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<meta name="keywords" content="C0559106, disease or syndrome, pre-excitation syndrome, preexcitation, ventricular pre-excitation, ventricular preexcitation, autosomal dominant, autosomal recessive, birth defects, chromosomal disease, chromosome, clinical features, clinical findings, clinical genetics, clinical recommendations, clinvar, congenital chromosomal disease, consumer genetic resources, cytogenetic location, disease characteristics, disease definitions, disease descriptions, disease ontology, disease synonyms, disease vocabulary, dysmorphology, entrez, familial disease, gene, gene-disease relationship, genereviews, genetic disease, genetic disorder, genetic terminology, genetic testing registry, genetics home reference, genomic disease, gtr, hereditary disease, heritable disease, hpo, human phenotype ontology, inherited disease, management guidelines, maternal inheritance, medgen, medical genetics, medical subject headings, mesh, mitochondrial inheritance, mode of inheritance, national center for biotechnology information, national institutes of health, national library of medicine, ncbi, nih, nlm, omim, ordo, orphanet, paternal inheritance, phenome, position statements, professional practice guidelines, rare disease, reference sequence, refseq, snomed ct, syndrome, undiagnosed diseases, x-linked recessive" /><meta name="description" content="An abnormality in which the cardiac ventricles depolarize too early as a result of an abnormality of cardiac conduction pathways such as an accessory pathway." /><meta name="robots" content="index,nofollow,noarchive" />
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<title>Ventricular preexcitation (Concept Id: C0559106)
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<!--
UID=107848
ConceptID=C0559106
-->
<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Ventricular preexcitation</div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>107848</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C0559106</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div><table class="medgenTable"><tbody><tr><td>Synonyms:</td>
<td>Pre-excitation syndrome; Preexcitation; Ventricular pre-excitation</td></tr>
<tr><td><span class="bold">SNOMED CT: </span></td>
<td>Ventricular pre-excitation (195060002)</td></tr>
<tr><td colspan="2" class="small"> </td></tr><tr><td>HPO:</td>
<td><a target="_blank" title="Human Phenotype Ontology" href="https://hpo.jax.org/app/browse/term/HP:0004309">HP:0004309</a></td></tr>
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<div class="portlet mgSection" id="ID_100">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Definition">Definition</h1><a sid="100" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln">An abnormality in which the cardiac ventricles depolarize too early as a result of an abnormality of cardiac conduction pathways such as an accessory pathway. [from <a title="Human Phenotype Ontology" href="http://www.human-phenotype-ontology.org" class="defSource" target="_blank">HPO</a>]</div>
</div>
<div class="portlet mgSection" id="ID_118">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test,  </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test,  </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM,  </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>,  </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar  </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="chiclet_list"><span class="chiclet unavailable round" title="Clinical test">C</span><span class="chiclet unavailable round" title="Research Tests">R</span><span class="chiclet unavailable" title="OMIM">O</span><span class="chiclet unavailable" title="GeneReviews">G</span><span class="chiclet unavailable" title="ClinVar">V</span></span><span class="TLline">Ventricular preexcitation</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="TLline"><a href="/medgen/2848" ref="tree=MeSH" title="MedGen record for Disorder of cardiovascular system">Disorder of cardiovascular system</a></span><ul><li><span class="TLline"><a href="/medgen/116727" ref="tree=MeSH" title="MedGen record for Abnormality of the cardiovascular system">Abnormality of the cardiovascular system</a></span><ul><li><span class="TLline"><a href="/medgen/869166" ref="tree=MeSH" title="MedGen record for Abnormal cardiovascular system physiology">Abnormal cardiovascular system physiology</a></span><ul><li><span class="TLline"><a href="/medgen/1393551" ref="tree=MeSH" title="MedGen record for Abnormality of cardiovascular system electrophysiology">Abnormality of cardiovascular system electrophysiology</a></span><ul><li><span class="TLline"><a href="/medgen/2039" ref="tree=MeSH" title="MedGen record for Cardiac arrhythmia">Cardiac arrhythmia</a></span><ul><li><span class="TLline"><a href="/medgen/39082" ref="tree=MeSH" title="MedGen record for Ventricular arrhythmia">Ventricular arrhythmia</a></span><ul><li><span class="matched_ds">Ventricular preexcitation</span><ul><li><span class="TLline"><a href="/medgen/870556" ref="tree=MeSH" title="MedGen record for Ventricular preexcitation with multiple accessory pathways">Ventricular preexcitation with multiple accessory pathways</a></span></li><li><span class="TLline"><a href="/medgen/12162" ref="tree=MeSH" title="MedGen record for Wolff-Parkinson-White pattern">Wolff-Parkinson-White pattern</a></span></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
</div>
<div class="portlet mgSection" id="ID_112">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Conditions_with_this_feature">Conditions with this feature</h1><a sid="112" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln clinfeat">
<div class="divPopper rprt" id="rdis_4435"><div><strong>Ebstein anomaly</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>4435</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C0013481</a></dd><dt><span class="dotprefix"></span></dt><dd>Congenital Abnormality</dd></dl></div></div></div>
<div class="spaceAbove">Ebstein anomaly is characterized by downward displacement of variable severity of the tricuspid valve into the right ventricle. The valve leaflets may be dysplastic, and a variable portion of the proximal part of the right ventricle is in continuity with the right atrium ('atrialized'), because of the abnormally positioned tricuspid valve. The severity of this defect includes a spectrum ranging from severe disturbance in fetal and neonatal life to virtually asymptomatic survival to adult life. Associated extracardiac anomalies in the setting of chromosomal or mendelian disorders occur in about 20% of patients with Ebstein anomaly. Nonsyndromic Ebstein anomaly can occur as a sporadic or a familial defect (summary by Digilio et al., 2011).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/4435">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_12162"><div><strong>Wolff-Parkinson-White pattern</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>12162</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C0043202</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Wolff-Parkinson-White syndrome is a condition characterized by abnormal electrical pathways in the heart that cause a disruption of the heart's normal rhythm (arrhythmia).\n\nThe heartbeat is controlled by electrical signals that move through the heart in a highly coordinated way. A specialized cluster of cells called the atrioventricular node conducts electrical impulses from the heart's upper chambers (the atria) to the lower chambers (the ventricles). Impulses move through the atrioventricular node during each heartbeat, stimulating the ventricles to contract slightly later than the atria.\n\nPeople with Wolff-Parkinson-White syndrome are born with an extra connection in the heart, called an accessory pathway, that allows electrical signals to bypass the atrioventricular node and move from the atria to the ventricles faster than usual. The accessory pathway may also transmit electrical impulses abnormally from the ventricles back to the atria. This extra connection can disrupt the coordinated movement of electrical signals through the heart, leading to an abnormally fast heartbeat (tachycardia) and other changes in heart rhythm. Resulting symptoms include dizziness, a sensation of fluttering or pounding in the chest (palpitations), shortness of breath, and fainting (syncope). In rare cases, arrhythmias associated with Wolff-Parkinson-White syndrome can lead to cardiac arrest and sudden death. The most common arrhythmia associated with Wolff-Parkinson-White syndrome is called paroxysmal supraventricular tachycardia.\n\nComplications of Wolff-Parkinson-White syndrome can occur at any age, although some individuals born with an accessory pathway in the heart never experience any health problems associated with the condition.\n\nWolff-Parkinson-White syndrome often occurs with other structural abnormalities of the heart or underlying heart disease. The most common heart defect associated with the condition is Ebstein anomaly, which affects the valve that allows blood to flow from the right atrium to the right ventricle (the tricuspid valve). Additionally, the heart rhythm problems associated with Wolff-Parkinson-White syndrome can be a component of several other genetic syndromes, including hypokalemic periodic paralysis (a condition that causes episodes of extreme muscle weakness), Pompe disease (a disorder characterized by the storage of excess glycogen), Danon disease (a condition that weakens the heart and skeletal muscles and causes intellectual disability), and tuberous sclerosis complex (a condition that results in the growth of noncancerous tumors in many parts of the body).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/12162">Condition Record</a></div></div>
<div class="divPopper rprt" id="rdis_331466"><div><strong>Hypertrophic cardiomyopathy 6</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>331466</dd><dt><span class="dotprefix"></span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS)&#10;Click for more information.">C1833236</a></dd><dt><span class="dotprefix"></span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
<div class="spaceAbove">Mutations in the PRKAG2 gene (602743) give rise to a moderate, essentially heart-specific, nonlysosomal glycogenosis with clinical onset typically in late adolescence or in the third decade of life, ventricular pre-excitation predisposing to supraventricular arrhythmias, mild to severe cardiac hypertrophy, enhanced risk of sudden cardiac death in midlife, and autosomal dominant inheritance with full penetrance (summary by Burwinkel et al., 2005).</div>
<div class="spaceAbove nowrap">See: <a href="/medgen/331466">Condition Record</a></div></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_4435" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Ebstein anomaly</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_331466" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Hypertrophic cardiomyopathy 6</a></div>
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_12162" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Wolff-Parkinson-White pattern</a></div></div>
</div>
<div class="portlet mgSection" id="ID_105">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
<div class="nl"><a target="_blank" href="/pubmed/32826411">The Pathophysiology, Diagnosis, and Management of Wolff-Parkinson-White Syndrome in the Neonate.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Chambers S,
Jnah A,
Newberry D</span><br />
<span class="medgenPMjournal">Adv Neonatal Care</span>
2021 Jun 1;21(3):178-188.
doi: 10.1097/ANC.0000000000000785.
<span class="bold">PMID: </span><a href="/pubmed/32826411" target="_blank">32826411</a></div>
<div class="nl"><a target="_blank" href="/pubmed/22579340">PACES/HRS expert consensus statement on the management of the asymptomatic young patient with a Wolff-Parkinson-White (WPW, ventricular preexcitation) electrocardiographic pattern: developed in partnership between the Pediatric and Congenital Electrophysiology Society (PACES) and the Heart Rhythm Society (HRS). Endorsed by the governing bodies of PACES, HRS, the American College of Cardiology Foundation (ACCF), the American Heart Association (AHA), the American Academy of Pediatrics (AAP), and the Canadian Heart Rhythm Society (CHRS).</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Pediatric and Congenital Electrophysiology Society (PACES);
Heart Rhythm Society (HRS);
American College of Cardiology Foundation (ACCF);
American Heart Association (AHA);
American Academy of Pediatrics (AAP);
Canadian Heart Rhythm Society (CHRS),
Cohen MI,
Triedman JK,
Cannon BC,
Davis AM,
Drago F,
Janousek J,
Klein GJ,
Law IH,
Morady FJ,
Paul T,
Perry JC,
Sanatani S,
Tanel RE</span><br />
<span class="medgenPMjournal">Heart Rhythm</span>
2012 Jun;9(6):1006-24.
Epub 2012 May 10
doi: 10.1016/j.hrthm.2012.03.050.
<span class="bold">PMID: </span><a href="/pubmed/22579340" target="_blank">22579340</a></div>
<div class="nl"><a target="_blank" href="/pubmed/6381927">Preexcitation syndromes. Mechanisms and management.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Prystowsky EN,
Miles WM,
Heger JJ,
Zipes DP</span><br />
<span class="medgenPMjournal">Med Clin North Am</span>
1984 Jul;68(4):831-93.
doi: 10.1016/s0025-7125(16)31104-x.
<span class="bold">PMID: </span><a href="/pubmed/6381927" target="_blank">6381927</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(%22ventricular%20preexcitation%22%5Btiab%3A~0%5D)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (13)</a></div></div>
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<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
<div class="portlet mgSection" id="ID_103">
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
<div class="nl"><a target="_blank" href="/pubmed/39351912">Intermittent ventricular preexcitation in children: not always a low-risk condition.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Yammine ML,
Tamborrino PP,
Flore F,
Di Mambro C,
Pazzano V,
Di Marzio S,
Drago F</span><br />
<span class="medgenPMjournal">Europace</span>
2024 Oct 3;26(10)
doi: 10.1093/europace/euae250.
<span class="bold">PMID: </span><a href="/pubmed/39351912" target="_blank">39351912</a><a href="/pmc/articles/PMC11481285" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/37877314">Hypertrophic Cardiomyopathy and Ventricular Preexcitation in the Young: Cause and Accessory Pathway Characteristics.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Przybylski R,
Saravu Vijayashankar S,
O'Leary ET,
Hylind RJ,
Noon J,
Dionne A,
DeWitt ES,
Bezzerides VJ,
Abrams DJ</span><br />
<span class="medgenPMjournal">Circ Arrhythm Electrophysiol</span>
2023 Nov;16(11):e012191.
Epub 2023 Oct 25
doi: 10.1161/CIRCEP.123.012191.
<span class="bold">PMID: </span><a href="/pubmed/37877314" target="_blank">37877314</a><a href="/pmc/articles/PMC10843507" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/33162000">Sudden Cardiac Death in Patients with Ventricular Preexcitation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Delise P,
Sciarra L</span><br />
<span class="medgenPMjournal">Card Electrophysiol Clin</span>
2020 Dec;12(4):519-525.
Epub 2020 Sep 23
doi: 10.1016/j.ccep.2020.08.002.
<span class="bold">PMID: </span><a href="/pubmed/33162000" target="_blank">33162000</a></div>
<div class="nl"><a target="_blank" href="/pubmed/29754436">Unresolved questions associated with the management of ventricular preexcitation syndrome.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Brembilla-Perrot B,
Girerd N,
Sellal JM</span><br />
<span class="medgenPMjournal">Pacing Clin Electrophysiol</span>
2018 Jul;41(7):839-844.
Epub 2018 Jun 8
doi: 10.1111/pace.13367.
<span class="bold">PMID: </span><a href="/pubmed/29754436" target="_blank">29754436</a></div>
<div class="nl"><a target="_blank" href="/pubmed/9272512">Anatomy of the atrioventricular junctions with regard to ventricular preexcitation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Anderson RH,
Ho SY</span><br />
<span class="medgenPMjournal">Pacing Clin Electrophysiol</span>
1997 Aug;20(8 Pt 2):2072-6.
doi: 10.1111/j.1540-8159.1997.tb03631.x.
<span class="bold">PMID: </span><a href="/pubmed/9272512" target="_blank">9272512</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Ventricular%20preexcitation%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (107)</a></div><h3 class="subhead">Diagnosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/33161999">Arrhythmias Involving Variants of Accessory Pathways.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Marazzato J,
Marazzi R,
Doni LA,
Angeli F,
Bagliani G,
Leonelli FM,
De Ponti R</span><br />
<span class="medgenPMjournal">Card Electrophysiol Clin</span>
2020 Dec;12(4):505-518.
Epub 2020 Sep 26
doi: 10.1016/j.ccep.2020.08.001.
<span class="bold">PMID: </span><a href="/pubmed/33161999" target="_blank">33161999</a></div>
<div class="nl"><a target="_blank" href="/pubmed/22349070">Ventricular preexcitation and atrioventricular block?</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Arias MA,
Pachón M,
Casares-Medrano J,
Puchol A</span><br />
<span class="medgenPMjournal">Heart Rhythm</span>
2013 Jan;10(1):142-3.
Epub 2012 Feb 17
doi: 10.1016/j.hrthm.2012.02.021.
<span class="bold">PMID: </span><a href="/pubmed/22349070" target="_blank">22349070</a></div>
<div class="nl"><a target="_blank" href="/pubmed/20630836">Wolff-Parkinson-White syndrome in infants.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Hermosura T,
Bradshaw WT</span><br />
<span class="medgenPMjournal">Neonatal Netw</span>
2010 Jul-Aug;29(4):215-23.
doi: 10.1891/0730-0832.29.4.215.
<span class="bold">PMID: </span><a href="/pubmed/20630836" target="_blank">20630836</a></div>
<div class="nl"><a target="_blank" href="/pubmed/3573234">The management of preexcitation syndromes.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Wellens HJ,
Brugada P,
Penn OC</span><br />
<span class="medgenPMjournal">JAMA</span>
1987 May 1;257(17):2325-33.
<span class="bold">PMID: </span><a href="/pubmed/3573234" target="_blank">3573234</a></div>
<div class="nl"><a target="_blank" href="/pubmed/324276">Preexcitation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Ferrer MI</span><br />
<span class="medgenPMjournal">Am J Med</span>
1977 May;62(5):715-30.
doi: 10.1016/0002-9343(77)90875-0.
<span class="bold">PMID: </span><a href="/pubmed/324276" target="_blank">324276</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Ventricular%20preexcitation%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (162)</a></div><h3 class="subhead">Therapy</h3>
<div class="nl"><a target="_blank" href="/pubmed/36891895">Ablation of Ventricular Preexcitation to Cure Preexcitation-Induced Dilated Cardiomyopathy in Infants: Diagnosis and Outcome.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Zhang Y,
Jiang H,
Cui J,
Li MT,
Zhou HM,
Li XM</span><br />
<span class="medgenPMjournal">Circ Arrhythm Electrophysiol</span>
2023 Apr;16(4):e011569.
Epub 2023 Mar 9
doi: 10.1161/CIRCEP.122.011569.
<span class="bold">PMID: </span><a href="/pubmed/36891895" target="_blank">36891895</a></div>
<div class="nl"><a target="_blank" href="/pubmed/20630836">Wolff-Parkinson-White syndrome in infants.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Hermosura T,
Bradshaw WT</span><br />
<span class="medgenPMjournal">Neonatal Netw</span>
2010 Jul-Aug;29(4):215-23.
doi: 10.1891/0730-0832.29.4.215.
<span class="bold">PMID: </span><a href="/pubmed/20630836" target="_blank">20630836</a></div>
<div class="nl"><a target="_blank" href="/pubmed/19732229">Cryoablation-induced ventricular preexcitation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Horduna I,
Dubuc M,
Jutras L,
Khairy P</span><br />
<span class="medgenPMjournal">J Cardiovasc Electrophysiol</span>
2010 Jan;21(1):103-4.
Epub 2009 Sep 2
doi: 10.1111/j.1540-8167.2009.01597.x.
<span class="bold">PMID: </span><a href="/pubmed/19732229" target="_blank">19732229</a></div>
<div class="nl"><a target="_blank" href="/pubmed/3573234">The management of preexcitation syndromes.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Wellens HJ,
Brugada P,
Penn OC</span><br />
<span class="medgenPMjournal">JAMA</span>
1987 May 1;257(17):2325-33.
<span class="bold">PMID: </span><a href="/pubmed/3573234" target="_blank">3573234</a></div>
<div class="nl"><a target="_blank" href="/pubmed/6381927">Preexcitation syndromes. Mechanisms and management.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Prystowsky EN,
Miles WM,
Heger JJ,
Zipes DP</span><br />
<span class="medgenPMjournal">Med Clin North Am</span>
1984 Jul;68(4):831-93.
doi: 10.1016/s0025-7125(16)31104-x.
<span class="bold">PMID: </span><a href="/pubmed/6381927" target="_blank">6381927</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Ventricular%20preexcitation%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (50)</a></div><h3 class="subhead">Prognosis</h3>
<div class="nl"><a target="_blank" href="/pubmed/37877314">Hypertrophic Cardiomyopathy and Ventricular Preexcitation in the Young: Cause and Accessory Pathway Characteristics.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Przybylski R,
Saravu Vijayashankar S,
O'Leary ET,
Hylind RJ,
Noon J,
Dionne A,
DeWitt ES,
Bezzerides VJ,
Abrams DJ</span><br />
<span class="medgenPMjournal">Circ Arrhythm Electrophysiol</span>
2023 Nov;16(11):e012191.
Epub 2023 Oct 25
doi: 10.1161/CIRCEP.123.012191.
<span class="bold">PMID: </span><a href="/pubmed/37877314" target="_blank">37877314</a><a href="/pmc/articles/PMC10843507" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/32314121">Cardiac MR manifestations in two cases of PRKAG2 mutations in a Chinese family.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Wang J,
Li X,
Xu Y</span><br />
<span class="medgenPMjournal">Int J Cardiovasc Imaging</span>
2020 Aug;36(8):1527-1531.
Epub 2020 Apr 20
doi: 10.1007/s10554-020-01848-y.
<span class="bold">PMID: </span><a href="/pubmed/32314121" target="_blank">32314121</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30827253">Risk-Stratification Strategy for Sudden Cardiac Death in the Very Young Children with Asymptomatic Ventricular Preexcitation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Rodriguez-Gonzalez M,
Castellano-Martinez A,
Perez-Reviriego AA</span><br />
<span class="medgenPMjournal">Curr Cardiol Rev</span>
2020;16(2):83-89.
doi: 10.2174/1573403X15666190301150754.
<span class="bold">PMID: </span><a href="/pubmed/30827253" target="_blank">30827253</a><a href="/pmc/articles/PMC7460710" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/29673006">Electro-vectorcardiographic demonstration of bifascicular block associated with ventricular preexcitation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Pérez-Riera AR,
Barbosa-Barros R,
Daminello-Raimundo R,
de Abreu LC,
Nikus K</span><br />
<span class="medgenPMjournal">Ann Noninvasive Electrocardiol</span>
2019 Mar;24(2):e12550.
Epub 2018 Apr 19
doi: 10.1111/anec.12550.
<span class="bold">PMID: </span><a href="/pubmed/29673006" target="_blank">29673006</a><a href="/pmc/articles/PMC6931686" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/324276">Preexcitation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Ferrer MI</span><br />
<span class="medgenPMjournal">Am J Med</span>
1977 May;62(5):715-30.
doi: 10.1016/0002-9343(77)90875-0.
<span class="bold">PMID: </span><a href="/pubmed/324276" target="_blank">324276</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Ventricular%20preexcitation%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (61)</a></div><h3 class="subhead">Clinical prediction guides</h3>
<div class="nl"><a target="_blank" href="/pubmed/37409656">Diagnosis and treatment of fetal and pediatric age patients (0-12 years) with Wolff-Parkinson-White syndrome and atrioventricular accessory pathways.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Leoni L,
Bronzetti G,
Colonna D,
Porcedda G,
Rimini A,
Silvetti MS;
Area Pediatrica, Associazione Italiana di Aritmologia e Cardiostimolazione (AIAC)</span><br />
<span class="medgenPMjournal">J Cardiovasc Med (Hagerstown)</span>
2023 Sep 1;24(9):589-601.
Epub 2023 May 29
doi: 10.2459/JCM.0000000000001484.
<span class="bold">PMID: </span><a href="/pubmed/37409656" target="_blank">37409656</a><a href="/pmc/articles/PMC10836786" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/34510237">Supraventricular Tachycardia Without Preexcitation as a Cause of Sudden Cardiac Arrest in Pediatric Patients.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Choi NH,
Silver ES,
Liberman L</span><br />
<span class="medgenPMjournal">Pediatr Cardiol</span>
2022 Jan;43(1):218-224.
Epub 2021 Sep 12
doi: 10.1007/s00246-021-02720-z.
<span class="bold">PMID: </span><a href="/pubmed/34510237" target="_blank">34510237</a></div>
<div class="nl"><a target="_blank" href="/pubmed/32778036">The Vectorcardiogram and the Main Dromotropic Disturbances.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Pérez-Riera AR,
Barbosa-Barros R,
Daminello-Raimundo R,
de Abreu LC,
Nikus K</span><br />
<span class="medgenPMjournal">Curr Cardiol Rev</span>
2021;17(1):50-59.
doi: 10.2174/1573403X16666200810105504.
<span class="bold">PMID: </span><a href="/pubmed/32778036" target="_blank">32778036</a><a href="/pmc/articles/PMC8142362" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/30827253">Risk-Stratification Strategy for Sudden Cardiac Death in the Very Young Children with Asymptomatic Ventricular Preexcitation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Rodriguez-Gonzalez M,
Castellano-Martinez A,
Perez-Reviriego AA</span><br />
<span class="medgenPMjournal">Curr Cardiol Rev</span>
2020;16(2):83-89.
doi: 10.2174/1573403X15666190301150754.
<span class="bold">PMID: </span><a href="/pubmed/30827253" target="_blank">30827253</a><a href="/pmc/articles/PMC7460710" target="_blank" class="PubMedFree">Free PMC Article</a></div>
<div class="nl"><a target="_blank" href="/pubmed/4197319">Basis of static and dynamic electrocardiographic variations in Wolff-Parkinson-White syndrome. Anatomic and electrophysiologic observations in right and left ventricular preexcitation.</a></div>
<div class="portlet_content ln"><span class="medgenPMauthor">Boineau JP,
Moore EN,
Spear JF,
Sealy WC</span><br />
<span class="medgenPMjournal">Am J Cardiol</span>
1973 Jul;32(1):32-45.
doi: 10.1016/s0002-9149(73)80084-0.
<span class="bold">PMID: </span><a href="/pubmed/4197319" target="_blank">4197319</a></div>
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Ventricular%20preexcitation%22%20AND%20Clinical%20prediction%20guides%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (83)</a></div></div>
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<div class="portlet_content ln"><ul><li><a href="https://clinicaltrials.gov/search?cond=Ventricular%20preexcitation" target="_blank">ClinicalTrials.gov</a></li></ul></div>
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