abnormality</dd></dl></div></div></div>
<div class="spaceAbove">Right atrial isomerism is characterized by bilateral triangular, morphologically right atrial, appendages, both joining the atrial chamber along a broad front with internal terminal crest.</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/465274">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_766590"><div><strong>Heterotaxy, visceral, 6, autosomal</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>766590</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C3553676</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Visceral heterotaxy-6 (HTX6) is characterized by dextrocardia with or without accompanying complex cardiovascular defects, as well as variable manifestations of visceral heterotaxy, including situs inversus totalis (Perles et al., 2012).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/766590">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_902629"><div><strong>Heterotaxy, visceral, 7, autosomal</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>902629</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C4225217</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Visceral heterotaxy-7 (HTX7) is an autosomal recessive developmental disorder characterized by complex congenital heart malformations and/or situs inversus and caused by defects in the normal left-right asymmetric positioning of internal organs. The phenotype is variable (summary by Guimier et al., 2015).&#13; For a discussion of the genetic heterogeneity of visceral heterotaxy, see HTX1 (306955).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/902629">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_1731253"><div><strong>Cardioacrofacial dysplasia 2</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>1731253</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C5436886</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Cardioacrofacial dysplasia-2 (CAFD2) is characterized by congenital cardiac defects, primarily common atrium or atrioventricular septal defect; limb anomalies, including short limbs, brachydactyly, and postaxial polydactyly; and dysmorphic facial features. Developmental delay of variable severity has also been observed (Palencia-Campos et al., 2020).&#13; For a discussion of genetic heterogeneity of CAFD, see CAFD1 (619142).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/1731253">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_1794200"><div><strong>Biliary, renal, neurologic, and skeletal syndrome</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>1794200</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C5561990</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Biliary, renal, neurologic, and skeletal syndrome (BRENS) is an autosomal recessive complex ciliopathy with multisystemic manifestations. The most common presentation is severe neonatal cholestasis that progresses to liver fibrosis and cirrhosis. Most patients have additional clinical features suggestive of a ciliopathy, including postaxial polydactyly, hydrocephalus, retinal abnormalities, and situs inversus. Additional features of the syndrome may include congenital cardiac defects, echogenic kidneys with renal failure, ocular abnormalities, joint hyperextensibility, and dysmorphic facial features. Some patients have global developmental delay. Brain imaging typically shows dilated ventricles, hypomyelination, and white matter abnormalities, although some patients have been described with abnormal pituitary development (summary by Shaheen et al., 2020 and David et al., 2020).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/1794200">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_1803695"><div><strong>Heterotaxy, visceral, 12, autosomal</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>1803695</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C5676898</a></dd><dt><span class="dotprefix"></span></dt><dd>Congenital Abnormality</dd></dl></div></div></div>
<div class="spaceAbove">Visceral heterotaxy-12 (HTX12) is an embryonic developmental disorder characterized by defects in the asymmetric positioning of visceral organs across the left-right axis, known as laterality defects. The phenotype is highly variable, ranging from complete organ reversal (situs inversus totalis) to selective misarrangement of organs (situs ambiguus) such as the liver, spleen, and pancreas. The disorder is often associated with dextrocardia or variable complex congenital heart defects. Early death may occur in the most severe cases (summary by Szenker-Ravi et al., 2022).&#13; For a discussion of the genetic heterogeneity of visceral heterotaxy, see HTX1 (306955).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/1803695">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_1851509"><div><strong>Ciliary dyskinesia, primary, 53</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>1851509</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C5882728</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Primary ciliary dyskinesia-53 (CILD53) is an autosomal recessive disorder characterized by randomization of the left-right body asymmetry and respiratory symptoms (Hjeij et al., 2023).&#13; For a discussion of genetic heterogeneity of primary ciliary dyskinesia, see CILD1 (244400).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/1851509">Condition Record</a></div></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_1794200" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Biliary, renal, neurologic, and skeletal syndrome</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_1731253" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Cardioacrofacial dysplasia 2</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_1851509" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Ciliary dyskinesia, primary, 53</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_8584" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Ellis-van Creveld syndrome</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_436265" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Faciocardiomelic syndrome</a></div><div class="jig-moreless" data-jigconfig="class: 'moveDown', moreText: 'See full list (13)', lessText: 'Show less', nodeBefore: 0"><span id="clinMore">
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_336609" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Heterotaxy, visceral, 1, X-linked</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_1803695" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Heterotaxy, visceral, 12, autosomal</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_462407" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Heterotaxy, visceral, 4, autosomal</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_766590" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Heterotaxy, visceral, 6, autosomal</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_902629" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Heterotaxy, visceral, 7, autosomal</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_120524" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Holt-Oram syndrome</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_373234" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Meacham syndrome</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_465274" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Right atrial isomerism</a></div></span></div></div>
</div>
<div class="portlet mgSection" id="ID_105">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
<div class="nl"><a target="_blank" href="/pubmed/37452811">AGA Clinical Practice Update on Evaluation and Management of Belching, Abdominal Bloating, and Distention: Expert Review.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Moshiree B,
Drossman D,
Shaukat A</span><br />
<span class="medgenPMjournal">Gastroenterology</span>
2023 Sep;165(3):791-800.e3.
Epub 2023 Jul 13
doi: 10.1053/j.gastro.2023.04.039.
<span class="bold">PMID: </span><a href="/pubmed/37452811" target="_blank">37452811</a></div>
<div class="nl"><a target="_blank" href="/pubmed/35027110">Management of Atrial Fibrillation in Patients 75 Years and Older: JACC State-of-the-Art Review.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Volgman AS,
Nair G,
Lyubarova R,
Merchant FM,
Mason P,
Curtis AB,
Wenger NK,
Aggarwal NT,
Kirkpatrick JN,
Benjamin EJ</span><br />
<span class="medgenPMjournal">J Am Coll Cardiol</span>
2022 Jan 18;79(2):166-179.
doi: 10.1016/j.jacc.2021.10.037.
<span class="bold">PMID: </span><a href="/pubmed/35027110" target="_blank">35027110</a></div>
<div class="nl"><a target="_blank" href="/pubmed/33929376">ACG Clinical Guideline: Diagnosis and Management of Idiosyncratic Drug-Induced Liver Injury.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Chalasani NP,
Maddur H,
Russo MW,
Wong RJ,
Reddy KR;
Practice Parameters Committee of the American College of Gastroenterology</span><br />
<span class="medgenPMjournal">Am J Gastroenterol</span>
2021 May 1;116(5):878-898.
doi: 10.14309/ajg.0000000000001259.
<span class="bold">PMID: </span><a href="/pubmed/33929376" target="_blank">33929376</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(common%20atrium)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (229)</a></div></div>
</div>
<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
<div class="portlet mgSection" id="ID_103">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
<div class="nl"><a target="_blank" href="/pubmed/30431572">Common atrium and the associated malformations: Evaluation by low-dose dual-source computed tomography.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Zhang Y,
Yang ZG,
Yang MX,
Shi K,
Li R,
Diao KY,
Guo YK</span><br />
<span class="medgenPMjournal">Medicine (Baltimore)</span>
2018 Nov;97(46):e12983.
doi: 10.1097/MD.0000000000012983.
<span class="bold">PMID: </span><a href="/pubmed/30431572" target="_blank">30431572</a><a href="/pmc/articles/PMC6257481" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30070188">Utilisation of blood and blood products during open heart surgery in a low-income country: our local experience in 3 years.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Nwafor IA,
Arua OA,
Eze JC,
Ezemba N,
Nwafor MN</span><br />
<span class="medgenPMjournal">Cardiol Young</span>
2018 Nov;28(11):1289-1294.
Epub 2018 Aug 2
doi: 10.1017/S1047951118001269.
<span class="bold">PMID: </span><a href="/pubmed/30070188" target="_blank">30070188</a></div>
<div class="nl"><a target="_blank" href="/pubmed/23360092">Coincidence of total anomalous pulmonary venous drainage to the superior vena cava, common atrium, and single ventricle: a very rare condition.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Nabati M,
Bagheri B,
Habibi V</span><br />
<span class="medgenPMjournal">Echocardiography</span>
2013 Apr;30(4):E98-101.
Epub 2013 Jan 30
doi: 10.1111/echo.12141.
<span class="bold">PMID: </span><a href="/pubmed/23360092" target="_blank">23360092</a></div>
<div class="nl"><a target="_blank" href="/pubmed/19022036">Cor triatriatum associated with ASD and common atrium in 7-month-old with tachypnea and failure to thrive.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">McLean MK,
Kung GC,
Polimenakos A,
Wells WJ,
Reemtsen BL</span><br />
<span class="medgenPMjournal">Ann Thorac Surg</span>
2008 Dec;86(6):1999.
doi: 10.1016/j.athoracsur.2008.01.037.
<span class="bold">PMID: </span><a href="/pubmed/19022036" target="_blank">19022036</a></div>
<div class="nl"><a target="_blank" href="/pubmed/18022916">Creation of a coronary sinus to atrial communication in coronary sinus ostial atresia improves cardiac function after Fontan.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Petit CJ,
Webb GD,
Rome JJ</span><br />
<span class="medgenPMjournal">Catheter Cardiovasc Interv</span>
2007 Nov 15;70(6):897-9.
doi: 10.1002/ccd.21264.
<span class="bold">PMID: </span><a href="/pubmed/18022916" target="_blank">18022916</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Common%20atrium%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (34)</a></div><h3 class="subhead">Diagnosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/26363758">Common atrium: A rare congenital heart anomaly.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Demirelli S,
Fırtına S,
Ermiş E,
İnci S</span><br />
<span class="medgenPMjournal">Turk Kardiyol Dern Ars</span>
2015 Sep;43(6):579.
doi: 10.5543/tkda.2015.93027.
<span class="bold">PMID: </span><a href="/pubmed/26363758" target="_blank">26363758</a></div>
<div class="nl"><a target="_blank" href="/pubmed/19022036">Cor triatriatum associated with ASD and common atrium in 7-month-old with tachypnea and failure to thrive.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">McLean MK,
Kung GC,
Polimenakos A,
Wells WJ,
Reemtsen BL</span><br />
<span class="medgenPMjournal">Ann Thorac Surg</span>
2008 Dec;86(6):1999.
doi: 10.1016/j.athoracsur.2008.01.037.
<span class="bold">PMID: </span><a href="/pubmed/19022036" target="_blank">19022036</a></div>
<div class="nl"><a target="_blank" href="/pubmed/15053799">Definitive diagnosis of cor triatriatum with common atrium by three-dimensional transesophageal echocardiography in an adult.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Baweja G,
Nanda NC,
Kirklin JK</span><br />
<span class="medgenPMjournal">Echocardiography</span>
2004 Apr;21(3):303-6.
doi: 10.1111/j.0742-2822.2004.03095.x.
<span class="bold">PMID: </span><a href="/pubmed/15053799" target="_blank">15053799</a></div>
<div class="nl"><a target="_blank" href="/pubmed/4746356">Successful repair of complete atrioventricular canal associated with dextroversion, common atrium, and total anomalous systemic venous return.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Danielson GK,
McMullan MH,
Kinsley RH,
DuShane JW</span><br />
<span class="medgenPMjournal">J Thorac Cardiovasc Surg</span>
1973 Nov;66(5):817-22.
<span class="bold">PMID: </span><a href="/pubmed/4746356" target="_blank">4746356</a></div>
<div class="nl"><a target="_blank" href="/pubmed/4711870">Electrocardiographic and angiographic features of common atrium.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Hung JS,
Ritter DG,
Feldt RH,
Kincaid OW</span><br />
<span class="medgenPMjournal">Chest</span>
1973 Jun;63(6):970-5.
doi: 10.1378/chest.63.6.970.
<span class="bold">PMID: </span><a href="/pubmed/4711870" target="_blank">4711870</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Common%20atrium%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (52)</a></div><h3 class="subhead">Therapy</h3>
<div class="nl"><a target="_blank" href="/pubmed/27556319">Major Intrahepatic Veno-Venous Fistula after Fontan Operation Treated by Transcatheter Implantation of Amplatzer Septal Occluder through Internal Jugular Vein.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Guzeltas A,
Tanidir IC,
Saygi M</span><br />
<span class="medgenPMjournal">Braz J Cardiovasc Surg</span>
2016 Apr;31(2):174-7.
doi: 10.5935/1678-9741.20160020.
<span class="bold">PMID: </span><a href="/pubmed/27556319" target="_blank">27556319</a><a href="/pmc/articles/PMC5062733" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/16432106">A pitfall in ligation of intrahepatic shunting after Fontan type operation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Ikeda A,
Hiramatsu Y,
Horigome H,
Hori T,
Noma M,
Sakakibara Y</span><br />
<span class="medgenPMjournal">Asian Cardiovasc Thorac Ann</span>
2006 Feb;14(1):e6-8.
doi: 10.1177/021849230601400130.
<span class="bold">PMID: </span><a href="/pubmed/16432106" target="_blank">16432106</a></div>
<div class="nl"><a target="_blank" href="/pubmed/11816632">Cardiac rhythm disturbances in patients with left atrial isomerism.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Wu MH,
Wang JK,
Lin JL,
Lai LP,
Lue HC,
Hsieh FJ</span><br />
<span class="medgenPMjournal">Pacing Clin Electrophysiol</span>
2001 Nov;24(11):1631-8.
doi: 10.1046/j.1460-9592.2001.01631.x.
<span class="bold">PMID: </span><a href="/pubmed/11816632" target="_blank">11816632</a></div>
<div class="nl"><a target="_blank" href="/pubmed/10430527">Atrial isomerism: a surgical experience.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Sinzobahamvya N,
Arenz C,
Brecher AM,
Urban AE</span><br />
<span class="medgenPMjournal">Cardiovasc Surg</span>
1999 Jun;7(4):436-42.
doi: 10.1016/s0967-2109(98)00151-3.
<span class="bold">PMID: </span><a href="/pubmed/10430527" target="_blank">10430527</a></div>
<div class="nl"><a target="_blank" href="/pubmed/7254976">Congenital asplenia: immunologic assessment and a clinical review of eight surviving patients.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Biggar WD,
Ramirez RA,
Rose V</span><br />
<span class="medgenPMjournal">Pediatrics</span>
1981 Apr;67(4):548-51.
<span class="bold">PMID: </span><a href="/pubmed/7254976" target="_blank">7254976</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Common%20atrium%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (6)</a></div><h3 class="subhead">Prognosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/30070188">Utilisation of blood and blood products during open heart surgery in a low-income country: our local experience in 3 years.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Nwafor IA,
Arua OA,
Eze JC,
Ezemba N,
Nwafor MN</span><br />
<span class="medgenPMjournal">Cardiol Young</span>
2018 Nov;28(11):1289-1294.
Epub 2018 Aug 2
doi: 10.1017/S1047951118001269.
<span class="bold">PMID: </span><a href="/pubmed/30070188" target="_blank">30070188</a></div>
<div class="nl"><a target="_blank" href="/pubmed/20392685">64-Slice MDCT imaging of endocardial cushion defect associated with other cardiac and extracardiac abnormalities.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Oyama N,
Goto D,
Sasaki T,
Tsutsui H,
Tamaki N,
Terae S,
Shirato H</span><br />
<span class="medgenPMjournal">J Cardiovasc Comput Tomogr</span>
2010 May-Jun;4(3):218-20.
Epub 2010 Feb 20
doi: 10.1016/j.jcct.2010.02.001.
<span class="bold">PMID: </span><a href="/pubmed/20392685" target="_blank">20392685</a></div>
<div class="nl"><a target="_blank" href="/pubmed/19022036">Cor triatriatum associated with ASD and common atrium in 7-month-old with tachypnea and failure to thrive.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">McLean MK,
Kung GC,
Polimenakos A,
Wells WJ,
Reemtsen BL</span><br />
<span class="medgenPMjournal">Ann Thorac Surg</span>
2008 Dec;86(6):1999.
doi: 10.1016/j.athoracsur.2008.01.037.
<span class="bold">PMID: </span><a href="/pubmed/19022036" target="_blank">19022036</a></div>
<div class="nl"><a target="_blank" href="/pubmed/18022916">Creation of a coronary sinus to atrial communication in coronary sinus ostial atresia improves cardiac function after Fontan.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Petit CJ,
Webb GD,
Rome JJ</span><br />
<span class="medgenPMjournal">Catheter Cardiovasc Interv</span>
2007 Nov 15;70(6):897-9.
doi: 10.1002/ccd.21264.
<span class="bold">PMID: </span><a href="/pubmed/18022916" target="_blank">18022916</a></div>
<div class="nl"><a target="_blank" href="/pubmed/618385">The course of the conduction system in dextrocardia.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Bharati S,
Lev M</span><br />
<span class="medgenPMjournal">Circulation</span>
1978 Jan;57(1):163-71.
doi: 10.1161/01.cir.57.1.163.
<span class="bold">PMID: </span><a href="/pubmed/618385" target="_blank">618385</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Common%20atrium%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (29)</a></div><h3 class="subhead">Clinical prediction guides</h3>
<div class="nl"><a target="_blank" href="/pubmed/38884736">TAPVR: Molecular Pathways and Animal Models.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Poelmann RE,
Jongbloed MRM,
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<span class="medgenPMjournal">Adv Exp Med Biol</span>
2024;1441:599-614.
doi: 10.1007/978-3-031-44087-8_34.
<span class="bold">PMID: </span><a href="/pubmed/38884736" target="_blank">38884736</a></div>
<div class="nl"><a target="_blank" href="/pubmed/33058759">Germline and Mosaic Variants in PRKACA and PRKACB Cause a Multiple Congenital Malformation Syndrome.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Palencia-Campos A,
Aoto PC,
Machal EMF,
Rivera-Barahona A,
Soto-Bielicka P,
Bertinetti D,
Baker B,
Vu L,
Piceci-Sparascio F,
Torrente I,
Boudin E,
Peeters S,
Van Hul W,
Huber C,
Bonneau D,
Hildebrand MS,
Coleman M,
Bahlo M,
Bennett MF,
Schneider AL,
Scheffer IE,
Kibæk M,
Kristiansen BS,
Issa MY,
Mehrez MI,
Ismail S,
Tenorio J,
Li G,
Skålhegg BS,
Otaify GA,
Temtamy S,
Aglan M,
Jønch AE,
De Luca A,
Mortier G,
Cormier-Daire V,
Ziegler A,
Wallis M,
Lapunzina P,
Herberg FW,
Taylor SS,
Ruiz-Perez VL</span><br />
<span class="medgenPMjournal">Am J Hum Genet</span>
2020 Nov 5;107(5):977-988.
Epub 2020 Oct 14
doi: 10.1016/j.ajhg.2020.09.005.
<span class="bold">PMID: </span><a href="/pubmed/33058759" target="_blank">33058759</a><a href="/pmc/articles/PMC7675002" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/20392685">64-Slice MDCT imaging of endocardial cushion defect associated with other cardiac and extracardiac abnormalities.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Oyama N,
Goto D,
Sasaki T,
Tsutsui H,
Tamaki N,
Terae S,
Shirato H</span><br />
<span class="medgenPMjournal">J Cardiovasc Comput Tomogr</span>
2010 May-Jun;4(3):218-20.
Epub 2010 Feb 20
doi: 10.1016/j.jcct.2010.02.001.
<span class="bold">PMID: </span><a href="/pubmed/20392685" target="_blank">20392685</a></div>
<div class="nl"><a target="_blank" href="/pubmed/9262616">Simultaneous surgical correction of a common atrium and impure flutter.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Yamauchi S,
Imura H,
Bessho R,
Yamada K,
Tanaka S</span><br />
<span class="medgenPMjournal">Ann Thorac Surg</span>
1997 Aug;64(2):548-52.
doi: 10.1016/S0003-4975(97)00459-1.
<span class="bold">PMID: </span><a href="/pubmed/9262616" target="_blank">9262616</a></div>
<div class="nl"><a target="_blank" href="/pubmed/2599539">Single ventricle (morphologic study of 21 cases).</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Kinare SG,
Sivaraman A,
Deshpande J</span><br />
<span class="medgenPMjournal">Indian Heart J</span>
1989 Sep-Oct;41(5):301-6.
<span class="bold">PMID: </span><a href="/pubmed/2599539" target="_blank">2599539</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Common%20atrium%22%20AND%20Clinical%20prediction%20guides%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (15)</a></div></div>
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