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Mandibulofacial dysostosis with mental deficiency

MedGen UID:
1632207
Concept ID:
C4692584
Disease or Syndrome
Synonym: MANDIBULOFACIAL DYSOSTOSIS WITH MENTAL RETARDATION
 
Monarch Initiative: MONDO:0009559
OMIM®: 248400

Professional guidelines

PubMed

Mouthon L, Busa T, Bretelle F, Karmous-Benailly H, Missirian C, Philip N, Sigaudy S
Am J Med Genet A 2019 Dec;179(12):2365-2373. Epub 2019 Sep 11 doi: 10.1002/ajmg.a.61359. PMID: 31509347
Trainor PA, Andrews BT
Am J Med Genet C Semin Med Genet 2013 Nov;163C(4):283-94. Epub 2013 Oct 4 doi: 10.1002/ajmg.c.31375. PMID: 24123981Free PMC Article

Recent clinical studies

Etiology

Güleray N, Koşukcu C, Oğuz S, Ürel Demir G, Taşkıran EZ, Kiper PÖŞ, Utine GE, Alanay Y, Boduroğlu K, Alikaşifoğlu M
Cleft Palate Craniofac J 2022 Sep;59(9):1114-1124. Epub 2021 Aug 19 doi: 10.1177/10556656211038115. PMID: 34410171
Wieczorek D
Clin Genet 2013 Jun;83(6):499-510. Epub 2013 Apr 8 doi: 10.1111/cge.12123. PMID: 23565775
Song D, Maher CO
Neurosurg Clin N Am 2007 Jul;18(3):499-514. doi: 10.1016/j.nec.2007.05.004. PMID: 17678751
Johansson M, Billstedt E, Danielsson S, Strömland K, Miller M, Granström G, Flodmark O, Råstam M, Gillberg C
Dev Med Child Neurol 2007 Apr;49(4):280-8. doi: 10.1111/j.1469-8749.2007.00280.x. PMID: 17376139
Pashayan H, Pinsky L, Fraser FC
J Med Genet 1970 Jun;7(2):185-8. doi: 10.1136/jmg.7.2.185. PMID: 4997787Free PMC Article

Diagnosis

Chen Y, Yang R, Chen X, Lin N, Li C, Fu Y, He A, Wang Y, Zhang T, Ma J
Mol Genet Genomic Med 2024 Apr;12(4):e2426. doi: 10.1002/mgg3.2426. PMID: 38562046Free PMC Article
Huang L, Vanstone MR, Hartley T, Osmond M, Barrowman N, Allanson J, Baker L, Dabir TA, Dipple KM, Dobyns WB, Estrella J, Faghfoury H, Favaro FP, Goel H, Gregersen PA, Gripp KW, Grix A, Guion-Almeida ML, Harr MH, Hudson C, Hunter AG, Johnson J, Joss SK, Kimball A, Kini U, Kline AD, Lauzon J, Lildballe DL, López-González V, Martinezmoles J, Meldrum C, Mirzaa GM, Morel CF, Morton JE, Pyle LC, Quintero-Rivera F, Richer J, Scheuerle AE, Schönewolf-Greulich B, Shears DJ, Silver J, Smith AC, Temple IK; UCLA Clinical Genomics Center, van de Kamp JM, van Dijk FS, Vandersteen AM, White SM, Zackai EH, Zou R; Care4Rare Canada Consortium, Bulman DE, Boycott KM, Lines MA
Hum Mutat 2016 Feb;37(2):148-54. Epub 2015 Nov 19 doi: 10.1002/humu.22924. PMID: 26507355Free PMC Article
Lehalle D, Wieczorek D, Zechi-Ceide RM, Passos-Bueno MR, Lyonnet S, Amiel J, Gordon CT
Clin Genet 2015 Nov;88(5):405-15. Epub 2015 May 1 doi: 10.1111/cge.12596. PMID: 25865758
Song D, Maher CO
Neurosurg Clin N Am 2007 Jul;18(3):499-514. doi: 10.1016/j.nec.2007.05.004. PMID: 17678751
Johansson M, Billstedt E, Danielsson S, Strömland K, Miller M, Granström G, Flodmark O, Råstam M, Gillberg C
Dev Med Child Neurol 2007 Apr;49(4):280-8. doi: 10.1111/j.1469-8749.2007.00280.x. PMID: 17376139

Therapy

Neophytou P, Artemiadis A, Hadjigeorgiou GM, Zis P
Acta Neurol Belg 2023 Oct;123(5):1693-1701. Epub 2023 Jul 19 doi: 10.1007/s13760-023-02336-5. PMID: 37468803Free PMC Article
Jiang F, Kuper H, Bright T, Qin WZ
Am J Audiol 2020 Jun 8;29(2):236-243. Epub 2020 May 21 doi: 10.1044/2020_AJA-19-00029. PMID: 32437266
Balci S, Engiz O, Alikasifoglu M, Esinler I, Sinan Beksac M
Indian J Pediatr 2008 Jun;75(6):638-40. Epub 2008 Aug 31 doi: 10.1007/s12098-008-0123-5. PMID: 18759096

Prognosis

Bano S, Nawaz A, Nasim A, Numan A, Zahid M
J Coll Physicians Surg Pak 2024 Feb;34(2):187-192. doi: 10.29271/jcpsp.2024.02.187. PMID: 38342870
Neophytou P, Artemiadis A, Hadjigeorgiou GM, Zis P
Acta Neurol Belg 2023 Oct;123(5):1693-1701. Epub 2023 Jul 19 doi: 10.1007/s13760-023-02336-5. PMID: 37468803Free PMC Article
Thomas HB, Wood KA, Buczek WA, Gordon CT, Pingault V, Attié-Bitach T, Hentges KE, Varghese VC, Amiel J, Newman WG, O'Keefe RT
Hum Mutat 2020 Aug;41(8):1372-1382. Epub 2020 May 3 doi: 10.1002/humu.24027. PMID: 32333448
Mouthon L, Busa T, Bretelle F, Karmous-Benailly H, Missirian C, Philip N, Sigaudy S
Am J Med Genet A 2019 Dec;179(12):2365-2373. Epub 2019 Sep 11 doi: 10.1002/ajmg.a.61359. PMID: 31509347
Pashayan H, Pinsky L, Fraser FC
J Med Genet 1970 Jun;7(2):185-8. doi: 10.1136/jmg.7.2.185. PMID: 4997787Free PMC Article

Clinical prediction guides

Antal G, Zsigmond A, Till Á, Szabó A, Maász A, Bene J, Hadzsiev K
Int J Mol Sci 2024 Oct 23;25(21) doi: 10.3390/ijms252111400. PMID: 39518953Free PMC Article
Chen Y, Yang R, Chen X, Lin N, Li C, Fu Y, He A, Wang Y, Zhang T, Ma J
Mol Genet Genomic Med 2024 Apr;12(4):e2426. doi: 10.1002/mgg3.2426. PMID: 38562046Free PMC Article
Bano S, Nawaz A, Nasim A, Numan A, Zahid M
J Coll Physicians Surg Pak 2024 Feb;34(2):187-192. doi: 10.29271/jcpsp.2024.02.187. PMID: 38342870
Thomas HB, Wood KA, Buczek WA, Gordon CT, Pingault V, Attié-Bitach T, Hentges KE, Varghese VC, Amiel J, Newman WG, O'Keefe RT
Hum Mutat 2020 Aug;41(8):1372-1382. Epub 2020 May 3 doi: 10.1002/humu.24027. PMID: 32333448
Cohen N, Cohen E, Gaiero A, Zecca S, Fichera G, Baldi F, Giordanetto JF, Mercier JM, Cohen A
Am J Med Genet A 2017 May;173(5):1208-1218. Epub 2017 Mar 20 doi: 10.1002/ajmg.a.38151. PMID: 28319315

Recent systematic reviews

Neophytou P, Artemiadis A, Hadjigeorgiou GM, Zis P
Acta Neurol Belg 2023 Oct;123(5):1693-1701. Epub 2023 Jul 19 doi: 10.1007/s13760-023-02336-5. PMID: 37468803Free PMC Article
Renkema RW, Caron CJJM, Wolvius EB, Dunaway DJ, Forrest CR, Padwa BL, Koudstaal MJ
Int J Oral Maxillofac Surg 2018 Jan;47(1):27-34. Epub 2017 Jul 20 doi: 10.1016/j.ijom.2017.06.009. PMID: 28736116

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