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HEMOGLOBIN S

MedGen UID:
854851
Concept ID:
C3888302
Finding
OMIM®: 141900

Professional guidelines

PubMed

Elendu C, Amaechi DC, Alakwe-Ojimba CE, Elendu TC, Elendu RC, Ayabazu CP, Aina TO, Aborisade O, Adenikinju JS
Medicine (Baltimore) 2023 Sep 22;102(38):e35237. doi: 10.1097/MD.0000000000035237. PMID: 37746969Free PMC Article
Schroeder P, Fulzele K, Forsyth S, Ribadeneira MD, Guichard S, Wilker E, Marshall CG, Drake A, Fessler R, Konstantinidis DG, Seu KG, Kalfa TA
J Pharmacol Exp Ther 2022 Mar;380(3):210-219. Epub 2022 Jan 14 doi: 10.1124/jpet.121.000743. PMID: 35031585
Jagadeeswaran R, Rivers A
Hematology Am Soc Hematol Educ Program 2017 Dec 8;2017(1):440-446. doi: 10.1182/asheducation-2017.1.440. PMID: 29222291Free PMC Article

Recent clinical studies

Etiology

Pecker LH, Lanzkron S
Ann Intern Med 2021 Jan;174(1):ITC1-ITC16. Epub 2021 Jan 12 doi: 10.7326/AITC202101190. PMID: 33428443
Nader E, Romana M, Connes P
Front Immunol 2020;11:454. Epub 2020 Mar 13 doi: 10.3389/fimmu.2020.00454. PMID: 32231672Free PMC Article
Vichinsky E, Hoppe CC, Ataga KI, Ware RE, Nduba V, El-Beshlawy A, Hassab H, Achebe MM, Alkindi S, Brown RC, Diuguid DL, Telfer P, Tsitsikas DA, Elghandour A, Gordeuk VR, Kanter J, Abboud MR, Lehrer-Graiwer J, Tonda M, Intondi A, Tong B, Howard J; HOPE Trial Investigators
N Engl J Med 2019 Aug 8;381(6):509-519. Epub 2019 Jun 14 doi: 10.1056/NEJMoa1903212. PMID: 31199090
Buchanan GR, DeBaun MR, Quinn CT, Steinberg MH
Hematology Am Soc Hematol Educ Program 2004:35-47. doi: 10.1182/asheducation-2004.1.35. PMID: 15561675
Kark JA, Ward FT
Semin Hematol 1994 Jul;31(3):181-225. PMID: 7973777

Diagnosis

Elendu C, Amaechi DC, Alakwe-Ojimba CE, Elendu TC, Elendu RC, Ayabazu CP, Aina TO, Aborisade O, Adenikinju JS
Medicine (Baltimore) 2023 Sep 22;102(38):e35237. doi: 10.1097/MD.0000000000035237. PMID: 37746969Free PMC Article
Pecker LH, Lanzkron S
Ann Intern Med 2021 Jan;174(1):ITC1-ITC16. Epub 2021 Jan 12 doi: 10.7326/AITC202101190. PMID: 33428443
Nader E, Romana M, Connes P
Front Immunol 2020;11:454. Epub 2020 Mar 13 doi: 10.3389/fimmu.2020.00454. PMID: 32231672Free PMC Article
Yosmanovich D, Rotter M, Aprelev A, Ferrone FA
J Mol Biol 2016 Apr 24;428(8):1506-14. Epub 2016 Mar 11 doi: 10.1016/j.jmb.2016.03.001. PMID: 26975885
McCurdy PR, Lorkin PA, Casey R, Lehmann H, Uddin DE, Dickson LG
Am J Med 1974 Oct;57(4):665-70. doi: 10.1016/0002-9343(74)90021-7. PMID: 4432868

Therapy

Ferraresi M, Panzieri DL, Leoni S, Cappellini MD, Kattamis A, Motta I
Eur J Pediatr 2023 Jun;182(6):2509-2519. Epub 2023 Mar 31 doi: 10.1007/s00431-023-04900-w. PMID: 36997768Free PMC Article
Lettre G
Cell 2020 Mar 5;180(5):819. doi: 10.1016/j.cell.2020.01.019. PMID: 32142671
Vichinsky E, Hoppe CC, Ataga KI, Ware RE, Nduba V, El-Beshlawy A, Hassab H, Achebe MM, Alkindi S, Brown RC, Diuguid DL, Telfer P, Tsitsikas DA, Elghandour A, Gordeuk VR, Kanter J, Abboud MR, Lehrer-Graiwer J, Tonda M, Intondi A, Tong B, Howard J; HOPE Trial Investigators
N Engl J Med 2019 Aug 8;381(6):509-519. Epub 2019 Jun 14 doi: 10.1056/NEJMoa1903212. PMID: 31199090
Eaton WA, Bunn HF
Blood 2017 May 18;129(20):2719-2726. Epub 2017 Apr 6 doi: 10.1182/blood-2017-02-765891. PMID: 28385699Free PMC Article
Ribeil JA, Hacein-Bey-Abina S, Payen E, Magnani A, Semeraro M, Magrin E, Caccavelli L, Neven B, Bourget P, El Nemer W, Bartolucci P, Weber L, Puy H, Meritet JF, Grevent D, Beuzard Y, Chrétien S, Lefebvre T, Ross RW, Negre O, Veres G, Sandler L, Soni S, de Montalembert M, Blanche S, Leboulch P, Cavazzana M
N Engl J Med 2017 Mar 2;376(9):848-855. doi: 10.1056/NEJMoa1609677. PMID: 28249145

Prognosis

D'Alessandro A, Le K, Lundt M, Li Q, Dunkelberger EB, Cellmer T, Worth AJ, Patil S, Huston C, Grier A, Dzieciatkowska M, Stephenson D, Eaton WA, Thein SL
Haematologica 2024 Aug 1;109(8):2639-2652. doi: 10.3324/haematol.2023.284831. PMID: 38450513Free PMC Article
Metaferia B, Cellmer T, Dunkelberger EB, Li Q, Henry ER, Hofrichter J, Staton D, Hsieh MM, Conrey AK, Tisdale JF, Chatterjee AK, Thein SL, Eaton WA
Proc Natl Acad Sci U S A 2022 Oct 4;119(40):e2210779119. Epub 2022 Sep 26 doi: 10.1073/pnas.2210779119. PMID: 36161945Free PMC Article
Uyoga S, Watson JA, Wanjiku P, Rop JC, Makale J, Macharia AW, Kariuki SN, Nyutu GM, Shebe M, Mosobo M, Mturi N, Rockett KA, Woodrow CJ, Dondorp AM, Maitland K, White NJ, Williams TN
Nat Commun 2022 Jun 8;13(1):3307. doi: 10.1038/s41467-022-30990-5. PMID: 35676275Free PMC Article
Yosmanovich D, Rotter M, Aprelev A, Ferrone FA
J Mol Biol 2016 Apr 24;428(8):1506-14. Epub 2016 Mar 11 doi: 10.1016/j.jmb.2016.03.001. PMID: 26975885
Buchanan GR, DeBaun MR, Quinn CT, Steinberg MH
Hematology Am Soc Hematol Educ Program 2004:35-47. doi: 10.1182/asheducation-2004.1.35. PMID: 15561675

Clinical prediction guides

Choi J, Markantonis JE, De Simone N, Nero A, Kim J, Sarode R
J Clin Apher 2023 Dec;38(6):677-684. Epub 2023 Aug 1 doi: 10.1002/jca.22078. PMID: 37525930
Fertrin KY, Samsel L, van Beers EJ, Mendelsohn L, Kato GJ, McCoy JP Jr
Methods Mol Biol 2016;1389:279-92. doi: 10.1007/978-1-4939-3302-0_20. PMID: 27460253Free PMC Article
Yosmanovich D, Rotter M, Aprelev A, Ferrone FA
J Mol Biol 2016 Apr 24;428(8):1506-14. Epub 2016 Mar 11 doi: 10.1016/j.jmb.2016.03.001. PMID: 26975885
Mohanty D, Mukherjee MB, Colah RB, Wadia M, Ghosh K, Chottray GP, Jain D, Italia Y, Ashokan KS, Kaul R, Shukla DK, Muthuswamy V
Asia Pac J Public Health 2015 Mar;27(2):NP562-71. Epub 2013 Mar 19 doi: 10.1177/1010539513480231. PMID: 23513007
Buchanan GR, DeBaun MR, Quinn CT, Steinberg MH
Hematology Am Soc Hematol Educ Program 2004:35-47. doi: 10.1182/asheducation-2004.1.35. PMID: 15561675

Recent systematic reviews

Lundgren CR
Am J Clin Pathol 2022 Nov 3;158(5):574-582. doi: 10.1093/ajcp/aqac103. PMID: 36048898
Olowoyeye A, Okwundu CI
Cochrane Database Syst Rev 2020 Nov 30;11(11):CD007652. doi: 10.1002/14651858.CD007652.pub7. PMID: 33251574Free PMC Article
Yue H, Xu X, Liu Q, Li X, Jiang W, Hu B
Hematology 2020 Dec;25(1):309-319. doi: 10.1080/16078454.2020.1748927. PMID: 32783601
Olowoyeye A, Okwundu CI
Cochrane Database Syst Rev 2018 Nov 16;11(11):CD007652. doi: 10.1002/14651858.CD007652.pub6. PMID: 30480767Free PMC Article
Olowoyeye A, Okwundu CI
Cochrane Database Syst Rev 2016 Nov 14;11:CD007652. doi: 10.1002/14651858.CD007652.pub5. PMID: 27841932

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

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    Consumer resources