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Progressive limb weakness

MedGen UID:
1778126
Concept ID:
C3509787
Sign or Symptom

Professional guidelines

PubMed

Helfferich J, Neuteboom RF, de Lange MMA, Benschop KSM, Van Leer-Buter CC, Meijer A, Bakker DP, de Bie E, Braakman HMH, Brandsma R, Niks EH, Niermeijer JM, Roelfsema V, Schoenmaker N, Sie LT, Niesters HG, Te Wierik MJM, Jacobs BC, Brouwer OF
Eur J Paediatr Neurol 2023 May;44:28-36. Epub 2023 Mar 22 doi: 10.1016/j.ejpn.2023.03.002. PMID: 36996587

Curated

UK NICE Guideline (NG127), Suspected neurological conditions: recognition and referral, 2023

Recent clinical studies

Etiology

Yang T, Zhu J, Kang Y, Tang C, Zhang L, Guo L
BMC Musculoskelet Disord 2024 Aug 23;25(1):661. doi: 10.1186/s12891-024-07772-9. PMID: 39174932Free PMC Article
Melkus G, Sampaio ML, Smith IC, Rakhra KS, Bourque PR, Breiner A, Zwicker J, Lochmüller H, Brais B, Warman-Chardon J
Neuromuscul Disord 2023 Jan;33(1):24-31. Epub 2022 Oct 2 doi: 10.1016/j.nmd.2022.09.010. PMID: 36462961
Wei X, Zhang X, Song Z, Wang F
J Neurol Surg A Cent Eur Neurosurg 2021 Nov;82(6):526-537. Epub 2021 Apr 12 doi: 10.1055/s-0041-1723810. PMID: 33845511
Gupta A, Kumar PS, Puri V, Saran RK, Narang P, Chowdhury D
Pract Neurol 2018 Oct;18(5):382-388. Epub 2018 May 14 doi: 10.1136/practneurol-2017-001877. PMID: 31091191
Kasarskis EJ, Mendiondo MS, Matthews DE, Mitsumoto H, Tandan R, Simmons Z, Bromberg MB, Kryscio RJ; ALS Nutrition/NIPPV Study Group
Am J Clin Nutr 2014 Apr;99(4):792-803. Epub 2014 Feb 12 doi: 10.3945/ajcn.113.069997. PMID: 24522445Free PMC Article

Diagnosis

Le Tri S, Nguyen Vinh K, Dang TQ, Umapathi T
BMJ Case Rep 2023 Oct 10;16(10) doi: 10.1136/bcr-2023-257076. PMID: 37816575Free PMC Article
Gupta A, Kumar PS, Puri V, Saran RK, Narang P, Chowdhury D
Pract Neurol 2018 Oct;18(5):382-388. Epub 2018 May 14 doi: 10.1136/practneurol-2017-001877. PMID: 31091191
Fokkink WJ, Selman MH, Dortland JR, Durmuş B, Kuitwaard K, Huizinga R, van Rijs W, Tio-Gillen AP, van Doorn PA, Deelder AM, Wuhrer M, Jacobs BC
J Proteome Res 2014 Mar 7;13(3):1722-30. Epub 2014 Feb 17 doi: 10.1021/pr401213z. PMID: 24533874
Man BL, Yuen YP, Yip SF, Ng SH
BMJ Case Rep 2013 Aug 13;2013 doi: 10.1136/bcr-2013-200205. PMID: 23943810Free PMC Article
Tsuda E, Imai T, Matsumura A, Hisahara S, Nonaka M, Shiraishi H, Motomura M, Shimohama S
Intern Med 2008;47(5):445-7. Epub 2008 Mar 3 doi: 10.2169/internalmedicine.47.0682. PMID: 18310980

Therapy

Le Tri S, Nguyen Vinh K, Dang TQ, Umapathi T
BMJ Case Rep 2023 Oct 10;16(10) doi: 10.1136/bcr-2023-257076. PMID: 37816575Free PMC Article
Tutar NK, Eyigürbüz T, Yildirim Z, Kale N
Ideggyogy Sz 2021 Jul 30;74(7-08):286-288. doi: 10.18071/isz.74.0286. PMID: 34370408
Fokkink WJ, Selman MH, Dortland JR, Durmuş B, Kuitwaard K, Huizinga R, van Rijs W, Tio-Gillen AP, van Doorn PA, Deelder AM, Wuhrer M, Jacobs BC
J Proteome Res 2014 Mar 7;13(3):1722-30. Epub 2014 Feb 17 doi: 10.1021/pr401213z. PMID: 24533874
Kasarskis EJ, Mendiondo MS, Matthews DE, Mitsumoto H, Tandan R, Simmons Z, Bromberg MB, Kryscio RJ; ALS Nutrition/NIPPV Study Group
Am J Clin Nutr 2014 Apr;99(4):792-803. Epub 2014 Feb 12 doi: 10.3945/ajcn.113.069997. PMID: 24522445Free PMC Article
Tsuda E, Imai T, Matsumura A, Hisahara S, Nonaka M, Shiraishi H, Motomura M, Shimohama S
Intern Med 2008;47(5):445-7. Epub 2008 Mar 3 doi: 10.2169/internalmedicine.47.0682. PMID: 18310980

Prognosis

Xie N, Yang G, Zhang W, Xu H, Sun Q
Neurology 2022 Apr 5;98(14):592-596. Epub 2022 Feb 10 doi: 10.1212/WNL.0000000000200008. PMID: 35145004
Wei X, Zhang X, Song Z, Wang F
J Neurol Surg A Cent Eur Neurosurg 2021 Nov;82(6):526-537. Epub 2021 Apr 12 doi: 10.1055/s-0041-1723810. PMID: 33845511
Fokkink WJ, Selman MH, Dortland JR, Durmuş B, Kuitwaard K, Huizinga R, van Rijs W, Tio-Gillen AP, van Doorn PA, Deelder AM, Wuhrer M, Jacobs BC
J Proteome Res 2014 Mar 7;13(3):1722-30. Epub 2014 Feb 17 doi: 10.1021/pr401213z. PMID: 24533874
Kasarskis EJ, Mendiondo MS, Matthews DE, Mitsumoto H, Tandan R, Simmons Z, Bromberg MB, Kryscio RJ; ALS Nutrition/NIPPV Study Group
Am J Clin Nutr 2014 Apr;99(4):792-803. Epub 2014 Feb 12 doi: 10.3945/ajcn.113.069997. PMID: 24522445Free PMC Article
Barohn RJ, Brumback RA, Mendell JR
Neuromuscul Disord 1994 May;4(3):257-62. doi: 10.1016/0960-8966(94)90027-2. PMID: 7522681

Clinical prediction guides

Valls A, Gutiérrez-Gutiérrez G, Martínez A, Ruiz-Roldán C, Camaño P, López de Munain A, Sáenz A
Muscle Nerve 2024 Apr;69(4):472-476. Epub 2024 Feb 1 doi: 10.1002/mus.28045. PMID: 38299438
He CH, Feng SF, Chen SX, Han DK, He TR, Cao JW, Mai HQ
BMC Infect Dis 2023 Mar 30;23(1):192. doi: 10.1186/s12879-023-08190-3. PMID: 36997914Free PMC Article
Melkus G, Sampaio ML, Smith IC, Rakhra KS, Bourque PR, Breiner A, Zwicker J, Lochmüller H, Brais B, Warman-Chardon J
Neuromuscul Disord 2023 Jan;33(1):24-31. Epub 2022 Oct 2 doi: 10.1016/j.nmd.2022.09.010. PMID: 36462961
Wei X, Zhang X, Song Z, Wang F
J Neurol Surg A Cent Eur Neurosurg 2021 Nov;82(6):526-537. Epub 2021 Apr 12 doi: 10.1055/s-0041-1723810. PMID: 33845511
Kasarskis EJ, Mendiondo MS, Matthews DE, Mitsumoto H, Tandan R, Simmons Z, Bromberg MB, Kryscio RJ; ALS Nutrition/NIPPV Study Group
Am J Clin Nutr 2014 Apr;99(4):792-803. Epub 2014 Feb 12 doi: 10.3945/ajcn.113.069997. PMID: 24522445Free PMC Article

Recent systematic reviews

Wei X, Zhang X, Song Z, Wang F
J Neurol Surg A Cent Eur Neurosurg 2021 Nov;82(6):526-537. Epub 2021 Apr 12 doi: 10.1055/s-0041-1723810. PMID: 33845511

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Curated

    • NICE, 2023
      UK NICE Guideline (NG127), Suspected neurological conditions: recognition and referral, 2023

    Consumer resources

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