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Idiopathic transverse myelitis

MedGen UID:
739599
Concept ID:
C1719404
Disease or Syndrome
SNOMED CT: Idiopathic transverse myelitis (425756000)

Definition

A rare immune-mediated inflammatory demyelinating disorder of the spinal cord with motor, sensory and autonomic involvement. [from ORPHANET]

Professional guidelines

PubMed

Eckstein C, Saidha S, Levy M
J Neurol 2012 May;259(5):801-16. Epub 2011 Sep 20 doi: 10.1007/s00415-011-6240-5. PMID: 21932127
Fadil H, Kelley RE, Gonzalez-Toledo E
Int Rev Neurobiol 2007;79:393-422. doi: 10.1016/S0074-7742(07)79018-9. PMID: 17531852

Recent clinical studies

Etiology

Abboud H, Sun R, Modak N, Elkasaby M, Wang A, Levy M
J Neurol 2024 Sep;271(9):5875-5885. Epub 2024 Jul 8 doi: 10.1007/s00415-024-12527-6. PMID: 38977461Free PMC Article
Kim KW, Lee EJ, Kim SY, Jung HJ, Kim HJ, Kim S, Kim H, Seo D, So J, Kim J, Kim H, Kim KK, Lim YM
Sci Rep 2023 Mar 9;13(1):3988. doi: 10.1038/s41598-023-30755-0. PMID: 36894677Free PMC Article
Lopez Chiriboga S, Flanagan EP
Continuum (Minneap Minn) 2021 Feb 1;27(1):62-92. doi: 10.1212/CON.0000000000000900. PMID: 33522737
Smith E, Jaakonmäki N, Nylund M, Kupila L, Matilainen M, Airas L
Mult Scler Relat Disord 2020 Nov;46:102562. Epub 2020 Oct 7 doi: 10.1016/j.msard.2020.102562. PMID: 33059215
Greenberg BM, Thomas KP, Krishnan C, Kaplin AI, Calabresi PA, Kerr DA
Neurology 2007 May 8;68(19):1614-7. doi: 10.1212/01.wnl.0000260970.63493.c8. PMID: 17485649

Diagnosis

Lopez Chiriboga S, Flanagan EP
Continuum (Minneap Minn) 2021 Feb 1;27(1):62-92. doi: 10.1212/CON.0000000000000900. PMID: 33522737
Bevan CJ, Cree BA
Semin Neurol 2015 Dec;35(6):656-66. Epub 2015 Nov 23 doi: 10.1055/s-0035-1564682. PMID: 26595866
Kumar N
Semin Neurol 2010 Feb;30(1):38-43. Epub 2010 Feb 1 doi: 10.1055/s-0029-1244993. PMID: 20127580
Centers for Disease Control and Prevention (CDC)
MMWR Morb Mortal Wkly Rep 2008 May 2;57(17):460-2. PMID: 18451757
Krishnan C, Kerr DA
Arch Neurol 2005 Jun;62(6):1011-3. doi: 10.1001/archneur.62.6.1011. PMID: 15956176

Therapy

Escobar-Villalba A, Sainz de la Maza S, Pérez Torre P, Galán JC, Rodríguez-Domínguez M, Monreal Laguillo E, Martínez Ulloa PL, Buisán Catevilla J, Corral I
J Clin Virol 2016 Apr;77:63-5. Epub 2016 Feb 11 doi: 10.1016/j.jcv.2016.02.001. PMID: 26906233
Hofer MJ, Campbell IL
Br J Pharmacol 2016 Feb;173(4):716-28. Epub 2015 Jun 12 doi: 10.1111/bph.13175. PMID: 25917268Free PMC Article
Bevan CJ, Cree BA
Semin Neurol 2015 Dec;35(6):656-66. Epub 2015 Nov 23 doi: 10.1055/s-0035-1564682. PMID: 26595866
Green M, Berliner J, Frontera J
J Pediatr Rehabil Med 2012;5(1):1-6. doi: 10.3233/PRM-2011-0187. PMID: 22543887
Greenberg BM, Thomas KP, Krishnan C, Kaplin AI, Calabresi PA, Kerr DA
Neurology 2007 May 8;68(19):1614-7. doi: 10.1212/01.wnl.0000260970.63493.c8. PMID: 17485649

Prognosis

Abboud H, Sun R, Modak N, Elkasaby M, Wang A, Levy M
J Neurol 2024 Sep;271(9):5875-5885. Epub 2024 Jul 8 doi: 10.1007/s00415-024-12527-6. PMID: 38977461Free PMC Article
Lopez Chiriboga S, Flanagan EP
Continuum (Minneap Minn) 2021 Feb 1;27(1):62-92. doi: 10.1212/CON.0000000000000900. PMID: 33522737
Kumar N
Semin Neurol 2010 Feb;30(1):38-43. Epub 2010 Feb 1 doi: 10.1055/s-0029-1244993. PMID: 20127580
Ravaglia S, Bastianello S, Franciotta D, Ceroni M, Pichiecchio A, Tavazzi E, Moglia A, Marchioni E
Spinal Cord 2009 Jul;47(7):531-7. Epub 2008 Dec 23 doi: 10.1038/sc.2008.157. PMID: 19104509
Centers for Disease Control and Prevention (CDC)
MMWR Morb Mortal Wkly Rep 2008 May 2;57(17):460-2. PMID: 18451757

Clinical prediction guides

Abboud H, Sun R, Modak N, Elkasaby M, Wang A, Levy M
J Neurol 2024 Sep;271(9):5875-5885. Epub 2024 Jul 8 doi: 10.1007/s00415-024-12527-6. PMID: 38977461Free PMC Article
Lee HL, Seok JM, Chung YH, Min JH, Baek SH, Kim SM, Sohn E, Kim J, Kang SY, Hong YH, Shin HY, Cho JY, Oh J, Lee SS, Kim S, Kim SH, Kim HJ, Kim BJ, Kim BJ
Mult Scler Relat Disord 2023 Nov;79:104957. Epub 2023 Sep 1 doi: 10.1016/j.msard.2023.104957. PMID: 37688927
Kumar N
Semin Neurol 2010 Feb;30(1):38-43. Epub 2010 Feb 1 doi: 10.1055/s-0029-1244993. PMID: 20127580
Ravaglia S, Bastianello S, Franciotta D, Ceroni M, Pichiecchio A, Tavazzi E, Moglia A, Marchioni E
Spinal Cord 2009 Jul;47(7):531-7. Epub 2008 Dec 23 doi: 10.1038/sc.2008.157. PMID: 19104509
Scott TF
Acta Neurol Scand 2007 Jun;115(6):371-6. doi: 10.1111/j.1600-0404.2007.00835.x. PMID: 17511844

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