Etiology
Daccò V,
Rosazza C,
Mariani A,
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Terlizzi V,
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Pediatr Pulmonol
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McNally P,
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VX15-770-124 Study Group
J Cyst Fibros
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Surace C,
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Pancreatology
2024 May;24(3):394-403.
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Fajac I,
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McKone EF,
Ramsey BW,
Sutharsan S,
Taylor-Cousar JL,
Tullis E,
Ahluwalia N,
Jun LS,
Moskowitz SM,
Prieto-Centurion V,
Tian S,
Waltz D,
Xuan F,
Zhang Y,
Rowe SM,
Polineni D;
VX18-445-104 Study Group
N Engl J Med
2021 Aug 26;385(9):815-825.
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Bagheri-Behrouzi A,
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Nährlich L
Klin Padiatr
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Diagnosis
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Agarwal R
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2021 Mar;159(3):e155-e158.
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Ren CL
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Dtsch Arztebl Int
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PMID: 28855057Free PMC Article
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Steiß JO,
Zimmer KP,
Nährlich L
Klin Padiatr
2015 Mar;227(2):96-7.
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PMID: 25751685
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Therapy
Daccò V,
Rosazza C,
Mariani A,
Rizza C,
Ingianni N,
Nazzari E,
Terlizzi V,
Blasi FA,
Alicandro G
Pediatr Pulmonol
2024 Nov;59(11):2792-2799.
Epub 2024 Jun 13
doi: 10.1002/ppul.27125.
PMID: 38869349
Barry PJ,
Mall MA,
Álvarez A,
Colombo C,
de Winter-de Groot KM,
Fajac I,
McBennett KA,
McKone EF,
Ramsey BW,
Sutharsan S,
Taylor-Cousar JL,
Tullis E,
Ahluwalia N,
Jun LS,
Moskowitz SM,
Prieto-Centurion V,
Tian S,
Waltz D,
Xuan F,
Zhang Y,
Rowe SM,
Polineni D;
VX18-445-104 Study Group
N Engl J Med
2021 Aug 26;385(9):815-825.
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PMID: 34437784Free PMC Article
Sears EH,
Gartman EJ,
Casserly BP
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Madoff L
J Pediatr
1968 Aug;73(2):244-6.
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Prognosis
McNally P,
Singh A,
McColley SA,
Davies JC,
Higgins M,
Liu M,
Lu J,
Rodriguez-Romero V,
Shih JL,
Rosenfeld M;
VX15-770-124 Study Group
J Cyst Fibros
2024 May;23(3):429-435.
Epub 2024 Apr 4
doi: 10.1016/j.jcf.2024.03.012.
PMID: 38580563
Kim MD,
Bengtson CD,
Yoshida M,
Niloy AJ,
Dennis JS,
Baumlin N,
Salathe M
J Clin Invest
2022 Jun 1;132(11)
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PMID: 35446787Free PMC Article
Barry PJ,
Mall MA,
Álvarez A,
Colombo C,
de Winter-de Groot KM,
Fajac I,
McBennett KA,
McKone EF,
Ramsey BW,
Sutharsan S,
Taylor-Cousar JL,
Tullis E,
Ahluwalia N,
Jun LS,
Moskowitz SM,
Prieto-Centurion V,
Tian S,
Waltz D,
Xuan F,
Zhang Y,
Rowe SM,
Polineni D;
VX18-445-104 Study Group
N Engl J Med
2021 Aug 26;385(9):815-825.
doi: 10.1056/NEJMoa2100665.
PMID: 34437784Free PMC Article
Baker LB,
Wolfe AS
Eur J Appl Physiol
2020 Apr;120(4):719-752.
Epub 2020 Mar 2
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PMID: 32124007Free PMC Article
Naehrig S,
Chao CM,
Naehrlich L
Dtsch Arztebl Int
2017 Aug 21;114(33-34):564-574.
doi: 10.3238/arztebl.2017.0564.
PMID: 28855057Free PMC Article
Clinical prediction guides
Daccò V,
Rosazza C,
Mariani A,
Rizza C,
Ingianni N,
Nazzari E,
Terlizzi V,
Blasi FA,
Alicandro G
Pediatr Pulmonol
2024 Nov;59(11):2792-2799.
Epub 2024 Jun 13
doi: 10.1002/ppul.27125.
PMID: 38869349
Proud D,
Duckers J
J Cyst Fibros
2023 Sep;22(5):847-850.
Epub 2023 Jun 23
doi: 10.1016/j.jcf.2023.06.002.
PMID: 37355345
Barry PJ,
Mall MA,
Álvarez A,
Colombo C,
de Winter-de Groot KM,
Fajac I,
McBennett KA,
McKone EF,
Ramsey BW,
Sutharsan S,
Taylor-Cousar JL,
Tullis E,
Ahluwalia N,
Jun LS,
Moskowitz SM,
Prieto-Centurion V,
Tian S,
Waltz D,
Xuan F,
Zhang Y,
Rowe SM,
Polineni D;
VX18-445-104 Study Group
N Engl J Med
2021 Aug 26;385(9):815-825.
doi: 10.1056/NEJMoa2100665.
PMID: 34437784Free PMC Article
Baker LB,
Wolfe AS
Eur J Appl Physiol
2020 Apr;120(4):719-752.
Epub 2020 Mar 2
doi: 10.1007/s00421-020-04323-7.
PMID: 32124007Free PMC Article
McPherson MA,
Shori DK,
Dormer RL
Biosci Rep
1988 Feb;8(1):27-33.
doi: 10.1007/BF01128969.
PMID: 2456106