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Eccrine porocarcinoma

MedGen UID:
266098
Concept ID:
C1266065
Neoplastic Process
Synonyms: Eccrine Porocarcinoma; Eccrine Porocarcinomas; Eccrine Poroma, Malignant; Eccrine Poromas, Malignant; Malignant Eccrine Poroma; Malignant Eccrine Poromas; Porocarcinoma, Eccrine; Porocarcinomas, Eccrine; Poroma, Malignant Eccrine; Poromas, Malignant Eccrine
SNOMED CT: Porocarcinoma (128685001); Eccrine poroma, malignant (128685001); Eccrine porocarcinoma of skin (254708001); Eccrine porocarcinoma (254708001); Eccrine porocarcinoma (128685001)
 
Monarch Initiative: MONDO:0006189

Definition

A carcinoma with eccrine differentiation arising from the sweat glands. It may arise de novo or as a malignant transformation of a pre-existing poroma. It usually grows in the legs, buttocks, feet, and trunk and usually presents as an ulcerative plaque. It is characterized by the presence of intraepidermal and dermal nests of malignant epithelial cells. It may recur after excision and metastasize to the lymph nodes and less frequently to distal anatomic sites. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • Eccrine porocarcinoma

Professional guidelines

PubMed

Schukow C, McCalmont TH, Surprenant D, Yang HH
Am J Dermatopathol 2023 Oct 1;45(10):728-730. Epub 2023 Jul 28 doi: 10.1097/DAD.0000000000002503. PMID: 37506277

Recent clinical studies

Etiology

Joshy J, Mistry K, Levell NJ, van Bodegraven B, Vernon S, Rajan N, Craig P, Venables ZC
Clin Exp Dermatol 2022 Jun;47(6):1030-1035. Epub 2022 Mar 20 doi: 10.1111/ced.15126. PMID: 35149987
Jarocki C, Kozlow J, Harms PW, Schmidt BM
Foot Ankle Spec 2020 Oct;13(5):415-419. Epub 2020 Aug 17 doi: 10.1177/1938640020946190. PMID: 32924585
Tsunoda K, Onishi M, Maeda F, Akasaka T, Sugai T, Amano H
Acta Derm Venereol 2019 Jun 1;99(7):691-692. doi: 10.2340/00015555-3173. PMID: 30868172
Rehal B, Merin MR, Barr K
Cutis 2013 Aug;92(2):67-70. PMID: 24087778
Dubas LE, Ingraffea A
Facial Plast Surg Clin North Am 2013 Feb;21(1):43-53. doi: 10.1016/j.fsc.2012.10.003. PMID: 23369588

Diagnosis

Joshy J, Mistry K, Levell NJ, van Bodegraven B, Vernon S, Rajan N, Craig P, Venables ZC
Clin Exp Dermatol 2022 Jun;47(6):1030-1035. Epub 2022 Mar 20 doi: 10.1111/ced.15126. PMID: 35149987
Rehal B, Merin MR, Barr K
Cutis 2013 Aug;92(2):67-70. PMID: 24087778
Whitt P, Whelchel J, Ruff T
Ear Nose Throat J 1996 Aug;75(8):536-8. PMID: 8828278
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Landa NG, Winkelmann RK
J Am Acad Dermatol 1991 Jan;24(1):27-31. doi: 10.1016/0190-9622(91)70004-l. PMID: 1999525

Therapy

Lee KA, Cioni M, Robson A, Bataille V
BMJ Case Rep 2019 Sep 5;12(9) doi: 10.1136/bcr-2018-228917. PMID: 31492726Free PMC Article
Gardner S
Br J Nurs 2017 Nov 8;26(Sup20a):S16-S17. doi: 10.12968/bjon.2017.26.Sup20a.S16. PMID: 29144783
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J Dermatol 2007 Aug;34(8):516-22. doi: 10.1111/j.1346-8138.2007.00324.x. PMID: 17683381
Kose R, Coban YK, Ciralik H
Dermatol Online J 2006 Oct 31;12(6):18. PMID: 17083898

Prognosis

Yong WWD, Gungab AGNL, Tan Ze Lin G, Lee Boniao E, Zhang Ting T, Choi Ci-En E, Wong Soon Boon J, Sundar G
Orbit 2024 Oct;43(5):591-595. Epub 2023 Jun 8 doi: 10.1080/01676830.2023.2220116. PMID: 37288759
Joshy J, Mistry K, Levell NJ, van Bodegraven B, Vernon S, Rajan N, Craig P, Venables ZC
Clin Exp Dermatol 2022 Jun;47(6):1030-1035. Epub 2022 Mar 20 doi: 10.1111/ced.15126. PMID: 35149987
Goon PKC, Gurung P, Levell NJ, Subramanian P, Yong ASW, Lee KYC, Igali L, Greenberg D, Shah SN, Tan EKH
Acta Derm Venereol 2018 Nov 5;98(10):991-992. doi: 10.2340/00015555-3000. PMID: 29956715
Val-Bernal JF, Hermana S
Rom J Morphol Embryol 2017;58(4):1611-1616. PMID: 29556664
Rehal B, Merin MR, Barr K
Cutis 2013 Aug;92(2):67-70. PMID: 24087778

Clinical prediction guides

Kervarrec T, Westphal D, Pissaloux D, Legrand M, Tirode F, Neuhart A, Drouot F, Becker JC, Macagno N, Seris A, Jouary T, Beltzung F, Jullie ML, Harms PW, Cribier B, Mourah S, Jouenne F, Fromont G, Louveau B, Mancini M, Kazakov DV, de la Fouchardière A, Battistella M
Histopathology 2024 Oct;85(4):566-578. Epub 2024 May 24 doi: 10.1111/his.15214. PMID: 38785043
Kolm I, Konstantinova AM, Kutzner H, Barghorn A, Vanecek T, Mangana J, Kazakov DV
Am J Dermatopathol 2023 Aug 1;45(8):544-548. Epub 2023 Jun 15 doi: 10.1097/DAD.0000000000002465. PMID: 37335840
Val-Bernal JF, Hermana S
Rom J Morphol Embryol 2017;58(4):1611-1616. PMID: 29556664
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Akiyoshi E, Nogita T, Yamaguchi R, Toyoda H, Kawashima M, Hidano A
Dermatologica 1991;182(4):239-42. doi: 10.1159/000247804. PMID: 1653154

Recent systematic reviews

Bienstman T, Güvenç C, Garmyn M
Int J Mol Sci 2024 May 25;25(11) doi: 10.3390/ijms25115760. PMID: 38891945Free PMC Article
Fionda B, Di Stefani A, Lancellotta V, Gentileschi S, Caretto AA, Casà C, Federico F, Rembielak A, Rossi E, Morganti AG, Schinzari G, Peris K, Tagliaferri L
Eur Rev Med Pharmacol Sci 2022 Mar;26(5):1695-1700. doi: 10.26355/eurrev_202203_28238. PMID: 35302218
Rao EM, Knackstedt TJ
Int J Dermatol 2022 Jul;61(7):812-820. Epub 2021 Sep 8 doi: 10.1111/ijd.15893. PMID: 34494261
Nazemi A, Higgins S, Swift R, In G, Miller K, Wysong A
Dermatol Surg 2018 Oct;44(10):1247-1261. doi: 10.1097/DSS.0000000000001566. PMID: 29894433

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