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Idiopathic cardiomyopathy

MedGen UID:
18634
Concept ID:
C0033141
Disease or Syndrome
Synonyms: Cardiomyopathies, Primary; Cardiomyopathy, Primary; Disease, Primary Myocardial; Diseases, Primary Myocardial; Myocardial Disease, Primary; Myocardial Diseases, Primary; Primary Cardiomyopathies; Primary Cardiomyopathy; Primary Myocardial Disease; Primary Myocardial Diseases
SNOMED CT: Primary cardiomyopathy (89461002)
 
Monarch Initiative: MONDO:0005110

Definition

Disease of the heart muscle associated with electrical or mechanical dysfunction, in which the heart is the sole or predominantly involved organ. [from SNOMEDCT_US]

Term Hierarchy

Professional guidelines

PubMed

Wanert C, El Louali F, Al Dybiat S, Nguyen K, Zaffran S, Ovaert C
Arch Cardiovasc Dis 2023 Jun-Jul;116(6-7):309-315. Epub 2023 May 16 doi: 10.1016/j.acvd.2023.04.008. PMID: 37246080
Shen WK
Heart Rhythm 2021 Sep;18(9):1613-1614. doi: 10.1016/j.hrthm.2021.06.1198. PMID: 34474744
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article

Recent clinical studies

Etiology

Ciuca C, Ragni L, Hasan T, Balducci A, Angeli E, Prandstraller D, Egidy-Assenza G, Donti A, Bonvicini M, Gargiulo GD
Future Cardiol 2019 Mar;15(2):95-107. Epub 2019 Mar 8 doi: 10.2217/fca-2018-0030. PMID: 30848673
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Griez EJ, Mammar N, Loirat JC, Djega N, Trochut JN, Bouhour JB
J Psychosom Res 2000 Jun;48(6):585-7. doi: 10.1016/s0022-3999(00)00140-9. PMID: 11033378
Cannom DS
J Interv Card Electrophysiol 2000 Jan;4 Suppl 1:109-15. doi: 10.1023/a:1009842918121. PMID: 10590497

Diagnosis

Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Huhn GD, Gross C, Schnurr D, Preas C, Yagi S, Reagan S, Paddock C, Passaro D, Dworkin MS
Emerg Infect Dis 2005 Oct;11(10):1621-4. doi: 10.3201/eid1110.041152. PMID: 16318710Free PMC Article
Griez EJ, Mammar N, Loirat JC, Djega N, Trochut JN, Bouhour JB
J Psychosom Res 2000 Jun;48(6):585-7. doi: 10.1016/s0022-3999(00)00140-9. PMID: 11033378
Cannom DS
J Interv Card Electrophysiol 2000 Jan;4 Suppl 1:109-15. doi: 10.1023/a:1009842918121. PMID: 10590497
Tracy S, Wiegand V, McManus B, Gauntt C, Pallansch M, Beck M, Chapman N
J Am Coll Cardiol 1990 Jun;15(7):1688-94. doi: 10.1016/0735-1097(90)92846-t. PMID: 2161026

Therapy

Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
Petersen MG, Brinegar K, Oklu R
BMJ Case Rep 2015 Oct 29;2015 doi: 10.1136/bcr-2015-212555. PMID: 26516252Free PMC Article
Tracy S, Wiegand V, McManus B, Gauntt C, Pallansch M, Beck M, Chapman N
J Am Coll Cardiol 1990 Jun;15(7):1688-94. doi: 10.1016/0735-1097(90)92846-t. PMID: 2161026
Segal JP, Stapleton JF, McClellan JR, Waller BF, Harvey WP
Curr Probl Cardiol 1978 Sep;3(6):1-48. doi: 10.1016/0146-2806(78)90026-9. PMID: 568537

Prognosis

Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Cannom DS
J Interv Card Electrophysiol 2000 Jan;4 Suppl 1:109-15. doi: 10.1023/a:1009842918121. PMID: 10590497
Pierard LA, Hoffer EP
Am J Cardiol 1998 Jun 18;81(12A):111G-114G. doi: 10.1016/s0002-9149(98)00066-6. PMID: 9662240
Miller BR, Moseley HS, DaCosta LR, Sandison JW, Stuart KL
Pathol Microbiol (Basel) 1970;35(1):49-54. doi: 10.1159/000162199. PMID: 5472025

Clinical prediction guides

Turnbull D
Minerva Anestesiol 2021 Mar;87(3):334-340. Epub 2020 Dec 10 doi: 10.23736/S0375-9393.20.14703-5. PMID: 33300322
Ciuca C, Ragni L, Hasan T, Balducci A, Angeli E, Prandstraller D, Egidy-Assenza G, Donti A, Bonvicini M, Gargiulo GD
Future Cardiol 2019 Mar;15(2):95-107. Epub 2019 Mar 8 doi: 10.2217/fca-2018-0030. PMID: 30848673
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Pierard LA, Hoffer EP
Am J Cardiol 1998 Jun 18;81(12A):111G-114G. doi: 10.1016/s0002-9149(98)00066-6. PMID: 9662240

Recent systematic reviews

Batchelder K, Mayosi BM
S Afr Med J 2005 Mar;95(3):171-5. PMID: 15832667

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