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Cardiomyopathy, fatal infantile

MedGen UID:
865049
Concept ID:
C4016612
Finding
Synonym: CARDIOMYOPATHY, FATAL INFANTILE
 
OMIM®: 590045

Professional guidelines

PubMed

Darin N, Moslemi AR, Lebon S, Rustin P, Holme E, Oldfors A, Tulinius M
Neuropediatrics 2003 Dec;34(6):311-7. doi: 10.1055/s-2003-44670. PMID: 14681757

Recent clinical studies

Etiology

Poeta M, Moracas C, Calò Carducci FI, Cafagno C, Buonsenso D, Maglione M, Sgubbi S, Liberati C, Venturini E, Limongelli G, Nunziata F, Petrarca L, Mandato C, Colomba C, Guarino A; Pediatric INF-ACT Network Study Group; Collaborators of the Paediatric INF-ACT Network Study Group
Euro Surveill 2024 Nov;29(48) doi: 10.2807/1560-7917.ES.2024.29.48.2400746. PMID: 39611212Free PMC Article
Gilbert-Barness E
Ann Clin Lab Sci 2004 Winter;34(1):15-34. PMID: 15038665
Freisinger P, Horvath R, Macmillan C, Peters J, Jaksch M
J Inherit Metab Dis 2004;27(1):67-79. doi: 10.1023/B:BOLI.0000016614.47380.2f. PMID: 14970747
Robinson BH
Pediatr Res 2000 Nov;48(5):581-5. doi: 10.1203/00006450-200011000-00004. PMID: 11044474
Loeffen JL, Smeitink JA, Trijbels JM, Janssen AJ, Triepels RH, Sengers RC, van den Heuvel LP
Hum Mutat 2000;15(2):123-34. doi: 10.1002/(SICI)1098-1004(200002)15:2<123::AID-HUMU1>3.0.CO;2-P. PMID: 10649489

Diagnosis

Poeta M, Moracas C, Calò Carducci FI, Cafagno C, Buonsenso D, Maglione M, Sgubbi S, Liberati C, Venturini E, Limongelli G, Nunziata F, Petrarca L, Mandato C, Colomba C, Guarino A; Pediatric INF-ACT Network Study Group; Collaborators of the Paediatric INF-ACT Network Study Group
Euro Surveill 2024 Nov;29(48) doi: 10.2807/1560-7917.ES.2024.29.48.2400746. PMID: 39611212Free PMC Article
Dedeoglu S, Dede E, Oztunc F, Gedikbasi A, Yesil G, Dedeoglu R
Orphanet J Rare Dis 2022 Sep 15;17(1):359. doi: 10.1186/s13023-022-02483-7. PMID: 36109815Free PMC Article
Finsterer J, Stöllberger C
Pediatr Neurol 2015 Dec;53(6):473-7. Epub 2015 Aug 28 doi: 10.1016/j.pediatrneurol.2015.08.014. PMID: 26507755
Alfadhel M, Lillquist YP, Waters PJ, Sinclair G, Struys E, McFadden D, Hendson G, Hyams L, Shoffner J, Vallance HD
Am J Med Genet A 2011 Apr;155A(4):840-4. Epub 2011 Mar 15 doi: 10.1002/ajmg.a.33881. PMID: 21412973
Inwald DP, Yen Ho S, Shepherd MN, Daubeney PE
Arch Dis Child 2006 Nov;91(11):928. doi: 10.1136/adc.2006.103093. PMID: 17056867Free PMC Article

Therapy

Poeta M, Moracas C, Calò Carducci FI, Cafagno C, Buonsenso D, Maglione M, Sgubbi S, Liberati C, Venturini E, Limongelli G, Nunziata F, Petrarca L, Mandato C, Colomba C, Guarino A; Pediatric INF-ACT Network Study Group; Collaborators of the Paediatric INF-ACT Network Study Group
Euro Surveill 2024 Nov;29(48) doi: 10.2807/1560-7917.ES.2024.29.48.2400746. PMID: 39611212Free PMC Article
Hordeaux J, Dubreil L, Robveille C, Deniaud J, Pascal Q, Dequéant B, Pailloux J, Lagalice L, Ledevin M, Babarit C, Costiou P, Jamme F, Fusellier M, Mallem Y, Ciron C, Huchet C, Caillaud C, Colle MA
Acta Neuropathol Commun 2017 Sep 6;5(1):66. doi: 10.1186/s40478-017-0464-2. PMID: 28874182Free PMC Article
Glatz AC, Pawel BR, Hsu DT, Weinberg P, Chrisant MR
Pediatr Transplant 2006 Mar;10(2):225-33. doi: 10.1111/j.1399-3046.2005.00414.x. PMID: 16573612
Freisinger P, Horvath R, Macmillan C, Peters J, Jaksch M
J Inherit Metab Dis 2004;27(1):67-79. doi: 10.1023/B:BOLI.0000016614.47380.2f. PMID: 14970747
Ibdah JA, Dasouki MJ, Strauss AW
J Inherit Metab Dis 1999 Oct;22(7):811-4. doi: 10.1023/a:1005506024055. PMID: 10518281

Prognosis

Tamamitsu AM, Nakagama Y, Domoto Y, Yoshida K, Ogawa S, Hirono K, Shindo T, Ogawa Y, Nakano K, Asakai H, Hirata Y, Matsui H, Inuzuka R
Int Heart J 2021 Mar 30;62(2):445-447. Epub 2021 Mar 17 doi: 10.1536/ihj.20-639. PMID: 33731536
Schaffer LR, Caltharp SA, Milla SS, Kogon BF, Cundiff CA, Dalal A, Quigley PC, Shehata BM
Cardiovasc Pathol 2016 Jan-Feb;25(1):72-7. Epub 2015 Aug 31 doi: 10.1016/j.carpath.2015.08.011. PMID: 26419627
Inwald DP, Yen Ho S, Shepherd MN, Daubeney PE
Arch Dis Child 2006 Nov;91(11):928. doi: 10.1136/adc.2006.103093. PMID: 17056867Free PMC Article
Glatz AC, Pawel BR, Hsu DT, Weinberg P, Chrisant MR
Pediatr Transplant 2006 Mar;10(2):225-33. doi: 10.1111/j.1399-3046.2005.00414.x. PMID: 16573612
Elleder M, Shin YS, Zuntová A, Vojtovic P, Chalupecký V
Virchows Arch A Pathol Anat Histopathol 1993;423(4):303-7. doi: 10.1007/BF01606895. PMID: 8236826

Clinical prediction guides

Dedeoglu S, Dede E, Oztunc F, Gedikbasi A, Yesil G, Dedeoglu R
Orphanet J Rare Dis 2022 Sep 15;17(1):359. doi: 10.1186/s13023-022-02483-7. PMID: 36109815Free PMC Article
Spiegel R, Saada A, Flannery PJ, Burté F, Soiferman D, Khayat M, Eisner V, Vladovski E, Taylor RW, Bindoff LA, Shaag A, Mandel H, Schuler-Furman O, Shalev SA, Elpeleg O, Yu-Wai-Man P
J Med Genet 2016 Feb;53(2):127-31. Epub 2015 Nov 11 doi: 10.1136/jmedgenet-2015-103361. PMID: 26561570Free PMC Article
Leary SC, Antonicka H, Sasarman F, Weraarpachai W, Cobine PA, Pan M, Brown GK, Brown R, Majewski J, Ha KC, Rahman S, Shoubridge EA
Hum Mutat 2013 Oct;34(10):1366-70. Epub 2013 Aug 12 doi: 10.1002/humu.22385. PMID: 23878101
Tomari Y, Hino N, Nagaike T, Suzuki T, Ueda T
J Biol Chem 2003 May 9;278(19):16828-33. Epub 2003 Mar 5 doi: 10.1074/jbc.M213216200. PMID: 12621050
Loeffen JL, Smeitink JA, Trijbels JM, Janssen AJ, Triepels RH, Sengers RC, van den Heuvel LP
Hum Mutat 2000;15(2):123-34. doi: 10.1002/(SICI)1098-1004(200002)15:2<123::AID-HUMU1>3.0.CO;2-P. PMID: 10649489

Recent systematic reviews

Fassone E, Rahman S
J Med Genet 2012 Sep;49(9):578-90. doi: 10.1136/jmedgenet-2012-101159. PMID: 22972949

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