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Normokalemic periodic paralysis, potassium-sensitive

MedGen UID:
356973
Concept ID:
C1868433
Disease or Syndrome
Synonym: Normokalemic Periodic Paralysis, Potassium-Sensitive
 
OMIM®: 170500; 603967

Professional guidelines

PubMed

Venance SL, Cannon SC, Fialho D, Fontaine B, Hanna MG, Ptacek LJ, Tristani-Firouzi M, Tawil R, Griggs RC; CINCH investigators
Brain 2006 Jan;129(Pt 1):8-17. Epub 2005 Sep 29 doi: 10.1093/brain/awh639. PMID: 16195244

Recent clinical studies

Etiology

Gun Bilgic D, Aydin Gumus A, Gerik Celebi HB, Bilgic A, Unaltuna Erginel N, Cam FS
J Clin Neurosci 2020 Aug;78:203-206. Epub 2020 Apr 23 doi: 10.1016/j.jocn.2020.04.061. PMID: 32336642
Gutmann L
Neurol Clin 2000 Feb;18(1):195-202. doi: 10.1016/s0733-8619(05)70185-7. PMID: 10658175

Diagnosis

Gun Bilgic D, Aydin Gumus A, Gerik Celebi HB, Bilgic A, Unaltuna Erginel N, Cam FS
J Clin Neurosci 2020 Aug;78:203-206. Epub 2020 Apr 23 doi: 10.1016/j.jocn.2020.04.061. PMID: 32336642
Jiang D, Gamal El-Din TM, Ing C, Lu P, Pomès R, Zheng N, Catterall WA
Nature 2018 May;557(7706):590-594. Epub 2018 May 16 doi: 10.1038/s41586-018-0120-4. PMID: 29769724Free PMC Article
Venance SL, Cannon SC, Fialho D, Fontaine B, Hanna MG, Ptacek LJ, Tristani-Firouzi M, Tawil R, Griggs RC; CINCH investigators
Brain 2006 Jan;129(Pt 1):8-17. Epub 2005 Sep 29 doi: 10.1093/brain/awh639. PMID: 16195244
Vicart S, Sternberg D, Fournier E, Ochsner F, Laforet P, Kuntzer T, Eymard B, Hainque B, Fontaine B
Neurology 2004 Dec 14;63(11):2120-7. doi: 10.1212/01.wnl.0000145768.09934.ec. PMID: 15596759
Gutmann L
Neurol Clin 2000 Feb;18(1):195-202. doi: 10.1016/s0733-8619(05)70185-7. PMID: 10658175

Therapy

Venance SL, Cannon SC, Fialho D, Fontaine B, Hanna MG, Ptacek LJ, Tristani-Firouzi M, Tawil R, Griggs RC; CINCH investigators
Brain 2006 Jan;129(Pt 1):8-17. Epub 2005 Sep 29 doi: 10.1093/brain/awh639. PMID: 16195244
Vicart S, Sternberg D, Fournier E, Ochsner F, Laforet P, Kuntzer T, Eymard B, Hainque B, Fontaine B
Neurology 2004 Dec 14;63(11):2120-7. doi: 10.1212/01.wnl.0000145768.09934.ec. PMID: 15596759

Prognosis

Gutmann L
Neurol Clin 2000 Feb;18(1):195-202. doi: 10.1016/s0733-8619(05)70185-7. PMID: 10658175

Clinical prediction guides

Hayward LJ, Kim JS, Lee MY, Zhou H, Kim JW, Misra K, Salajegheh M, Wu FF, Matsuda C, Reid V, Cros D, Hoffman EP, Renaud JM, Cannon SC, Brown RH Jr
J Clin Invest 2008 Apr;118(4):1437-49. doi: 10.1172/JCI32638. PMID: 18317596Free PMC Article
Venance SL, Cannon SC, Fialho D, Fontaine B, Hanna MG, Ptacek LJ, Tristani-Firouzi M, Tawil R, Griggs RC; CINCH investigators
Brain 2006 Jan;129(Pt 1):8-17. Epub 2005 Sep 29 doi: 10.1093/brain/awh639. PMID: 16195244

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