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<meta name="keywords" content="C1377916, benign vascular neoplasm, benign vascular tumor, neoplastic process, vascular neoplasms, benign, autosomal dominant, autosomal recessive, birth defects, chromosomal disease, chromosome, clinical features, clinical findings, clinical genetics, clinical recommendations, clinvar, congenital chromosomal disease, consumer genetic resources, cytogenetic location, disease characteristics, disease definitions, disease descriptions, disease ontology, disease synonyms, disease vocabulary, dysmorphology, entrez, familial disease, gene, gene-disease relationship, genereviews, genetic disease, genetic disorder, genetic terminology, genetic testing registry, genetics home reference, genomic disease, gtr, hereditary disease, heritable disease, hpo, human phenotype ontology, inherited disease, management guidelines, maternal inheritance, medgen, medical genetics, medical subject headings, mesh, mitochondrial inheritance, mode of inheritance, national center for biotechnology information, national institutes of health, national library of medicine, ncbi, nih, nlm, omim, ordo, orphanet, paternal inheritance, phenome, position statements, professional practice guidelines, rare disease, reference sequence, refseq, snomed ct, syndrome, undiagnosed diseases, x-linked recessive" /><meta name="description" content="A mesenchymal neoplasm that arises from vascular tissue usually of the skin. It is characterized by the presence of vascular channel formation and endothelial cells. There is no evidence of atypical or malignant cytological and architectural features, invasive features, or metastases." /><meta name="robots" content="index,nofollow,noarchive" />
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<title>Benign vascular tumor (Concept Id: C1377916)
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<!--
UID=235124
ConceptID=C1377916
-->
<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Benign vascular tumor</div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>235124</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C1377916</a></dd><dt><span class="dotprefix"></span></dt><dd>Neoplastic Process</dd></dl></div></div><table class="medgenTable"><tbody><tr><td>Synonyms:</td>
<td>Benign Vascular Neoplasm; Benign Vascular Tumor; benign vascular tumor; Vascular Neoplasms, Benign</td></tr>
<tr><td colspan="2" class="small"> </td></tr><tr><td>Monarch Initiative:</td>
<td><a href="https://monarchinitiative.org/disease/MONDO:0971115" target="_blank">MONDO:0971115</a></td></tr>
</tbody></table></div><div class="rprt-body jig-ncbiinpagenav" data-jigconfig="smoothScroll: false, gotoTopLink: true, gotoTopLinkText: '', gotoTopLinkAttrs: {'title': 'Go to the top of the page'},allHeadingLevels: ['h1'], topOfPageTOC: true, tocId: 'my-toc'"><div id="rprt-tabs-1" class="rprt-tab"><div id="tb-termsProp-1"><div class="leftCol mgCol"><div>
<div class="portlet mgSection" id="ID_100">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Definition">Definition</h1><a sid="100" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln">A mesenchymal neoplasm that arises from vascular tissue usually of the skin. It is characterized by the presence of vascular channel formation and endothelial cells. There is no evidence of atypical or malignant cytological and architectural features, invasive features, or metastases. [from <a title="NCI Thesaurus" href="http://ncit.nci.nih.gov" class="defSource" target="_blank">NCI</a>]</div>
</div>
<div class="portlet mgSection" id="ID_118">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test,  </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test,  </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM,  </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>,  </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar  </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="chiclet_list"><span class="chiclet unavailable round" title="Clinical test">C</span><span class="chiclet unavailable round" title="Research Tests">R</span><span class="chiclet unavailable" title="OMIM">O</span><span class="chiclet unavailable" title="GeneReviews">G</span><span class="chiclet unavailable" title="ClinVar">V</span></span><span class="TLline">Benign vascular tumor</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="TLline"><a href="/medgen/18325" ref="tree=MeSH" title="MedGen record for Pathological process">Pathological process</a></span><ul><li><span class="TLline"><a href="/medgen/4347" ref="tree=MeSH" title="MedGen record for Disease">Disease</a></span><ul><li><span class="TLline"><a href="/medgen/10294" ref="tree=MeSH" title="MedGen record for Neoplasm">Neoplasm</a></span><ul><li><span class="TLline"><a href="/medgen/235364" ref="tree=MeSH" title="MedGen record for Neoplasm by Special Category">Neoplasm by Special Category</a></span><ul><li><span class="TLline"><a href="/medgen/39483" ref="tree=MeSH" title="MedGen record for Benign neoplasm">Benign neoplasm</a></span><ul><li><span class="TLline"><a href="/medgen/83866" ref="tree=MeSH" title="MedGen record for Benign connective and soft tissue neoplasm">Benign connective and soft tissue neoplasm</a></span><ul><li><span class="matched_ds">Benign vascular tumor</span><ul><li><span class="TLline"><a href="/medgen/195779" ref="tree=MeSH" title="MedGen record for Benign blood vessel neoplasm">Benign blood vessel neoplasm</a></span><ul><li><span class="TLline"><a href="/medgen/1931" ref="tree=MeSH" title="MedGen record for Angiomatosis">Angiomatosis</a></span><ul><li><span class="TLline"><a href="/medgen/9646" ref="tree=MeSH" title="MedGen record for Angioosteohypertrophic syndrome">Angioosteohypertrophic syndrome</a></span></li><li><span class="TLline"><a href="/medgen/88409" ref="tree=MeSH" title="MedGen record for Bacillary angiomatosis">Bacillary angiomatosis</a></span></li><li><span class="TLline"><a href="/medgen/307304" ref="tree=MeSH" title="MedGen record for Breast angiomatosis">Breast angiomatosis</a></span></li><li><span class="TLline"><a href="/medgen/65122" ref="tree=MeSH" title="MedGen record for Kasabach-Merritt syndrome">Kasabach-Merritt syndrome</a></span></li><li><span class="TLline"><a href="/medgen/21361" ref="tree=MeSH" title="MedGen record for Sturge-Weber syndrome">Sturge-Weber syndrome</a></span></li><li><span class="TLline"><a href="/medgen/42458" ref="tree=MeSH" title="MedGen record for Von Hippel-Lindau syndrome">Von Hippel-Lindau syndrome</a></span></li></ul></li><li><span class="TLline"><a href="/medgen/5477" ref="tree=MeSH" title="MedGen record for Hemangioma">Hemangioma</a></span><ul><li><span class="TLline"><a href="/medgen/208988" ref="tree=MeSH" title="MedGen record for Acquired hemangioma">Acquired hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/868599" ref="tree=MeSH" title="MedGen record for Arachnoid hemangiomatosis">Arachnoid hemangiomatosis</a></span></li><li><span class="TLline"><a href="/medgen/1697907" ref="tree=MeSH" title="MedGen record for Bladder Hemangioma">Bladder Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/234042" ref="tree=MeSH" title="MedGen record for Bone Hemangioma">Bone Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/163122" ref="tree=MeSH" title="MedGen record for Breast hemangioma">Breast hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/64643" ref="tree=MeSH" title="MedGen record for Capillary hemangioma">Capillary hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/310590" ref="tree=MeSH" title="MedGen record for Cardiac hemangioma">Cardiac hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/9184" ref="tree=MeSH" title="MedGen record for Cavernous hemangioma">Cavernous hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/272703" ref="tree=MeSH" title="MedGen record for Central nervous system hemangioma">Central nervous system hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/156018" ref="tree=MeSH" title="MedGen record for Central Nervous System Venous Angioma">Central Nervous System Venous Angioma</a></span></li><li><span class="TLline"><a href="/medgen/195606" ref="tree=MeSH" title="MedGen record for Chorangioma">Chorangioma</a></span></li><li><span class="TLline"><a href="/medgen/83424" ref="tree=MeSH" title="MedGen record for Choroidal hemangioma">Choroidal hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/65912" ref="tree=MeSH" title="MedGen record for Congenital hemangioma">Congenital hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1627494" ref="tree=MeSH" title="MedGen record for Conjunctival Hemangioma">Conjunctival Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/232421" ref="tree=MeSH" title="MedGen record for Deep hemangioma">Deep hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/66794" ref="tree=MeSH" title="MedGen record for Digestive System Hemangioma">Digestive System Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/61449" ref="tree=MeSH" title="MedGen record for Epithelioid hemangioma">Epithelioid hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/459491" ref="tree=MeSH" title="MedGen record for Esophageal hemangioma">Esophageal hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/340224" ref="tree=MeSH" title="MedGen record for Glabellar hemangioma">Glabellar hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/224917" ref="tree=MeSH" title="MedGen record for Glomeruloid hemangioma">Glomeruloid hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/42384" ref="tree=MeSH" title="MedGen record for Hemangioendothelioma">Hemangioendothelioma</a></span></li><li><span class="TLline"><a href="/medgen/108426" ref="tree=MeSH" title="MedGen record for Hemangioma of gingiva">Hemangioma of gingiva</a></span></li><li><span class="TLline"><a href="/medgen/233268" ref="tree=MeSH" title="MedGen record for Hemangioma of orbit">Hemangioma of orbit</a></span></li><li><span class="TLline"><a href="/medgen/232595" ref="tree=MeSH" title="MedGen record for Hemangioma of peripheral nerve">Hemangioma of peripheral nerve</a></span></li><li><span class="TLline"><a href="/medgen/146343" ref="tree=MeSH" title="MedGen record for Hemangioma of subcutaneous tissue">Hemangioma of subcutaneous tissue</a></span></li><li><span class="TLline"><a href="/medgen/278015" ref="tree=MeSH" title="MedGen record for Hemangiomatosis">Hemangiomatosis</a></span></li><li><span class="TLline"><a href="/medgen/91080" ref="tree=MeSH" title="MedGen record for Hobnail hemangioma">Hobnail hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/57583" ref="tree=MeSH" title="MedGen record for Intra-abdominal hemangioma">Intra-abdominal hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/57582" ref="tree=MeSH" title="MedGen record for Intracranial hemangioma">Intracranial hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1706328" ref="tree=MeSH" title="MedGen record for Intrathoracic hemangioma">Intrathoracic hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1692908" ref="tree=MeSH" title="MedGen record for Kidney Hemangioma">Kidney Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1691308" ref="tree=MeSH" title="MedGen record for Labial hemangioma">Labial hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1689552" ref="tree=MeSH" title="MedGen record for Laryngeal hemangioma">Laryngeal hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1704959" ref="tree=MeSH" title="MedGen record for Lumbosacral hemangioma">Lumbosacral hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1634380" ref="tree=MeSH" title="MedGen record for Mediastinal Hemangioma">Mediastinal Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/66009" ref="tree=MeSH" title="MedGen record for Mucous Membrane Hemangioma">Mucous Membrane Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1698246" ref="tree=MeSH" title="MedGen record for Paraspinal hemangioma">Paraspinal hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1707784" ref="tree=MeSH" title="MedGen record for Paratesticular Hemangioma">Paratesticular Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1618015" ref="tree=MeSH" title="MedGen record for Perineal hemangioma">Perineal hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1692352" ref="tree=MeSH" title="MedGen record for Prostate Hemangioma">Prostate Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1705513" ref="tree=MeSH" title="MedGen record for Retropharyngeal hemangioma">Retropharyngeal hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/785105" ref="tree=MeSH" title="MedGen record for Salivary Gland Hemangioma">Salivary Gland Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1740353" ref="tree=MeSH" title="MedGen record for Sinonasal Hemangioma">Sinonasal Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/151951" ref="tree=MeSH" title="MedGen record for Skin hemangioma">Skin hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/224916" ref="tree=MeSH" title="MedGen record for Spindle cell hemangioma">Spindle cell hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/151930" ref="tree=MeSH" title="MedGen record for Splenic hemangioma">Splenic hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/234907" ref="tree=MeSH" title="MedGen record for Subglottic hemangioma">Subglottic hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1693638" ref="tree=MeSH" title="MedGen record for Supraglottic hemangioma">Supraglottic hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/234375" ref="tree=MeSH" title="MedGen record for Synovial angioma">Synovial angioma</a></span></li><li><span class="TLline"><a href="/medgen/1667339" ref="tree=MeSH" title="MedGen record for Thyroid Gland Hemangioma">Thyroid Gland Hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/83402" ref="tree=MeSH" title="MedGen record for Tufted angioma of skin">Tufted angioma of skin</a></span></li><li><span class="TLline"><a href="/medgen/90801" ref="tree=MeSH" title="MedGen record for Venous hemangioma">Venous hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1696187" ref="tree=MeSH" title="MedGen record for Visceral hemangioma">Visceral hemangioma</a></span></li><li><span class="TLline"><a href="/medgen/1671038" ref="tree=MeSH" title="MedGen record for Vulvar hemangioma">Vulvar hemangioma</a></span></li></ul></li></ul></li><li><span class="TLline"><a href="/medgen/224805" ref="tree=MeSH" title="MedGen record for Benign Lymphatic Vessel Neoplasm">Benign Lymphatic Vessel Neoplasm</a></span><ul><li><span class="TLline"><a href="/medgen/6153" ref="tree=MeSH" title="MedGen record for Lymphangioma">Lymphangioma</a></span><ul><li><span class="TLline"><a href="/medgen/104729" ref="tree=MeSH" title="MedGen record for Cavernous lymphangioma">Cavernous lymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/1788893" ref="tree=MeSH" title="MedGen record for Conjunctival Lymphangioma">Conjunctival Lymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/60195" ref="tree=MeSH" title="MedGen record for Cystic hygroma">Cystic hygroma</a></span></li><li><span class="TLline"><a href="/medgen/825766" ref="tree=MeSH" title="MedGen record for Diffuse lymphatic malformation">Diffuse lymphatic malformation</a></span></li><li><span class="TLline"><a href="/medgen/232546" ref="tree=MeSH" title="MedGen record for Gastric Lymphangioma">Gastric Lymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/45248" ref="tree=MeSH" title="MedGen record for Gorham-Stout disease">Gorham-Stout disease</a></span></li><li><span class="TLline"><a href="/medgen/90804" ref="tree=MeSH" title="MedGen record for Hemolymphangioma">Hemolymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/272766" ref="tree=MeSH" title="MedGen record for Intra-Abdominal Lymphangioma">Intra-Abdominal Lymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/1702492" ref="tree=MeSH" title="MedGen record for Kidney Lymphangioma">Kidney Lymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/7411" ref="tree=MeSH" title="MedGen record for Lymphangioendothelioma">Lymphangioendothelioma</a></span></li><li><span class="TLline"><a href="/medgen/87471" ref="tree=MeSH" title="MedGen record for Lymphangioma Circumscriptum">Lymphangioma Circumscriptum</a></span></li><li><span class="TLline"><a href="/medgen/734711" ref="tree=MeSH" title="MedGen record for Lymphangioma of the orbit">Lymphangioma of the orbit</a></span></li><li><span class="TLline"><a href="/medgen/462225" ref="tree=MeSH" title="MedGen record for Lymphedema-posterior choanal atresia syndrome">Lymphedema-posterior choanal atresia syndrome</a></span></li><li><span class="TLline"><a href="/medgen/898684" ref="tree=MeSH" title="MedGen record for Mediastinal cystic lymphangioma">Mediastinal cystic lymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/233684" ref="tree=MeSH" title="MedGen record for Mediastinal Lymphangioma">Mediastinal Lymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/1804470" ref="tree=MeSH" title="MedGen record for Multifocal lymphangioendotheliomatosis-thrombocytopenia syndrome">Multifocal lymphangioendotheliomatosis-thrombocytopenia syndrome</a></span></li><li><span class="TLline"><a href="/medgen/235466" ref="tree=MeSH" title="MedGen record for Parotid Gland Lymphangioma">Parotid Gland Lymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/232399" ref="tree=MeSH" title="MedGen record for Skin lymphangioma">Skin lymphangioma</a></span></li><li><span class="TLline"><a href="/medgen/1651906" ref="tree=MeSH" title="MedGen record for Thyroid Gland Lymphangioma">Thyroid Gland Lymphangioma</a></span></li></ul></li></ul></li><li><span class="TLline"><a href="/medgen/91129" ref="tree=MeSH" title="MedGen record for Benign Skin Vascular Neoplasm">Benign Skin Vascular Neoplasm</a></span></li><li><span class="TLline"><a href="/medgen/1652129" ref="tree=MeSH" title="MedGen record for Benign Thyroid Gland Vascular Neoplasm">Benign Thyroid Gland Vascular Neoplasm</a></span></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
</div>
<div class="portlet mgSection" id="ID_105">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
<div class="nl"><a target="_blank" href="/pubmed/37062411">Update on the diagnosis and treatment of choroidal hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">García Caride S,
Fernández-Vigo JI,
Valverde-Megías A</span><br />
<span class="medgenPMjournal">Arch Soc Esp Oftalmol (Engl Ed)</span>
2023 May;98(5):281-291.
Epub 2023 Apr 14
doi: 10.1016/j.oftale.2023.04.006.
<span class="bold">PMID: </span><a href="/pubmed/37062411" target="_blank">37062411</a></div>
<div class="nl"><a target="_blank" href="/pubmed/31755430">Circumscribed choroidal hemangioma: An overview of clinical manifestation, diagnosis and management.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Sen M,
Honavar SG</span><br />
<span class="medgenPMjournal">Indian J Ophthalmol</span>
2019 Dec;67(12):1965-1973.
doi: 10.4103/ijo.IJO_2036_19.
<span class="bold">PMID: </span><a href="/pubmed/31755430" target="_blank">31755430</a><a href="/pmc/articles/PMC6896540" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30054848">Kaposiform hemangioendothelioma in children: a benign vascular tumor with multiple treatment options.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Schmid I,
Klenk AK,
Sparber-Sauer M,
Koscielniak E,
Maxwell R,
Häberle B</span><br />
<span class="medgenPMjournal">World J Pediatr</span>
2018 Aug;14(4):322-329.
Epub 2018 Jul 27
doi: 10.1007/s12519-018-0171-5.
<span class="bold">PMID: </span><a href="/pubmed/30054848" target="_blank">30054848</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(%22benign%20vascular%20tumor%22%5Btiab%3A~0%5D)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (14)</a></div></div>
</div>
<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
<div class="portlet mgSection" id="ID_103">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
<div class="nl"><a target="_blank" href="/pubmed/38160670">Female Urethral Cavernous Hemangioma: Introducing Treatment and Follow-Up Course of Three Cases.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Mahmoudnejad N,
Mohammadi Torbati P,
Saberi N,
Sodeifian F</span><br />
<span class="medgenPMjournal">Urol Int</span>
2024;108(2):159-162.
Epub 2023 Dec 29
doi: 10.1159/000535464.
<span class="bold">PMID: </span><a href="/pubmed/38160670" target="_blank">38160670</a><a href="/pmc/articles/PMC10994592" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/38061014">Oral atenolol compared to oral propranolol for infantile hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Meza Viteri V,
Aranibar L</span><br />
<span class="medgenPMjournal">Medwave</span>
2023 Dec 7;23(11):e2753.
doi: 10.5867/medwave.2023.11.2753.
<span class="bold">PMID: </span><a href="/pubmed/38061014" target="_blank">38061014</a></div>
<div class="nl"><a target="_blank" href="/pubmed/31511312">Successful Medical Management of Life-threatening Hepatic Hemangioma in Neonates.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Lekwuttikarn R,
Josephs S,
Teng JM</span><br />
<span class="medgenPMjournal">Pediatrics</span>
2019 Oct;144(4)
Epub 2019 Sep 11
doi: 10.1542/peds.2019-1339.
<span class="bold">PMID: </span><a href="/pubmed/31511312" target="_blank">31511312</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30054848">Kaposiform hemangioendothelioma in children: a benign vascular tumor with multiple treatment options.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Schmid I,
Klenk AK,
Sparber-Sauer M,
Koscielniak E,
Maxwell R,
Häberle B</span><br />
<span class="medgenPMjournal">World J Pediatr</span>
2018 Aug;14(4):322-329.
Epub 2018 Jul 27
doi: 10.1007/s12519-018-0171-5.
<span class="bold">PMID: </span><a href="/pubmed/30054848" target="_blank">30054848</a></div>
<div class="nl"><a target="_blank" href="/pubmed/27989349">Intravascular Papillary Endothelial Hyperplasia at Foot Level: A Case Report and Literature Review.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Espinosa A,
González J,
García-Navas F</span><br />
<span class="medgenPMjournal">J Foot Ankle Surg</span>
2017 Jan-Feb;56(1):72-74.
doi: 10.1053/j.jfas.2016.09.016.
<span class="bold">PMID: </span><a href="/pubmed/27989349" target="_blank">27989349</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Benign%20vascular%20tumor%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (43)</a></div><h3 class="subhead">Diagnosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/34134540">Nasal Septal Angiofibroma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Thobejane O,
Maharaj S</span><br />
<span class="medgenPMjournal">Ear Nose Throat J</span>
2023 Oct;102(10):NP483-NP484.
Epub 2021 Jun 16
doi: 10.1177/01455613211026517.
<span class="bold">PMID: </span><a href="/pubmed/34134540" target="_blank">34134540</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30475166">A mobile hemangioblastoma of the cauda equina: Case report and review of the literature.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Luo H,
Xiao J,
Lv S,
Zhu X,
Cheng Z</span><br />
<span class="medgenPMjournal">J Spinal Cord Med</span>
2020 Sep;43(5):719-722.
Epub 2018 Nov 26
doi: 10.1080/10790268.2018.1547855.
<span class="bold">PMID: </span><a href="/pubmed/30475166" target="_blank">30475166</a><a href="/pmc/articles/PMC7534281" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/15763200">Choroidal hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Singh AD,
Kaiser PK,
Sears JE</span><br />
<span class="medgenPMjournal">Ophthalmol Clin North Am</span>
2005 Mar;18(1):151-61, ix.
doi: 10.1016/j.ohc.2004.07.004.
<span class="bold">PMID: </span><a href="/pubmed/15763200" target="_blank">15763200</a></div>
<div class="nl"><a target="_blank" href="/pubmed/12777933">Circumscribed choroidal hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Mashayekhi A,
Shields CL</span><br />
<span class="medgenPMjournal">Curr Opin Ophthalmol</span>
2003 Jun;14(3):142-9.
doi: 10.1097/00055735-200306000-00006.
<span class="bold">PMID: </span><a href="/pubmed/12777933" target="_blank">12777933</a></div>
<div class="nl"><a target="_blank" href="/pubmed/6485968">Renal hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Takeuchi T,
Kuriyama M,
Shinoda I,
Nishiura T,
Tei K,
Matsushita I,
Yamaha M,
Isogai K</span><br />
<span class="medgenPMjournal">Hinyokika Kiyo</span>
1984 Jun;30(6):767-74.
<span class="bold">PMID: </span><a href="/pubmed/6485968" target="_blank">6485968</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Benign%20vascular%20tumor%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (158)</a></div><h3 class="subhead">Therapy</h3>
<div class="nl"><a target="_blank" href="/pubmed/38618963">Infantile hemangioma: the common and enigmatic vascular tumor.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Holm A,
Mulliken JB,
Bischoff J</span><br />
<span class="medgenPMjournal">J Clin Invest</span>
2024 Apr 15;134(8)
doi: 10.1172/JCI172836.
<span class="bold">PMID: </span><a href="/pubmed/38618963" target="_blank">38618963</a><a href="/pmc/articles/PMC11014660" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/37074104">Rare airway tumor in a previously healthy adolescent successfully treated with endoscopic resection and oral propranolol.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Gipsman AI,
Treat JR,
Piccione J</span><br />
<span class="medgenPMjournal">Pediatr Pulmonol</span>
2023 Jul;58(7):2142-2144.
Epub 2023 Apr 19
doi: 10.1002/ppul.26421.
<span class="bold">PMID: </span><a href="/pubmed/37074104" target="_blank">37074104</a><a href="/pmc/articles/PMC10928546" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34677814">Medical Management of Infantile Hemangiomas: An Update.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Colmant C,
Powell J</span><br />
<span class="medgenPMjournal">Paediatr Drugs</span>
2022 Jan;24(1):29-43.
Epub 2021 Oct 22
doi: 10.1007/s40272-021-00477-9.
<span class="bold">PMID: </span><a href="/pubmed/34677814" target="_blank">34677814</a></div>
<div class="nl"><a target="_blank" href="/pubmed/33490272">Proanthocyanidins as a Potential Novel Way for the Treatment of Hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Tang R,
Xian D,
Xu J,
Peng H,
Pan S,
Zhong J</span><br />
<span class="medgenPMjournal">Biomed Res Int</span>
2021;2021:5695378.
Epub 2021 Jan 2
doi: 10.1155/2021/5695378.
<span class="bold">PMID: </span><a href="/pubmed/33490272" target="_blank">33490272</a><a href="/pmc/articles/PMC7801061" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30054848">Kaposiform hemangioendothelioma in children: a benign vascular tumor with multiple treatment options.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Schmid I,
Klenk AK,
Sparber-Sauer M,
Koscielniak E,
Maxwell R,
Häberle B</span><br />
<span class="medgenPMjournal">World J Pediatr</span>
2018 Aug;14(4):322-329.
Epub 2018 Jul 27
doi: 10.1007/s12519-018-0171-5.
<span class="bold">PMID: </span><a href="/pubmed/30054848" target="_blank">30054848</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Benign%20vascular%20tumor%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (28)</a></div><h3 class="subhead">Prognosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/37062411">Update on the diagnosis and treatment of choroidal hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">García Caride S,
Fernández-Vigo JI,
Valverde-Megías A</span><br />
<span class="medgenPMjournal">Arch Soc Esp Oftalmol (Engl Ed)</span>
2023 May;98(5):281-291.
Epub 2023 Apr 14
doi: 10.1016/j.oftale.2023.04.006.
<span class="bold">PMID: </span><a href="/pubmed/37062411" target="_blank">37062411</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34677814">Medical Management of Infantile Hemangiomas: An Update.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Colmant C,
Powell J</span><br />
<span class="medgenPMjournal">Paediatr Drugs</span>
2022 Jan;24(1):29-43.
Epub 2021 Oct 22
doi: 10.1007/s40272-021-00477-9.
<span class="bold">PMID: </span><a href="/pubmed/34677814" target="_blank">34677814</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30054848">Kaposiform hemangioendothelioma in children: a benign vascular tumor with multiple treatment options.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Schmid I,
Klenk AK,
Sparber-Sauer M,
Koscielniak E,
Maxwell R,
Häberle B</span><br />
<span class="medgenPMjournal">World J Pediatr</span>
2018 Aug;14(4):322-329.
Epub 2018 Jul 27
doi: 10.1007/s12519-018-0171-5.
<span class="bold">PMID: </span><a href="/pubmed/30054848" target="_blank">30054848</a></div>
<div class="nl"><a target="_blank" href="/pubmed/22565125">Evolution of hemangioma endothelium.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Kleiman A,
Keats EC,
Chan NG,
Khan ZA</span><br />
<span class="medgenPMjournal">Exp Mol Pathol</span>
2012 Oct;93(2):264-72.
Epub 2012 May 4
doi: 10.1016/j.yexmp.2012.04.020.
<span class="bold">PMID: </span><a href="/pubmed/22565125" target="_blank">22565125</a></div>
<div class="nl"><a target="_blank" href="/pubmed/15763200">Choroidal hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Singh AD,
Kaiser PK,
Sears JE</span><br />
<span class="medgenPMjournal">Ophthalmol Clin North Am</span>
2005 Mar;18(1):151-61, ix.
doi: 10.1016/j.ohc.2004.07.004.
<span class="bold">PMID: </span><a href="/pubmed/15763200" target="_blank">15763200</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Benign%20vascular%20tumor%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (36)</a></div><h3 class="subhead">Clinical prediction guides</h3>
<div class="nl"><a target="_blank" href="/pubmed/39286286">Identification of Potential Therapeutics for Infantile Hemangioma via in silico Investigation and in vitro Validation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Lu W,
Yang Z,
Wang M,
Zhang Y,
Qi Z,
Yang X</span><br />
<span class="medgenPMjournal">Drug Des Devel Ther</span>
2024;18:4065-4088.
Epub 2024 Sep 12
doi: 10.2147/DDDT.S460575.
<span class="bold">PMID: </span><a href="/pubmed/39286286" target="_blank">39286286</a><a href="/pmc/articles/PMC11404501" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/38061014">Oral atenolol compared to oral propranolol for infantile hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Meza Viteri V,
Aranibar L</span><br />
<span class="medgenPMjournal">Medwave</span>
2023 Dec 7;23(11):e2753.
doi: 10.5867/medwave.2023.11.2753.
<span class="bold">PMID: </span><a href="/pubmed/38061014" target="_blank">38061014</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34677814">Medical Management of Infantile Hemangiomas: An Update.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Colmant C,
Powell J</span><br />
<span class="medgenPMjournal">Paediatr Drugs</span>
2022 Jan;24(1):29-43.
Epub 2021 Oct 22
doi: 10.1007/s40272-021-00477-9.
<span class="bold">PMID: </span><a href="/pubmed/34677814" target="_blank">34677814</a></div>
<div class="nl"><a target="_blank" href="/pubmed/16785378">Congenital, self-regressing tufted angioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Browning J,
Frieden I,
Baselga E,
Wagner A,
Metry D</span><br />
<span class="medgenPMjournal">Arch Dermatol</span>
2006 Jun;142(6):749-51.
doi: 10.1001/archderm.142.6.749.
<span class="bold">PMID: </span><a href="/pubmed/16785378" target="_blank">16785378</a></div>
<div class="nl"><a target="_blank" href="/pubmed/12777933">Circumscribed choroidal hemangioma.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Mashayekhi A,
Shields CL</span><br />
<span class="medgenPMjournal">Curr Opin Ophthalmol</span>
2003 Jun;14(3):142-9.
doi: 10.1097/00055735-200306000-00006.
<span class="bold">PMID: </span><a href="/pubmed/12777933" target="_blank">12777933</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Benign%20vascular%20tumor%22%20AND%20Clinical%20prediction%20guides%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (28)</a></div></div>
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