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PSORIASIS 2, PUSTULAR

MedGen UID:
865511
Concept ID:
C4017074
Finding
OMIM®: 607211

Professional guidelines

PubMed

Choon SE, van de Kerkhof P, Gudjonsson JE, de la Cruz C, Barker J, Morita A, Romiti R, Affandi AM, Asawanonda P, Burden AD, Gonzalez C, Marrakchi S, Mowla MR, Okubo Y, Oon HH, Terui T, Tsai TF, Callis-Duffin K, Fujita H, Jo SJ, Merola J, Mrowietz U, Puig L, Thaçi D, Velásquez M, Augustin M, El Sayed M, Navarini AA, Pink A, Prinz J, Turki H, Magalhães R, Capon F, Bachelez H; IPC Pustular Psoriasis Working Group
JAMA Dermatol 2024 Jul 1;160(7):758-768. doi: 10.1001/jamadermatol.2024.0915. PMID: 38691347
Morita A, Saeki H
J Dermatol 2024 Feb;51(2):185-195. Epub 2023 Dec 17 doi: 10.1111/1346-8138.17049. PMID: 38105636Free PMC Article
Garner KK, Hoy KDS, Carpenter AM
Am Fam Physician 2023 Dec;108(6):562-573. PMID: 38215417

Recent clinical studies

Etiology

Choon SE, van de Kerkhof P, Gudjonsson JE, de la Cruz C, Barker J, Morita A, Romiti R, Affandi AM, Asawanonda P, Burden AD, Gonzalez C, Marrakchi S, Mowla MR, Okubo Y, Oon HH, Terui T, Tsai TF, Callis-Duffin K, Fujita H, Jo SJ, Merola J, Mrowietz U, Puig L, Thaçi D, Velásquez M, Augustin M, El Sayed M, Navarini AA, Pink A, Prinz J, Turki H, Magalhães R, Capon F, Bachelez H; IPC Pustular Psoriasis Working Group
JAMA Dermatol 2024 Jul 1;160(7):758-768. doi: 10.1001/jamadermatol.2024.0915. PMID: 38691347
Erlandson M, Wertz MC, Rosenfeld E
Am Fam Physician 2023 Feb;107(2):152-158. PMID: 36791447
Bachelez H, Choon SE, Marrakchi S, Burden AD, Tsai TF, Morita A, Navarini AA, Zheng M, Xu J, Turki H, Anadkat MJ, Rajeswari S, Hua H, Vulcu SD, Hall D, Tetzlaff K, Thoma C, Lebwohl MG; Effisayil 1 Trial Investigators
N Engl J Med 2021 Dec 23;385(26):2431-2440. doi: 10.1056/NEJMoa2111563. PMID: 34936739
Twelves S, Mostafa A, Dand N, Burri E, Farkas K, Wilson R, Cooper HL, Irvine AD, Oon HH, Kingo K, Köks S, Mrowietz U, Puig L, Reynolds N, Tan ES, Tanew A, Torz K, Trattner H, Valentine M, Wahie S, Warren RB, Wright A, Bata-Csörgő Z, Szell M, Griffiths CEM, Burden AD, Choon SE, Smith CH, Barker JN, Navarini AA, Capon F
J Allergy Clin Immunol 2019 Mar;143(3):1021-1026. Epub 2018 Jul 21 doi: 10.1016/j.jaci.2018.06.038. PMID: 30036598Free PMC Article
Weigle N, McBane S
Am Fam Physician 2013 May 1;87(9):626-33. PMID: 23668525

Diagnosis

Garner KK, Hoy KDS, Carpenter AM
Am Fam Physician 2023 Dec;108(6):562-573. PMID: 38215417
Erlandson M, Wertz MC, Rosenfeld E
Am Fam Physician 2023 Feb;107(2):152-158. PMID: 36791447
Prinz JC, Choon SE, Griffiths CEM, Merola JF, Morita A, Ashcroft DM, Viguier M
J Eur Acad Dermatol Venereol 2023 Feb;37(2):256-273. Epub 2022 Dec 3 doi: 10.1111/jdv.18720. PMID: 36331364
Twelves S, Mostafa A, Dand N, Burri E, Farkas K, Wilson R, Cooper HL, Irvine AD, Oon HH, Kingo K, Köks S, Mrowietz U, Puig L, Reynolds N, Tan ES, Tanew A, Torz K, Trattner H, Valentine M, Wahie S, Warren RB, Wright A, Bata-Csörgő Z, Szell M, Griffiths CEM, Burden AD, Choon SE, Smith CH, Barker JN, Navarini AA, Capon F
J Allergy Clin Immunol 2019 Mar;143(3):1021-1026. Epub 2018 Jul 21 doi: 10.1016/j.jaci.2018.06.038. PMID: 30036598Free PMC Article
Weigle N, McBane S
Am Fam Physician 2013 May 1;87(9):626-33. PMID: 23668525

Therapy

Martin A, Ibraheim MK, Gupta R, Wu JJ
Dermatol Clin 2025 Jan;43(1):1-9. Epub 2024 Sep 10 doi: 10.1016/j.det.2024.08.001. PMID: 39542556
Morita A, Strober B, Burden AD, Choon SE, Anadkat MJ, Marrakchi S, Tsai TF, Gordon KB, Thaçi D, Zheng M, Hu N, Haeufel T, Thoma C, Lebwohl MG
Lancet 2023 Oct 28;402(10412):1541-1551. Epub 2023 Sep 19 doi: 10.1016/S0140-6736(23)01378-8. PMID: 37738999
Baum P, Visvanathan S, Garcet S, Roy J, Schmid R, Bossert S, Lang B, Bachelez H, Bissonnette R, Thoma C, Krueger JG
J Allergy Clin Immunol 2022 Apr;149(4):1402-1412. Epub 2021 Oct 20 doi: 10.1016/j.jaci.2021.09.035. PMID: 34678325
Bachelez H, Choon SE, Marrakchi S, Burden AD, Tsai TF, Morita A, Navarini AA, Zheng M, Xu J, Turki H, Anadkat MJ, Rajeswari S, Hua H, Vulcu SD, Hall D, Tetzlaff K, Thoma C, Lebwohl MG; Effisayil 1 Trial Investigators
N Engl J Med 2021 Dec 23;385(26):2431-2440. doi: 10.1056/NEJMoa2111563. PMID: 34936739
Weigle N, McBane S
Am Fam Physician 2013 May 1;87(9):626-33. PMID: 23668525

Prognosis

Martin A, Ibraheim MK, Gupta R, Wu JJ
Dermatol Clin 2025 Jan;43(1):1-9. Epub 2024 Sep 10 doi: 10.1016/j.det.2024.08.001. PMID: 39542556
Elewski BE, Lebwohl MG, Anadkat MJ, Barker J, Ghoreschi K, Imafuku S, Mrowietz U, Li L, Quaresma M, Thoma C, Bachelez H
J Am Acad Dermatol 2023 Jul;89(1):36-44. Epub 2023 Mar 2 doi: 10.1016/j.jaad.2023.02.040. PMID: 36870370
Choon SE, Lebwohl MG, Turki H, Zheng M, Burden AD, Li L, Quaresma M, Thoma C, Bachelez H
Dermatology 2023;239(3):345-354. Epub 2023 Feb 16 doi: 10.1159/000529274. PMID: 36796336Free PMC Article
Prinz JC, Choon SE, Griffiths CEM, Merola JF, Morita A, Ashcroft DM, Viguier M
J Eur Acad Dermatol Venereol 2023 Feb;37(2):256-273. Epub 2022 Dec 3 doi: 10.1111/jdv.18720. PMID: 36331364
Choon SE, Navarini AA, Pinter A
Am J Clin Dermatol 2022 Jan;23(Suppl 1):21-29. Epub 2022 Jan 21 doi: 10.1007/s40257-021-00654-z. PMID: 35061227Free PMC Article

Clinical prediction guides

Martin A, Ibraheim MK, Gupta R, Wu JJ
Dermatol Clin 2025 Jan;43(1):1-9. Epub 2024 Sep 10 doi: 10.1016/j.det.2024.08.001. PMID: 39542556
Passeron T, Perrot JL, Jullien D, Goujon C, Ruer M, Boyé T, Villani AP, Quiles Tsimaratos N
JAMA Dermatol 2024 Feb 1;160(2):199-203. doi: 10.1001/jamadermatol.2023.5051. PMID: 38054800Free PMC Article
Morita A, Strober B, Burden AD, Choon SE, Anadkat MJ, Marrakchi S, Tsai TF, Gordon KB, Thaçi D, Zheng M, Hu N, Haeufel T, Thoma C, Lebwohl MG
Lancet 2023 Oct 28;402(10412):1541-1551. Epub 2023 Sep 19 doi: 10.1016/S0140-6736(23)01378-8. PMID: 37738999
Elewski BE, Lebwohl MG, Anadkat MJ, Barker J, Ghoreschi K, Imafuku S, Mrowietz U, Li L, Quaresma M, Thoma C, Bachelez H
J Am Acad Dermatol 2023 Jul;89(1):36-44. Epub 2023 Mar 2 doi: 10.1016/j.jaad.2023.02.040. PMID: 36870370
Bachelez H, Choon SE, Marrakchi S, Burden AD, Tsai TF, Morita A, Navarini AA, Zheng M, Xu J, Turki H, Anadkat MJ, Rajeswari S, Hua H, Vulcu SD, Hall D, Tetzlaff K, Thoma C, Lebwohl MG; Effisayil 1 Trial Investigators
N Engl J Med 2021 Dec 23;385(26):2431-2440. doi: 10.1056/NEJMoa2111563. PMID: 34936739

Recent systematic reviews

Chen BL, Liu QW, Dong XW, Bai YP
Front Immunol 2024;15:1462158. Epub 2024 Oct 14 doi: 10.3389/fimmu.2024.1462158. PMID: 39469713Free PMC Article
Abduelmula A, Rankin BD, Sood S, Georgakopoulos JR, Mufti A, Vender R, Yeung J, Prajapati VH
J Am Acad Dermatol 2023 Aug;89(2):417-419. Epub 2023 Apr 24 doi: 10.1016/j.jaad.2023.04.031. PMID: 37100243
Wu PC, Huang IH, Wang CW, Tsai CC, Chung WH, Chen CB
Am J Clin Dermatol 2022 Nov;23(6):775-799. Epub 2022 Sep 1 doi: 10.1007/s40257-022-00721-z. PMID: 36048409Free PMC Article
Gyldenløve M, Alinaghi F, Zachariae C, Skov L, Egeberg A
Am J Clin Dermatol 2022 Sep;23(5):605-613. Epub 2022 Jun 23 doi: 10.1007/s40257-022-00703-1. PMID: 35737251
Posso-De Los Rios CJ, Pope E, Lara-Corrales I
Pediatr Dermatol 2014 Jul-Aug;31(4):430-9. Epub 2014 May 29 doi: 10.1111/pde.12351. PMID: 24890463

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