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<!--
|
||
UID=1638446
|
||
ConceptID=C4551473
|
||
-->
|
||
<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Cystic medial necrosis</div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>1638446</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C4551473</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div><table class="medgenTable"><tbody><tr><td>Synonyms:</td>
|
||
<td>Arterial cystic medial necrosis; Cystic adventitial disease; Cystic medionecrosis</td></tr>
|
||
<tr><td><span class="bold">SNOMED CT: </span></td>
|
||
<td>Cystic adventitial disease (234021009); Cystic medial necrosis (234021009); Cystic medial necrosis (42182000); Cystic medionecrosis (42182000)</td></tr>
|
||
<tr><td colspan="2" class="small"> </td></tr><tr><td>HPO:</td>
|
||
<td><a target="_blank" title="Human Phenotype Ontology" href="https://hpo.jax.org/app/browse/term/HP:0012180">HP:0012180</a></td></tr>
|
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</tbody></table></div><div class="rprt-body jig-ncbiinpagenav" data-jigconfig="smoothScroll: false, gotoTopLink: true, gotoTopLinkText: '', gotoTopLinkAttrs: {'title': 'Go to the top of the page'},allHeadingLevels: ['h1'], topOfPageTOC: true, tocId: 'my-toc'"><div id="rprt-tabs-1" class="rprt-tab"><div id="tb-termsProp-1"><div class="leftCol mgCol"><div>
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<div class="portlet mgSection" id="ID_100">
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||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Definition">Definition</h1><a sid="100" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln">A disorder of large arteries, in particular the aorta, characterized by an accumulation of basophilic ground substance in the media with cyst-like lesions associated with degenerative changes of collagen, elastin and the vascular smooth muscle cells. [from <a title="Human Phenotype Ontology" href="http://www.human-phenotype-ontology.org" class="defSource" target="_blank">HPO</a>]</div>
|
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</div>
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||
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||
<div class="portlet mgSection" id="ID_118">
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test, </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test, </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM, </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>, </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="chiclet_list"><span class="chiclet unavailable round" title="Clinical test">C</span><span class="chiclet unavailable round" title="Research Tests">R</span><span class="chiclet unavailable" title="OMIM">O</span><span class="chiclet unavailable" title="GeneReviews">G</span><span class="chiclet unavailable" title="ClinVar">V</span></span><span class="TLline">Cystic medial necrosis</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="TLline"><a href="/medgen/2848" ref="tree=MeSH" title="MedGen record for Disorder of cardiovascular system">Disorder of cardiovascular system</a></span><ul><li><span class="TLline"><a href="/medgen/116727" ref="tree=MeSH" title="MedGen record for Abnormality of the cardiovascular system">Abnormality of the cardiovascular system</a></span><ul><li><span class="TLline"><a href="/medgen/892473" ref="tree=MeSH" title="MedGen record for Abnormal cardiovascular system morphology">Abnormal cardiovascular system morphology</a></span><ul><li><span class="TLline"><a href="/medgen/927608" ref="tree=MeSH" title="MedGen record for Abnormal vascular morphology">Abnormal vascular morphology</a></span><ul><li><span class="TLline"><a href="/medgen/1778737" ref="tree=MeSH" title="MedGen record for Abnormal blood vessel morphology">Abnormal blood vessel morphology</a></span><ul><li><span class="TLline"><a href="/medgen/892767" ref="tree=MeSH" title="MedGen record for Abnormal systemic arterial morphology">Abnormal systemic arterial morphology</a></span><ul><li><span class="matched_ds">Cystic medial necrosis</span></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_112">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Conditions_with_this_feature">Conditions with this feature</h1><a sid="112" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln clinfeat">
|
||
<div class="divPopper rprt" id="rdis_325345"><div><strong>Arterial dissection-lentiginosis syndrome</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>325345</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C1838122</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">A rare association syndrome, reported in several members of two families to date, characterized by arterial dissection, occurring at an early age and presenting with a range of manifestations depending on the vascular territory involved (ex. headache, dysphasia, hemiparesis), in association with cystic medial necrosis and multiple lentigines (brown and black in color and mainly affecting the skin of the trunk and extremities).</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/325345">Condition Record</a></div></div>
|
||
<div class="divPopper rprt" id="rdis_338704"><div><strong>Aortic aneurysm, familial thoracic 4</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>338704</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C1851504</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Any familial thoracic aortic aneurysm and aortic dissection in which the cause of the disease is a mutation in the MYH11 gene.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/338704">Condition Record</a></div></div>
|
||
<div class="divPopper rprt" id="rdis_377701"><div><strong>Idiopathic spontaneous coronary artery dissection</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>377701</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C1852540</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">A rare vascular disease characterized by idiopathic detachment of the layers of the walls of coronary arteries, creating a false lumen which limits the main coronary flow, leading to myocardial ischemia. Clinical manifestations include acute coronary syndromes, especially ST-segment elevation myocardial infarction (STEMI), syncope, cardiogenic shock, or sudden cardiac death. The condition typically affects young women.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/377701">Condition Record</a></div></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_338704" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Aortic aneurysm, familial thoracic 4</a></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_325345" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Arterial dissection-lentiginosis syndrome</a></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_377701" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Idiopathic spontaneous coronary artery dissection</a></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_105">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/27031798">Consensus statement on surgical pathology of the aorta from the Society for Cardiovascular Pathology and the Association For European Cardiovascular Pathology: II. Noninflammatory degenerative diseases - nomenclature and diagnostic criteria.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Halushka MK,
|
||
Angelini A,
|
||
Bartoloni G,
|
||
Basso C,
|
||
Batoroeva L,
|
||
Bruneval P,
|
||
Buja LM,
|
||
Butany J,
|
||
d'Amati G,
|
||
Fallon JT,
|
||
Gallagher PJ,
|
||
Gittenberger-de Groot AC,
|
||
Gouveia RH,
|
||
Kholova I,
|
||
Kelly KL,
|
||
Leone O,
|
||
Litovsky SH,
|
||
Maleszewski JJ,
|
||
Miller DV,
|
||
Mitchell RN,
|
||
Preston SD,
|
||
Pucci A,
|
||
Radio SJ,
|
||
Rodriguez ER,
|
||
Sheppard MN,
|
||
Stone JR,
|
||
Suvarna SK,
|
||
Tan CD,
|
||
Thiene G,
|
||
Veinot JP,
|
||
van der Wal AC</span><br />
|
||
<span class="medgenPMjournal">Cardiovasc Pathol</span>
|
||
2016 May-Jun;25(3):247-257.
|
||
Epub 2016 Mar 12
|
||
doi: 10.1016/j.carpath.2016.03.002.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27031798" target="_blank">27031798</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/5008118">Operative treatment of aneurysms of the thoracic aorta due to cystic medial necrosis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Shumacker HB Jr</span><br />
|
||
<span class="medgenPMjournal">J Thorac Cardiovasc Surg</span>
|
||
1972 Jan;63(1):1-13.
|
||
<span class="bold">PMID: </span><a href="/pubmed/5008118" target="_blank">5008118</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(%22cystic%20medial%20necrosis%22%5Btiab%3A~0%5D)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (2)</a></div></div>
|
||
</div>
|
||
<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
|
||
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
|
||
<div class="portlet mgSection" id="ID_103">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/18273550">Sudden death due to aortic rupture in acromegaly.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Maffei P,
|
||
Menegazzo C,
|
||
Michelotto M,
|
||
Salmaso R,
|
||
Martini C,
|
||
De Carlo E,
|
||
Carli M,
|
||
Barban M,
|
||
Fassina A,
|
||
Vettor R,
|
||
Sicolo N</span><br />
|
||
<span class="medgenPMjournal">Heart Vessels</span>
|
||
2008 Jan;23(1):71-4.
|
||
Epub 2008 Feb 14
|
||
doi: 10.1007/s00380-007-1012-y.
|
||
<span class="bold">PMID: </span><a href="/pubmed/18273550" target="_blank">18273550</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/16129122">The bicuspid aortic valve.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Braverman AC,
|
||
Güven H,
|
||
Beardslee MA,
|
||
Makan M,
|
||
Kates AM,
|
||
Moon MR</span><br />
|
||
<span class="medgenPMjournal">Curr Probl Cardiol</span>
|
||
2005 Sep;30(9):470-522.
|
||
doi: 10.1016/j.cpcardiol.2005.06.002.
|
||
<span class="bold">PMID: </span><a href="/pubmed/16129122" target="_blank">16129122</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/10990289">Aortic dissection after ingestion of "ecstasy" (MDMA).</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Duflou J,
|
||
Mark A</span><br />
|
||
<span class="medgenPMjournal">Am J Forensic Med Pathol</span>
|
||
2000 Sep;21(3):261-3.
|
||
doi: 10.1097/00000433-200009000-00016.
|
||
<span class="bold">PMID: </span><a href="/pubmed/10990289" target="_blank">10990289</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/8121211">Sudden death screening.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Rich BS</span><br />
|
||
<span class="medgenPMjournal">Med Clin North Am</span>
|
||
1994 Mar;78(2):267-88.
|
||
doi: 10.1016/s0025-7125(16)30159-6.
|
||
<span class="bold">PMID: </span><a href="/pubmed/8121211" target="_blank">8121211</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/3079780">Sudden death and the competitive athlete: perspectives on preparticipation screening studies.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Epstein SE,
|
||
Maron BJ</span><br />
|
||
<span class="medgenPMjournal">J Am Coll Cardiol</span>
|
||
1986 Jan;7(1):220-30.
|
||
doi: 10.1016/s0735-1097(86)80285-6.
|
||
<span class="bold">PMID: </span><a href="/pubmed/3079780" target="_blank">3079780</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Cystic%20medial%20necrosis%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (72)</a></div><h3 class="subhead">Diagnosis</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/27031798">Consensus statement on surgical pathology of the aorta from the Society for Cardiovascular Pathology and the Association For European Cardiovascular Pathology: II. Noninflammatory degenerative diseases - nomenclature and diagnostic criteria.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Halushka MK,
|
||
Angelini A,
|
||
Bartoloni G,
|
||
Basso C,
|
||
Batoroeva L,
|
||
Bruneval P,
|
||
Buja LM,
|
||
Butany J,
|
||
d'Amati G,
|
||
Fallon JT,
|
||
Gallagher PJ,
|
||
Gittenberger-de Groot AC,
|
||
Gouveia RH,
|
||
Kholova I,
|
||
Kelly KL,
|
||
Leone O,
|
||
Litovsky SH,
|
||
Maleszewski JJ,
|
||
Miller DV,
|
||
Mitchell RN,
|
||
Preston SD,
|
||
Pucci A,
|
||
Radio SJ,
|
||
Rodriguez ER,
|
||
Sheppard MN,
|
||
Stone JR,
|
||
Suvarna SK,
|
||
Tan CD,
|
||
Thiene G,
|
||
Veinot JP,
|
||
van der Wal AC</span><br />
|
||
<span class="medgenPMjournal">Cardiovasc Pathol</span>
|
||
2016 May-Jun;25(3):247-257.
|
||
Epub 2016 Mar 12
|
||
doi: 10.1016/j.carpath.2016.03.002.
|
||
<span class="bold">PMID: </span><a href="/pubmed/27031798" target="_blank">27031798</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/15977781">Acute aortic dissection.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Prieto D,
|
||
Antunes MJ</span><br />
|
||
<span class="medgenPMjournal">Rev Port Cardiol</span>
|
||
2005 Apr;24(4):583-604.
|
||
<span class="bold">PMID: </span><a href="/pubmed/15977781" target="_blank">15977781</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/2650544">Turner's syndrome and cardiovascular anomalies: a case report and review of the literature.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Subramaniam PN</span><br />
|
||
<span class="medgenPMjournal">Am J Med Sci</span>
|
||
1989 Apr;297(4):260-2.
|
||
doi: 10.1097/00000441-198904000-00014.
|
||
<span class="bold">PMID: </span><a href="/pubmed/2650544" target="_blank">2650544</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/3079780">Sudden death and the competitive athlete: perspectives on preparticipation screening studies.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Epstein SE,
|
||
Maron BJ</span><br />
|
||
<span class="medgenPMjournal">J Am Coll Cardiol</span>
|
||
1986 Jan;7(1):220-30.
|
||
doi: 10.1016/s0735-1097(86)80285-6.
|
||
<span class="bold">PMID: </span><a href="/pubmed/3079780" target="_blank">3079780</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/4834138">Cystic medial necrosis. A correctable cause of the superior vena cava syndrome.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Roberts AJ,
|
||
Jaffe RB,
|
||
Michaelis LL,
|
||
Morrow AG</span><br />
|
||
<span class="medgenPMjournal">Arch Surg</span>
|
||
1974 Jul;109(1):84-6.
|
||
doi: 10.1001/archsurg.1974.01360010062015.
|
||
<span class="bold">PMID: </span><a href="/pubmed/4834138" target="_blank">4834138</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Cystic%20medial%20necrosis%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (91)</a></div><h3 class="subhead">Therapy</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/21177298">Rapidly growing aortic arch aneurysm in Behcet's disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Kojima N,
|
||
Sakano Y,
|
||
Ohki S,
|
||
Misawa Y</span><br />
|
||
<span class="medgenPMjournal">Interact Cardiovasc Thorac Surg</span>
|
||
2011 Mar;12(3):502-4.
|
||
Epub 2010 Dec 21
|
||
doi: 10.1510/icvts.2010.260976.
|
||
<span class="bold">PMID: </span><a href="/pubmed/21177298" target="_blank">21177298</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/19884902">Cellular and molecular mechanisms of thoracic aortic aneurysms.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">El-Hamamsy I,
|
||
Yacoub MH</span><br />
|
||
<span class="medgenPMjournal">Nat Rev Cardiol</span>
|
||
2009 Dec;6(12):771-86.
|
||
Epub 2009 Nov 3
|
||
doi: 10.1038/nrcardio.2009.191.
|
||
<span class="bold">PMID: </span><a href="/pubmed/19884902" target="_blank">19884902</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/10990289">Aortic dissection after ingestion of "ecstasy" (MDMA).</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Duflou J,
|
||
Mark A</span><br />
|
||
<span class="medgenPMjournal">Am J Forensic Med Pathol</span>
|
||
2000 Sep;21(3):261-3.
|
||
doi: 10.1097/00000433-200009000-00016.
|
||
<span class="bold">PMID: </span><a href="/pubmed/10990289" target="_blank">10990289</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/8644605">Aortic dissection complicating coronary angioplasty in cystic medial necrosis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Pande AK,
|
||
Gosselin G,
|
||
Leclerc Y,
|
||
Leung TK</span><br />
|
||
<span class="medgenPMjournal">Am Heart J</span>
|
||
1996 Jun;131(6):1221-3.
|
||
doi: 10.1016/s0002-8703(96)90101-5.
|
||
<span class="bold">PMID: </span><a href="/pubmed/8644605" target="_blank">8644605</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/5008118">Operative treatment of aneurysms of the thoracic aorta due to cystic medial necrosis.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Shumacker HB Jr</span><br />
|
||
<span class="medgenPMjournal">J Thorac Cardiovasc Surg</span>
|
||
1972 Jan;63(1):1-13.
|
||
<span class="bold">PMID: </span><a href="/pubmed/5008118" target="_blank">5008118</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Cystic%20medial%20necrosis%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (24)</a></div><h3 class="subhead">Prognosis</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/22687361">Acute aortic dissection associated with cystic medial necrosis of unknown etiology.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Akutsu K,
|
||
Kawamoto M,
|
||
Sato N,
|
||
Yamamoto T,
|
||
Tamura K,
|
||
Mizuno K,
|
||
Tanaka K</span><br />
|
||
<span class="medgenPMjournal">J Nippon Med Sch</span>
|
||
2012;79(2):159-62.
|
||
doi: 10.1272/jnms.79.159.
|
||
<span class="bold">PMID: </span><a href="/pubmed/22687361" target="_blank">22687361</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/18273550">Sudden death due to aortic rupture in acromegaly.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Maffei P,
|
||
Menegazzo C,
|
||
Michelotto M,
|
||
Salmaso R,
|
||
Martini C,
|
||
De Carlo E,
|
||
Carli M,
|
||
Barban M,
|
||
Fassina A,
|
||
Vettor R,
|
||
Sicolo N</span><br />
|
||
<span class="medgenPMjournal">Heart Vessels</span>
|
||
2008 Jan;23(1):71-4.
|
||
Epub 2008 Feb 14
|
||
doi: 10.1007/s00380-007-1012-y.
|
||
<span class="bold">PMID: </span><a href="/pubmed/18273550" target="_blank">18273550</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/10990289">Aortic dissection after ingestion of "ecstasy" (MDMA).</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Duflou J,
|
||
Mark A</span><br />
|
||
<span class="medgenPMjournal">Am J Forensic Med Pathol</span>
|
||
2000 Sep;21(3):261-3.
|
||
doi: 10.1097/00000433-200009000-00016.
|
||
<span class="bold">PMID: </span><a href="/pubmed/10990289" target="_blank">10990289</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/7810537">Spontaneous vertebral artery dissection as a complication of autosomal dominant polycystic kidney disease.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Larranaga J,
|
||
Rutecki GW,
|
||
Whittier FC</span><br />
|
||
<span class="medgenPMjournal">Am J Kidney Dis</span>
|
||
1995 Jan;25(1):70-4.
|
||
doi: 10.1016/0272-6386(95)90629-0.
|
||
<span class="bold">PMID: </span><a href="/pubmed/7810537" target="_blank">7810537</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/3079780">Sudden death and the competitive athlete: perspectives on preparticipation screening studies.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Epstein SE,
|
||
Maron BJ</span><br />
|
||
<span class="medgenPMjournal">J Am Coll Cardiol</span>
|
||
1986 Jan;7(1):220-30.
|
||
doi: 10.1016/s0735-1097(86)80285-6.
|
||
<span class="bold">PMID: </span><a href="/pubmed/3079780" target="_blank">3079780</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Cystic%20medial%20necrosis%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (52)</a></div><h3 class="subhead">Clinical prediction guides</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/38042913">Selenoprotein deficiency disorder predisposes to aortic aneurysm formation.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Schoenmakers E,
|
||
Marelli F,
|
||
Jørgensen HF,
|
||
Visser WE,
|
||
Moran C,
|
||
Groeneweg S,
|
||
Avalos C,
|
||
Jurgens SJ,
|
||
Figg N,
|
||
Finigan A,
|
||
Wali N,
|
||
Agostini M,
|
||
Wardle-Jones H,
|
||
Lyons G,
|
||
Rusk R,
|
||
Gopalan D,
|
||
Twiss P,
|
||
Visser JJ,
|
||
Goddard M,
|
||
Nashef SAM,
|
||
Heijmen R,
|
||
Clift P,
|
||
Sinha S,
|
||
Pirruccello JP,
|
||
Ellinor PT,
|
||
Busch-Nentwich EM,
|
||
Ramirez-Solis R,
|
||
Murphy MP,
|
||
Persani L,
|
||
Bennett M,
|
||
Chatterjee K</span><br />
|
||
<span class="medgenPMjournal">Nat Commun</span>
|
||
2023 Dec 2;14(1):7994.
|
||
doi: 10.1038/s41467-023-43851-6.
|
||
<span class="bold">PMID: </span><a href="/pubmed/38042913" target="_blank">38042913</a><a href="/pmc/articles/PMC10693596" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/17316418">Sudden death of a young woman due to aortic dissection caused by Turner's syndrome.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Mimasaka S,
|
||
Ohtsu Y,
|
||
Tsunenari S,
|
||
Matsukawa A,
|
||
Hashiyada M,
|
||
Takahashi S,
|
||
Funayama M</span><br />
|
||
<span class="medgenPMjournal">Pathol Int</span>
|
||
2007 Apr;57(4):219-23.
|
||
doi: 10.1111/j.1440-1827.2007.02084.x.
|
||
<span class="bold">PMID: </span><a href="/pubmed/17316418" target="_blank">17316418</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/15977781">Acute aortic dissection.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Prieto D,
|
||
Antunes MJ</span><br />
|
||
<span class="medgenPMjournal">Rev Port Cardiol</span>
|
||
2005 Apr;24(4):583-604.
|
||
<span class="bold">PMID: </span><a href="/pubmed/15977781" target="_blank">15977781</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/9130129">Aortic root replacement for annuloaortic ectasia in Shprintzen-Goldberg syndrome: a case report.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Fukunaga S,
|
||
Akashi H,
|
||
Tayama K,
|
||
Kawano H,
|
||
Kosuga K,
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Aoyagi S</span><br />
|
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<span class="medgenPMjournal">J Heart Valve Dis</span>
|
||
1997 Mar;6(2):181-3.
|
||
<span class="bold">PMID: </span><a href="/pubmed/9130129" target="_blank">9130129</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/639201">Dissecting aortic aneurysm associated with congenital bicuspid aortic valve.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Edwards WD,
|
||
Leaf DS,
|
||
Edwards JE</span><br />
|
||
<span class="medgenPMjournal">Circulation</span>
|
||
1978 May;57(5):1022-5.
|
||
doi: 10.1161/01.cir.57.5.1022.
|
||
<span class="bold">PMID: </span><a href="/pubmed/639201" target="_blank">639201</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Cystic%20medial%20necrosis%22%20AND%20Clinical%20prediction%20guides%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (25)</a></div></div>
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