Case Reports
doi: 10.1111/j.1442-2042.2005.01213.x.
Malignant retroperitoneal tumor arising in a multicystic dysplastic kidney of a girl with Schinzel-Giedion syndrome
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- PMID: 16409612
- DOI: 10.1111/j.1442-2042.2005.01213.x
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Case Reports
Malignant retroperitoneal tumor arising in a multicystic dysplastic kidney of a girl with Schinzel-Giedion syndrome
Int J Urol.
2005 Dec.
Abstract
We report the first case of malignant retroperitoneal tumor arising in a multicystic dysplastic kidney of an 8-year-old girl with Schinzel-Giedion syndrome. Although conservative treatment has been regarded as the standard management for asymptomatic multicystic dysplastic kidney, prophylactic surgical removal should be considered for selected children with potential risk of malignancy.
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