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Case Reports
. 1999 Jul;6(4):509-13.
doi: 10.1046/j.1468-1331.1999.640509.x.

Generalized freezing in Hallervorden-Spatz syndrome: case report

J Guimarães  1 , J V Santos
Affiliations
Case Reports

Generalized freezing in Hallervorden-Spatz syndrome: case report

J Guimarães et al. Eur J Neurol. 1999 Jul.

Abstract

We report the case of a female patient who was exhibiting slowly progressive, severe, generalized freezing of voluntary movement and disequilibrium. Brain magnetic resonance imaging showed a very low signal intensity in both pallidal nuclei, with a high signal intensity in the central portion, the so called 'eye-of-the-tiger' sign. Despite the unusual clinical features, we believe that this is a case of Hallervorden-Spatz syndrome, although without neuropathological examination we were unable to confirm the diagnosis with certainty. This case further demonstrates the complex role of the pallidum in voluntary movement.

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