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<!--
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||
UID=101044
|
||
ConceptID=C0520557
|
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-->
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<!--imgCountBooks = 0--><h1 class="medgenTitle"><div class="MedGenTitleText">Hepatic arteriovenous malformation</div></h1><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>101044</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C0520557</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Congenital Abnormality</dd></dl></div></div><table class="medgenTable"><tbody><tr><td>Synonym:</td>
|
||
<td>Liver arteriovenous malformation</td></tr>
|
||
<tr><td><span class="bold">SNOMED CT: </span></td>
|
||
<td>Arteriovenous malformation of liver (84150000); Hepatic arteriovenous malformation (84150000)</td></tr>
|
||
<tr><td colspan="2" class="small"> </td></tr><tr><td>HPO:</td>
|
||
<td><a target="_blank" title="Human Phenotype Ontology" href="https://hpo.jax.org/app/browse/term/HP:0006574">HP:0006574</a></td></tr>
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</tbody></table></div><div class="rprt-body jig-ncbiinpagenav" data-jigconfig="smoothScroll: false, gotoTopLink: true, gotoTopLinkText: '', gotoTopLinkAttrs: {'title': 'Go to the top of the page'},allHeadingLevels: ['h1'], topOfPageTOC: true, tocId: 'my-toc'"><div id="rprt-tabs-1" class="rprt-tab"><div id="tb-termsProp-1"><div class="leftCol mgCol"><div>
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<div class="portlet mgSection" id="ID_100">
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Definition">Definition</h1><a sid="100" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln">A benign vascular lesion characterized by the presence of a complex network of communicating arterial and venous vascular structures in the liver. [from <a title="NCI Thesaurus" href="http://ncit.nci.nih.gov" class="defSource" target="_blank">NCI</a>]</div>
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</div>
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<div class="portlet mgSection" id="ID_118">
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<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Term_Hierarchy">Term Hierarchy</h1><a sid="118" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
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<div class="portlet_content ln HierarchyGTR"><div class="jig-ncbitabs"><ul><li><a href="#tabGTR">GTR</a></li><li><a href="#tabMGEN">MeSH</a></li></ul><div id="tabGTR"><div class="search_result"><div class="rprts"><div class="chiclet_legend"><span class="chiclet_list" style="position:static;"><span title="Clinical test" class="chiclet Ccolor round">C</span><span>Clinical test, </span><span title="Research test" class="chiclet Rcolor round">R</span><span>Research test, </span><span title="OMIM" class="chiclet Ocolor ">O</span><span>OMIM, </span><span title="GeneReview" class="chiclet Gcolor">G</span><span><em>GeneReviews</em>, </span><span title="ClinVar" class="chiclet Vcolor">V</span><span>ClinVar </span></span></div><div id="hierarchy" class="margin_t1"><div class="ds_tree"><ul><li class="matched_ds"><span class="chiclet_list"><span class="chiclet unavailable round" title="Clinical test">C</span><span class="chiclet unavailable round" title="Research Tests">R</span><span class="chiclet unavailable" title="OMIM">O</span><span class="chiclet unavailable" title="GeneReviews">G</span><span class="chiclet unavailable" title="ClinVar">V</span></span><span class="TLline">Hepatic arteriovenous malformation</span></li></ul></div></div></div></div></div><div id="tabMGEN"><div class="ds_tree"><ul><li><span class="TLline"><a href="/medgen/871309" ref="tree=MeSH" title="MedGen record for Abnormality of prenatal development or birth">Abnormality of prenatal development or birth</a></span><ul><li><span class="TLline"><a href="/medgen/1254" ref="tree=MeSH" title="MedGen record for Fetal anomaly">Fetal anomaly</a></span><ul><li><span class="TLline"><a href="/medgen/474891" ref="tree=MeSH" title="MedGen record for Congenital Systemic Disorder">Congenital Systemic Disorder</a></span><ul><li><span class="TLline"><a href="/medgen/777113" ref="tree=MeSH" title="MedGen record for Congenital anomaly of cardiovascular system">Congenital anomaly of cardiovascular system</a></span><ul><li><span class="TLline"><a href="/medgen/743837" ref="tree=MeSH" title="MedGen record for Congenital vascular malformation">Congenital vascular malformation</a></span><ul><li><span class="TLline"><a href="/medgen/137780" ref="tree=MeSH" title="MedGen record for Arteriovenous hemangioma/malformation">Arteriovenous hemangioma/malformation</a></span><ul><li><span class="matched_ds">Hepatic arteriovenous malformation</span></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></li></ul></div></div></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_112">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Conditions_with_this_feature">Conditions with this feature</h1><a sid="112" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln clinfeat">
|
||
<div class="divPopper rprt" id="rdis_331400"><div><strong>Juvenile polyposis/hereditary hemorrhagic telangiectasia syndrome</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>331400</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C1832942</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Hereditary hemorrhagic telangiectasia (HHT) is characterized by the presence of multiple arteriovenous malformations (AVMs) that lack intervening capillaries and result in direct connections between arteries and veins. The most common clinical manifestation is spontaneous and recurrent nosebleeds (epistaxis) beginning on average at age 12 years. Telangiectases (small AVMs) are characteristically found on the lips, tongue, buccal and gastrointestinal (GI) mucosa, face, and fingers. The appearance of telangiectases is generally later than epistaxis but may be during childhood. Large AVMs occur most often in the lungs, liver, or brain; complications from bleeding or shunting may be sudden and catastrophic. A minority of individuals with HHT have GI bleeding, which is rarely seen before age 50 years.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/331400">Condition Record</a></div></div>
|
||
<div class="divPopper rprt" id="rdis_324960"><div><strong>Telangiectasia, hereditary hemorrhagic, type 2</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>324960</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C1838163</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Hereditary hemorrhagic telangiectasia (HHT) is characterized by the presence of multiple arteriovenous malformations (AVMs) that lack intervening capillaries and result in direct connections between arteries and veins. The most common clinical manifestation is spontaneous and recurrent nosebleeds (epistaxis) beginning on average at age 12 years. Telangiectases (small AVMs) are characteristically found on the lips, tongue, buccal and gastrointestinal (GI) mucosa, face, and fingers. The appearance of telangiectases is generally later than epistaxis but may be during childhood. Large AVMs occur most often in the lungs, liver, or brain; complications from bleeding or shunting may be sudden and catastrophic. A minority of individuals with HHT have GI bleeding, which is rarely seen before age 50 years.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/324960">Condition Record</a></div></div>
|
||
<div class="divPopper rprt" id="rdis_1643786"><div><strong>Telangiectasia, hereditary hemorrhagic, type 1</strong><div class="aux"><div class="resc"><dl class="rprtid"><dt>MedGen UID: </dt><dd>1643786</dd><dt><span class="dotprefix"> •</span>Concept ID: </dt><dd><a href="/medgen/docs/help/#sources" target="_blank" title="Concept Unique Identifier from NLM's Unified Medical Language system (UMLS) Click for more information.">C4551861</a></dd><dt><span class="dotprefix"> •</span></dt><dd>Disease or Syndrome</dd></dl></div></div></div>
|
||
<div class="spaceAbove">Hereditary hemorrhagic telangiectasia (HHT) is characterized by the presence of multiple arteriovenous malformations (AVMs) that lack intervening capillaries and result in direct connections between arteries and veins. The most common clinical manifestation is spontaneous and recurrent nosebleeds (epistaxis) beginning on average at age 12 years. Telangiectases (small AVMs) are characteristically found on the lips, tongue, buccal and gastrointestinal (GI) mucosa, face, and fingers. The appearance of telangiectases is generally later than epistaxis but may be during childhood. Large AVMs occur most often in the lungs, liver, or brain; complications from bleeding or shunting may be sudden and catastrophic. A minority of individuals with HHT have GI bleeding, which is rarely seen before age 50 years.</div>
|
||
<div class="spaceAbove nowrap">See: <a href="/medgen/1643786">Condition Record</a></div></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_331400" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Juvenile polyposis/hereditary hemorrhagic telangiectasia syndrome</a></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_1643786" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Telangiectasia, hereditary hemorrhagic, type 1</a></div>
|
||
<div class="hangingIndent"><a title="click for more information" class="jig-ncbipopper" href="#rdis_324960" data-jigconfig="hasArrow: true, openEvent: 'click', closeEvent: 'mouseout', openAnimation: 'fadeIn', closeAnimation: 'fadeOut', triggerPosition: 'center right', destPosition: 'center left', arrowDirection: 'left'">Telangiectasia, hereditary hemorrhagic, type 2</a></div></div>
|
||
</div>
|
||
|
||
<div class="portlet mgSection" id="ID_105">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Professional_guidelines">Professional guidelines</h1><a sid="105" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">PubMed<a class="help jig-ncbi-popper" data-jig="ncbipopper" href="#guidelinesHelpPM"><img class="pulldown" src="//static.pubmed.gov/portal/portal3rc.fcgi/4223267/img/4204968" /></a></h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/33138669">Prenatal diagnosis of abnormality of the umbilical portal DV complex: difficulty in universal classification due to various alternative routes in hepatic circulation for placental drainage.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Demirci O,
|
||
Akay HÖ</span><br />
|
||
<span class="medgenPMjournal">J Matern Fetal Neonatal Med</span>
|
||
2022 Oct;35(20):3872-3884.
|
||
Epub 2020 Nov 2
|
||
doi: 10.1080/14767058.2020.1842870.
|
||
<span class="bold">PMID: </span><a href="/pubmed/33138669" target="_blank">33138669</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/16155196">Genotype-phenotype relationship in hereditary haemorrhagic telangiectasia.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Letteboer TG,
|
||
Mager JJ,
|
||
Snijder RJ,
|
||
Koeleman BP,
|
||
Lindhout D,
|
||
Ploos van Amstel JK,
|
||
Westermann CJ</span><br />
|
||
<span class="medgenPMjournal">J Med Genet</span>
|
||
2006 Apr;43(4):371-7.
|
||
Epub 2005 Sep 9
|
||
doi: 10.1136/jmg.2005.035451.
|
||
<span class="bold">PMID: </span><a href="/pubmed/16155196" target="_blank">16155196</a><a href="/pmc/articles/PMC2563220" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=(%22hepatic%20arteriovenous%20malformation%22%5Btiab%3A~0%5D)%20AND%20(%22english%20and%20humans%22%5BFilter%5D)%20AND%20(%20(%22practice%20guideline%22%5BFilter%5D)%20OR%20(practice*%5Btitl%5D%20AND%20(guideline%5Btitl%5D%20OR%20parameter%5Btitl%5D%20OR%20resource%5Btitl%5D%20OR%20bulletin%5Btitl%5D%20OR%20best%5Btitl%5D))%20OR%20(genetic*%5Btitl%5D%20AND%20(evaluation%5Btitl%5D%20OR%20counseling%5Btitl%5D%20OR%20screening%5Btitl%5D%20OR%20test*%5Btitl%5D))%20OR%20(clinical%5Btitl%5D%20AND%20((expert%5Btitl%5D%20AND%20consensus%5Btitl%5D)%20OR%20utility%5Btitl%5D%20OR%20guideline*%5Btitl%5D))%20OR%20(management%5Btitl%5D%20AND%20(clinical%5Btitl%5D%20OR%20diagnos*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20pain%5Btitl%5D%20OR%20surveillance%5Btitl%5D%20OR%20emergency%5Btitl%5D%20OR%20guideline*%5Btitl%5D%20OR%20therap*))%20OR%20(treatment%5Btitl%5D%20AND%20((evaluation%5Btitl%5D%20AND%20diagnosis%5Btitl%5D)%20OR%20(assessment%5Btitl%5D%20AND%20prevention%5Btitl%5D)%20OR%20therap*))%20OR%20(Diagnos*%5Btitl%5D%20AND%20(prenatal%5Btitl%5D%20OR%20treatment%5Btitl%5D%20OR%20follow-up%5Btitl%5D%20OR%20statement%5Btitl%5D%20OR%20criteria%5Btitl%5D%20OR%20newborn%5Btitl%5D%20OR%20differential%5Btitl%5D%20OR%20neonatal%5Btitl%5D%20OR%20neonate%5Btitl%5D))%20OR%20(guideline*%5Btitl%5D%20AND%20(pharmacogenetic*%5Btitl%5D%20OR%20recommendation%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20evidence-based%5Btitl%5D%20OR%20consensus%5Btitl%5D%20OR%20(technical%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20(molecular%5Btitl%5D%20AND%20testing%5Btitl%5D)))%20OR%20(risk%5Btitl%5D%20AND%20assessment%5Btitl%5D)%20OR%20(recommendation*%5Btitl%5D%20AND%20(statement%5Btitl%5D%20OR%20Evidence-based%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(care%20AND%20((Patient%5Btitl%5D%20AND%20standard*%5Btitl%5D)%20OR%20primary%5Btitl%5D%20OR%20psychosocial%5Btitl%5D))%20OR%20(Health%5Btitl%5D%20AND%20supervision%5Btitl%5D)%20OR%20(statement%5Btitl%5D%20AND%20(policy%5Btitl%5D%20OR%20position%5Btitl%5D%20OR%20Consensus%5Btitl%5D))%20OR%20(pharmacogenetics%5Btitl%5D%20AND%20(Dosing%5Btitl%5D%20OR%20therap*%5Btitl%5D%20OR%20genotype*%5Btitl%5D%20OR%20drug*%5Btitl%5D))%20OR%20(Chemotherapy%5Btitl%5D%20AND%20decision*%5Btitl%5D)%20OR%20(screening%5Btitl%5D%20AND%20(newborn%5Btitl%5D%20OR%20neonat*%5Btitl%5D%20OR%20detection%5Btitl%5D%20OR%20diagnos*%5Btitl%5D))%20OR%20(criteria%5Btitl%5D%20OR%20genotype*%5Btitl%5D)%20)%20NOT%20(%22Case%20reports%22%5BPublication%20type%5D%20OR%20%22clinical%20study%22%5BPublication%20Type%5D%20OR%20%22randomized%20controlled%20trial%22%5BPublication%20Type%5D)" title="PubMed search">See all (2)</a></div></div>
|
||
</div>
|
||
<div class="display-none help-popup" id="guidelinesHelpPM">These guidelines are articles in PubMed that match specific search criteria developed by MedGen to capture the most relevant practice guidelines. This list may not be comprehensive and may include broader topics as well. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div><div class="display-none help-popup" id="guidelinesHelpCurated">These guidelines are manually curated by the MedGen team
|
||
to supplement articles available in PubMed. See the <a href="/medgen/docs/faq/" title="Frequently asked questions" target="_blank">FAQ</a> for details.</div>
|
||
<div class="portlet mgSection" id="ID_103">
|
||
<div class="portlet_head mgSectionHead ui-widget-header"><h1 class="nl" id="Recent_clinical_studies">Recent clinical studies</h1><a sid="103" href="#" class="portlet_shutter" title="Show/hide content"></a></div>
|
||
<div class="portlet_content ln"><h3 class="subhead">Etiology</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/33138669">Prenatal diagnosis of abnormality of the umbilical portal DV complex: difficulty in universal classification due to various alternative routes in hepatic circulation for placental drainage.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Demirci O,
|
||
Akay HÖ</span><br />
|
||
<span class="medgenPMjournal">J Matern Fetal Neonatal Med</span>
|
||
2022 Oct;35(20):3872-3884.
|
||
Epub 2020 Nov 2
|
||
doi: 10.1080/14767058.2020.1842870.
|
||
<span class="bold">PMID: </span><a href="/pubmed/33138669" target="_blank">33138669</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/32962750">Sequence variations of ACVRL1 play a critical role in hepatic vascular malformations in hereditary hemorrhagic telangiectasia.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Giraud S,
|
||
Bardel C,
|
||
Dupuis-Girod S,
|
||
Carette MF,
|
||
Gilbert-Dussardier B,
|
||
Riviere S,
|
||
Saurin JC,
|
||
Eyries M,
|
||
Patri S,
|
||
Decullier E,
|
||
Calender A,
|
||
Lesca G</span><br />
|
||
<span class="medgenPMjournal">Orphanet J Rare Dis</span>
|
||
2020 Sep 22;15(1):254.
|
||
doi: 10.1186/s13023-020-01533-2.
|
||
<span class="bold">PMID: </span><a href="/pubmed/32962750" target="_blank">32962750</a><a href="/pmc/articles/PMC7507685" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/31362328">Single-Center Study: Evaluating the Diagnostic Performance and Safety of Contrast-Enhanced Ultrasound (CEUS) in Pregnant Women to Assess Hepatic Lesions.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Schwarze V,
|
||
Marschner C,
|
||
Negrão de Figueiredo G,
|
||
Rübenthaler J,
|
||
Clevert DA</span><br />
|
||
<span class="medgenPMjournal">Ultraschall Med</span>
|
||
2020 Feb;41(1):29-35.
|
||
Epub 2019 Jul 30
|
||
doi: 10.1055/a-0973-8517.
|
||
<span class="bold">PMID: </span><a href="/pubmed/31362328" target="_blank">31362328</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/21996781">Transcatheter embolization of congenital hepatic arteriovenous malformation using ethylene-vinyl alcohol copolymer (Onyx).</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Zanjani KS,
|
||
Mazloumi M,
|
||
Zeinaloo A,
|
||
Hedayati M,
|
||
Khalilzadeh O,
|
||
Yazdi HR</span><br />
|
||
<span class="medgenPMjournal">Diagn Interv Radiol</span>
|
||
2012 Mar-Apr;18(2):231-5.
|
||
Epub 2011 Oct 14
|
||
doi: 10.4261/1305-3825.DIR.4418-11.0.
|
||
<span class="bold">PMID: </span><a href="/pubmed/21996781" target="_blank">21996781</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/19209381">Living donor liver transplantation as a means of rescuing post-embolization hepatic failure in a patient with idiopathic intrahepatic arteriovenous malformation in the liver.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Nishimori A,
|
||
Okajima H,
|
||
Okumura K,
|
||
Yoneyama T,
|
||
Takeichi T,
|
||
Asonuma K,
|
||
Ikeda O,
|
||
Inomata Y</span><br />
|
||
<span class="medgenPMjournal">J Hepatobiliary Pancreat Surg</span>
|
||
2009;16(3):382-5.
|
||
Epub 2009 Feb 10
|
||
doi: 10.1007/s00534-008-0032-z.
|
||
<span class="bold">PMID: </span><a href="/pubmed/19209381" target="_blank">19209381</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hepatic%20arteriovenous%20malformation%22%20AND%20Etiology%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (5)</a></div><h3 class="subhead">Diagnosis</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/38960693">Hereditary Hemorrhagic Telangiectasia with Recurrent Epistaxis, Telangiectasia, Hepatic Arteriovenous Malformation, and a Poorly Developed Middle Cerebral Artery in a Patient with a Novel Mutation in the ACVRL1 Gene.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Miki T,
|
||
Ishikura T,
|
||
Fujita N,
|
||
Nakano T,
|
||
Kimura H,
|
||
Sumi-Akamaru H,
|
||
Naka T</span><br />
|
||
<span class="medgenPMjournal">Intern Med</span>
|
||
2025 Feb 1;64(3):477-480.
|
||
Epub 2024 Jul 4
|
||
doi: 10.2169/internalmedicine.3485-24.
|
||
<span class="bold">PMID: </span><a href="/pubmed/38960693" target="_blank">38960693</a><a href="/pmc/articles/PMC11867738" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/34132417">Hepatic Arteriovenous Malformation: The Search for a PTEN Mutation!</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Duhaut L,
|
||
Eyries M,
|
||
Lewin M,
|
||
Ciacio O,
|
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Kounis I,
|
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Cherqui D,
|
||
Antonini T,
|
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Duclos-Vallée JC,
|
||
Feray C,
|
||
Samuel D,
|
||
Guettier C,
|
||
Coilly A</span><br />
|
||
<span class="medgenPMjournal">Hepatology</span>
|
||
2021 Aug;74(2):1121-1123.
|
||
Epub 2021 Jun 15
|
||
doi: 10.1002/hep.31694.
|
||
<span class="bold">PMID: </span><a href="/pubmed/34132417" target="_blank">34132417</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/33074180">Congenital Hepatic Arteriovenous Malformation Presenting as Isolated Massive Hepatomegaly in an Otherwise Healthy Neonate: A Case Report.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Tiwari C,
|
||
Nagdeve N,
|
||
Saoji R,
|
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Hatwar G,
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Sinha S,
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||
Thatte S</span><br />
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<span class="medgenPMjournal">J Mother Child</span>
|
||
2020 Jul 29;24(1):67-70.
|
||
doi: 10.34763/jmotherandchild.2020241.2002.000008.
|
||
<span class="bold">PMID: </span><a href="/pubmed/33074180" target="_blank">33074180</a><a href="/pmc/articles/PMC8518103" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/30232072">Severe pulmonary hypertension associated with hepatic arteriovenous malformation in a patient with hereditary haemorrhagic telangiectasia.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Montrivade S,
|
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Maneesow P,
|
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Osotthanakorn T,
|
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Chattranukulchai P</span><br />
|
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<span class="medgenPMjournal">BMJ Case Rep</span>
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2018 Sep 18;2018
|
||
doi: 10.1136/bcr-2018-226067.
|
||
<span class="bold">PMID: </span><a href="/pubmed/30232072" target="_blank">30232072</a><a href="/pmc/articles/PMC6150131" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/17646433">MR angiography of renal-hepatic arteriovenous malformation.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Pressacco J,
|
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Hudon G,
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Tanguay JF,
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Ugolini P</span><br />
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<span class="medgenPMjournal">AJR Am J Roentgenol</span>
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2007 Aug;189(2):W111-2.
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doi: 10.2214/AJR.05.0766.
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<span class="bold">PMID: </span><a href="/pubmed/17646433" target="_blank">17646433</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hepatic%20arteriovenous%20malformation%22%20AND%20Diagnosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (19)</a></div><h3 class="subhead">Therapy</h3>
|
||
<div class="nl"><a target="_blank" href="/pubmed/25873838">Regression of a large congenital hepatic arteriovenous malformation.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Agha HM,
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Zakaria R,
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Mostafa FA,
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Hamza H</span><br />
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<span class="medgenPMjournal">Tex Heart Inst J</span>
|
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2015 Apr;42(2):184-7.
|
||
Epub 2015 Apr 1
|
||
doi: 10.14503/THIJ-13-3660.
|
||
<span class="bold">PMID: </span><a href="/pubmed/25873838" target="_blank">25873838</a><a href="/pmc/articles/PMC4382893" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/25426243">Transarterial embolization of a hepatic arteriovenous malformation in an infant using Onyx: a case report and review of the differential diagnosis imaging findings.</a></div>
|
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<div class="portlet_content ln"><span class="medgenPMauthor">Bolus C,
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Yamada R,
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Alshora S,
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Anderson B</span><br />
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<span class="medgenPMjournal">J Radiol Case Rep</span>
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2014 Aug;8(8):33-42.
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Epub 2014 Aug 31
|
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doi: 10.3941/jrcr.v8i8.2171.
|
||
<span class="bold">PMID: </span><a href="/pubmed/25426243" target="_blank">25426243</a><a href="/pmc/articles/PMC4242145" target="_blank" class="PubMedFree">Free PMC Article</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/8625700">Unusual complications after embolization of a pulmonary arteriovenous malformation.</a></div>
|
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<div class="portlet_content ln"><span class="medgenPMauthor">Haitjema T,
|
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ten Berg JM,
|
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Overtoom TT,
|
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Ernst JM,
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Westermann CJ</span><br />
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<span class="medgenPMjournal">Chest</span>
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1996 May;109(5):1401-4.
|
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doi: 10.1378/chest.109.5.1401.
|
||
<span class="bold">PMID: </span><a href="/pubmed/8625700" target="_blank">8625700</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/1732452">Embolization of hepatic arteriovenous malformations using radiolabeled and nonradiolabeled polyvinyl alcohol sponge in a patient with hereditary hemorrhagic telangiectasia: case report.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Whiting JH Jr,
|
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Morton KA,
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Datz FL,
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1992 Feb;33(2):260-2.
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<span class="bold">PMID: </span><a href="/pubmed/1732452" target="_blank">1732452</a></div>
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<div class="nl"><a target="_blank" href="/pubmed/2911663">Mortalities associated with use of a commercial suspension of polyvinyl alcohol.</a></div>
|
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<div class="portlet_content ln"><span class="medgenPMauthor">Repa I,
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Moradian GP,
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Dehner LP,
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Tadavarthy SM,
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Hunter DW,
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Castañeda-Zúñiga WR,
|
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Wright GB,
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<span class="bold">PMID: </span><a href="/pubmed/2911663" target="_blank">2911663</a></div>
|
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<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hepatic%20arteriovenous%20malformation%22%20AND%20Therapy%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (9)</a></div><h3 class="subhead">Prognosis</h3>
|
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<div class="nl"><a target="_blank" href="/pubmed/24999773">Pulmonary hypertension and hepatic encephalopathy: lethal complications of Rendu-Osler-Weber disease.</a></div>
|
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<div class="portlet_content ln"><span class="medgenPMauthor">Ford TJ,
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Fong MW,
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Alexopolous C</span><br />
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doi: 10.4997/JRCPE.2014.207.
|
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<span class="bold">PMID: </span><a href="/pubmed/24999773" target="_blank">24999773</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/21996781">Transcatheter embolization of congenital hepatic arteriovenous malformation using ethylene-vinyl alcohol copolymer (Onyx).</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Zanjani KS,
|
||
Mazloumi M,
|
||
Zeinaloo A,
|
||
Hedayati M,
|
||
Khalilzadeh O,
|
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Yazdi HR</span><br />
|
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<span class="medgenPMjournal">Diagn Interv Radiol</span>
|
||
2012 Mar-Apr;18(2):231-5.
|
||
Epub 2011 Oct 14
|
||
doi: 10.4261/1305-3825.DIR.4418-11.0.
|
||
<span class="bold">PMID: </span><a href="/pubmed/21996781" target="_blank">21996781</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/21732018">Congenital hepatic arteriovenous malformation presenting with severe persistent pulmonary hypertension.</a></div>
|
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<div class="portlet_content ln"><span class="medgenPMauthor">Thatrimontrichai A,
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Chanvitan P,
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Janjindamai W,
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Dissaneevate S,
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Kritsaneepaiboon S,
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Hongsakul K</span><br />
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<span class="medgenPMjournal">Indian J Pediatr</span>
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2012 May;79(5):673-5.
|
||
Epub 2011 Jul 6
|
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doi: 10.1007/s12098-011-0512-z.
|
||
<span class="bold">PMID: </span><a href="/pubmed/21732018" target="_blank">21732018</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/10628935">Peripheral arterial coil embolization for hepatic arteriovenous malformation in Osler-Weber-Rendu disease; useful for controlling high output heart failure, but harmful to the liver.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Hisamatsu K,
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Ueeda M,
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Ando M,
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Koike K,
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Matsuo N,
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Matsu-ura K,
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Ueda H,
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Hirohata M,
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Imai M</span><br />
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<span class="medgenPMjournal">Intern Med</span>
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1999 Dec;38(12):962-8.
|
||
doi: 10.2169/internalmedicine.38.962.
|
||
<span class="bold">PMID: </span><a href="/pubmed/10628935" target="_blank">10628935</a></div>
|
||
|
||
<div class="nl"><a target="_blank" href="/pubmed/10228838">Intrahepatic bilomas associated with hepatic arteriovenous malformation.</a></div>
|
||
<div class="portlet_content ln"><span class="medgenPMauthor">Chen CH,
|
||
Yang PM,
|
||
Sheu JC,
|
||
Huang GT,
|
||
Tsang YM,
|
||
Lee PH,
|
||
Chen DS</span><br />
|
||
<span class="medgenPMjournal">Hepatogastroenterology</span>
|
||
1999 Jan-Feb;46(25):443-7.
|
||
<span class="bold">PMID: </span><a href="/pubmed/10228838" target="_blank">10228838</a></div>
|
||
<div><a target="_blank" href="https://pubmed.ncbi.nlm.nih.gov/?term=%22Hepatic%20arteriovenous%20malformation%22%20AND%20Prognosis%2Fbroad%5Bfilter%5D%20%20AND%20%22english%20and%20humans%22%5Bfilter%5D%20NOT%20comment%5BPTYP%5D%20NOT%20letter%5BPTYP%5D" title="PubMed search">See all (6)</a></div></div>
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