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Deafness, neurosensory autosomal recessive 21

MedGen UID:
865236
Concept ID:
C4016799
Finding
Synonym: DEAFNESS, NEUROSENSORY AUTOSOMAL RECESSIVE 21
 
OMIM®: 602574

Professional guidelines

PubMed

Ammar-Khodja F, Faugère V, Baux D, Giannesini C, Léonard S, Makrelouf M, Malek R, Djennaoui D, Zenati A, Claustres M, Roux AF
Eur J Med Genet 2009 Jul-Aug;52(4):174-9. Epub 2009 Apr 16 doi: 10.1016/j.ejmg.2009.03.018. PMID: 19375528

Recent clinical studies

Etiology

Li LP, Wei JJ, Chen JK, Wu DC, Coelho DH
Otol Neurotol 2022 Jun 1;43(5):e535-e539. Epub 2022 Feb 24 doi: 10.1097/MAO.0000000000003506. PMID: 35213479
Zalewski CK, Sydlowski SA, King KA, Bianconi S, Dang Do A, Porter FD, Brewer CC
Am J Med Genet A 2021 Apr;185(4):1131-1141. Epub 2021 Feb 2 doi: 10.1002/ajmg.a.62087. PMID: 33529473Free PMC Article
Shen J, Oza AM, Del Castillo I, Duzkale H, Matsunaga T, Pandya A, Kang HP, Mar-Heyming R, Guha S, Moyer K, Lo C, Kenna M, Alexander JJ, Zhang Y, Hirsch Y, Luo M, Cao Y, Wai Choy K, Cheng YF, Avraham KB, Hu X, Garrido G, Moreno-Pelayo MA, Greinwald J, Zhang K, Zeng Y, Brownstein Z, Basel-Salmon L, Davidov B, Frydman M, Weiden T, Nagan N, Willis A, Hemphill SE, Grant AR, Siegert RK, DiStefano MT, Amr SS, Rehm HL, Abou Tayoun AN; ClinGen Hearing Loss Working Group
Genet Med 2019 Nov;21(11):2442-2452. Epub 2019 Jun 4 doi: 10.1038/s41436-019-0535-9. PMID: 31160754Free PMC Article
Le Quesne Stabej P, Saihan Z, Rangesh N, Steele-Stallard HB, Ambrose J, Coffey A, Emmerson J, Haralambous E, Hughes Y, Steel KP, Luxon LM, Webster AR, Bitner-Glindzicz M
J Med Genet 2012 Jan;49(1):27-36. Epub 2011 Dec 1 doi: 10.1136/jmedgenet-2011-100468. PMID: 22135276Free PMC Article
McGee TL, Seyedahmadi BJ, Sweeney MO, Dryja TP, Berson EL
J Med Genet 2010 Jul;47(7):499-506. Epub 2010 May 27 doi: 10.1136/jmg.2009.075143. PMID: 20507924Free PMC Article

Diagnosis

Besci Ö, Patel KA, Yıldız G, Tüfekçi Ö, Acinikli KY, Erbaş İM, Abacı A, Böber E, Bayram MT, Yılmaz Ş, Demir K
Hormones (Athens) 2022 Sep;21(3):501-506. Epub 2022 Mar 14 doi: 10.1007/s42000-022-00352-3. PMID: 35284993Free PMC Article
Khatami S, Askari M, Bahreini F, Hashemzadeh-Chaleshtori M, Hematian S, Asgharzade S
BMC Med Genet 2020 Nov 18;21(1):226. doi: 10.1186/s12881-020-01168-x. PMID: 33208113Free PMC Article
Storey H, Savige J, Sivakumar V, Abbs S, Flinter FA
J Am Soc Nephrol 2013 Dec;24(12):1945-54. Epub 2013 Sep 19 doi: 10.1681/ASN.2012100985. PMID: 24052634Free PMC Article
McGee TL, Seyedahmadi BJ, Sweeney MO, Dryja TP, Berson EL
J Med Genet 2010 Jul;47(7):499-506. Epub 2010 May 27 doi: 10.1136/jmg.2009.075143. PMID: 20507924Free PMC Article
Malm D, Nilssen Ø
Orphanet J Rare Dis 2008 Jul 23;3:21. doi: 10.1186/1750-1172-3-21. PMID: 18651971Free PMC Article

Therapy

Wang L, Qin Y, Zhu L, Li X, Chen Y, Zhang L
Eur Arch Otorhinolaryngol 2022 Feb;279(2):695-702. Epub 2021 Mar 9 doi: 10.1007/s00405-021-06700-0. PMID: 33687508
Lagarde WH, Underwood LE, Moats-Staats BM, Calikoglu AS
Am J Med Genet A 2004 Mar 15;125A(3):299-305. doi: 10.1002/ajmg.a.20506. PMID: 14994241
Abdullah MA, Al-Hasnan Z, Okamoto E, Abomelha AM
Saudi Med J 2000 Mar;21(3):297-9. PMID: 11533803

Prognosis

Lim HD, Lee SM, Yun YJ, Lee DH, Lee JH, Oh SH, Lee SY
BMC Med Genomics 2023 Apr 11;16(1):79. doi: 10.1186/s12920-023-01506-x. PMID: 37041640Free PMC Article
Besci Ö, Patel KA, Yıldız G, Tüfekçi Ö, Acinikli KY, Erbaş İM, Abacı A, Böber E, Bayram MT, Yılmaz Ş, Demir K
Hormones (Athens) 2022 Sep;21(3):501-506. Epub 2022 Mar 14 doi: 10.1007/s42000-022-00352-3. PMID: 35284993Free PMC Article
Khatami S, Askari M, Bahreini F, Hashemzadeh-Chaleshtori M, Hematian S, Asgharzade S
BMC Med Genet 2020 Nov 18;21(1):226. doi: 10.1186/s12881-020-01168-x. PMID: 33208113Free PMC Article
Sher G, Naeem M
Eur J Med Genet 2014 Jan;57(1):21-4. Epub 2013 Nov 20 doi: 10.1016/j.ejmg.2013.11.001. PMID: 24269551
Malm D, Nilssen Ø
Orphanet J Rare Dis 2008 Jul 23;3:21. doi: 10.1186/1750-1172-3-21. PMID: 18651971Free PMC Article

Clinical prediction guides

Lim HD, Lee SM, Yun YJ, Lee DH, Lee JH, Oh SH, Lee SY
BMC Med Genomics 2023 Apr 11;16(1):79. doi: 10.1186/s12920-023-01506-x. PMID: 37041640Free PMC Article
Karempelis P, Greenlund L, Gruhl R, Dorrity J, Wagner J, Roby B
Int J Pediatr Otorhinolaryngol 2022 Apr;155:111068. Epub 2022 Feb 15 doi: 10.1016/j.ijporl.2022.111068. PMID: 35202898
Zalewski CK, Sydlowski SA, King KA, Bianconi S, Dang Do A, Porter FD, Brewer CC
Am J Med Genet A 2021 Apr;185(4):1131-1141. Epub 2021 Feb 2 doi: 10.1002/ajmg.a.62087. PMID: 33529473Free PMC Article
Sher G, Naeem M
Eur J Med Genet 2014 Jan;57(1):21-4. Epub 2013 Nov 20 doi: 10.1016/j.ejmg.2013.11.001. PMID: 24269551
Le Quesne Stabej P, Saihan Z, Rangesh N, Steele-Stallard HB, Ambrose J, Coffey A, Emmerson J, Haralambous E, Hughes Y, Steel KP, Luxon LM, Webster AR, Bitner-Glindzicz M
J Med Genet 2012 Jan;49(1):27-36. Epub 2011 Dec 1 doi: 10.1136/jmedgenet-2011-100468. PMID: 22135276Free PMC Article

Recent systematic reviews

Lim HD, Lee SM, Yun YJ, Lee DH, Lee JH, Oh SH, Lee SY
BMC Med Genomics 2023 Apr 11;16(1):79. doi: 10.1186/s12920-023-01506-x. PMID: 37041640Free PMC Article
Hansen MU, Rye Rasmussen E, Cayé-Thomasen P, Mey K
Ear Hear 2023 May-Jun 01;44(3):440-447. Epub 2022 Nov 18 doi: 10.1097/AUD.0000000000001309. PMID: 36397213
Alahmadi A, Abdelsamad Y, Salamah M, Alenzi S, Badr KM, Alghamdi S, Alsanosi A
Eur Arch Otorhinolaryngol 2022 Dec;279(12):5497-5509. Epub 2022 Jun 30 doi: 10.1007/s00405-022-07511-7. PMID: 35771280

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