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Moyamoya angiopathy

MedGen UID:
1842872
•Concept ID:
C5681261
•
Disease or Syndrome
Orphanet: ORPHA477768

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • Moyamoya angiopathy

Professional guidelines

PubMed

Evaluation and treatment of headache associated with moyamoya disease - a narrative review.
Chiang CC, Shahid AH, Harriott AM, Tietjen GE, Savastano LE, Klaas JP, Lanzino G
Cephalalgia 2022 May;42(6):542-552. Epub 2021 Nov 17 doi: 10.1177/03331024211056250. PMID: 34786968
Primary central nervous system vasculitis - An update on diagnosis, differential diagnosis and treatment.
Kraemer M, Berlit P
J Neurol Sci 2021 May 15;424:117422. Epub 2021 Mar 27 doi: 10.1016/j.jns.2021.117422. PMID: 33832773
Arterial ischemic stroke in non-neonate children: Diagnostic and therapeutic specificities.
Kossorotoff M, Chabrier S, Tran Dong K, Nguyen The Tich S, Dinomais M
Rev Neurol (Paris) 2020 Jan-Feb;176(1-2):20-29. Epub 2019 Jun 8 doi: 10.1016/j.neurol.2019.03.005. PMID: 31182310

Recent clinical studies

Etiology

European Stroke Organisation (ESO) Guidelines on Moyamoya angiopathy Endorsed by Vascular European Reference Network (VASCERN).
Bersano A, Khan N, Fuentes B, Acerbi F, Canavero I, Tournier-Lasserve E, Vajcoczy P, Zedde ML, Hussain S, Lémeret S, Kraemer M, Herve D
Eur Stroke J 2023 Mar;8(1):55-84. Epub 2023 Feb 2 doi: 10.1177/23969873221144089. PMID: 37021176Free PMC Article
Thalassemia and Moyamoya Syndrome: Epidemiology and long-term outcome.
Das S, Ray BK, Pandit A, Ghosh R, Chakraborty AP, Dubey S
Eur J Paediatr Neurol 2022 Nov;41:63-70. Epub 2022 Oct 17 doi: 10.1016/j.ejpn.2022.10.002. PMID: 36368232
Moyamoya disease: diagnosis and interventions.
Ihara M, Yamamoto Y, Hattori Y, Liu W, Kobayashi H, Ishiyama H, Yoshimoto T, Miyawaki S, Clausen T, Bang OY, Steinberg GK, Tournier-Lasserve E, Koizumi A
Lancet Neurol 2022 Aug;21(8):747-758. Epub 2022 May 20 doi: 10.1016/S1474-4422(22)00165-X. PMID: 35605621
Spicy foods triggering clinical symptoms in Moyamoya angiopathy.
Dubey S, Ghosh R, Chatterjee S, Dubey MJ, Ray BK, DAS S, Chatterjee A, Lahiri D, Kraemer M
J Neurosurg Sci 2021 Feb;65(1):85-88. Epub 2020 Jun 17 doi: 10.23736/S0390-5616.20.05030-4. PMID: 32550609
Heritable and non-heritable uncommon causes of stroke.
Bersano A, Kraemer M, Burlina A, Mancuso M, Finsterer J, Sacco S, Salvarani C, Caputi L, Chabriat H, Oberstein SL, Federico A, Lasserve ET, Hunt D, Dichgans M, Arnold M, Debette S, Markus HS
J Neurol 2021 Aug;268(8):2780-2807. Epub 2020 Apr 21 doi: 10.1007/s00415-020-09836-x. PMID: 32318851

Diagnosis

Cortical Blindness and Moyamoya Angiopathy in the Context of an Acute COVID-19 Infection.
Das S, Chakraborty AP, Dubey S, Ray BK
J Neuroophthalmol 2024 Mar 1;44(1):e172-e173. Epub 2022 Jun 8 doi: 10.1097/WNO.0000000000001633. PMID: 36166773
Moyamoya disease emerging as an immune-related angiopathy.
Asselman C, Hemelsoet D, Eggermont D, Dermaut B, Impens F
Trends Mol Med 2022 Nov;28(11):939-950. Epub 2022 Sep 14 doi: 10.1016/j.molmed.2022.08.009. PMID: 36115805
Moyamoya disease: diagnosis and interventions.
Ihara M, Yamamoto Y, Hattori Y, Liu W, Kobayashi H, Ishiyama H, Yoshimoto T, Miyawaki S, Clausen T, Bang OY, Steinberg GK, Tournier-Lasserve E, Koizumi A
Lancet Neurol 2022 Aug;21(8):747-758. Epub 2022 May 20 doi: 10.1016/S1474-4422(22)00165-X. PMID: 35605621
Primary central nervous system vasculitis - An update on diagnosis, differential diagnosis and treatment.
Kraemer M, Berlit P
J Neurol Sci 2021 May 15;424:117422. Epub 2021 Mar 27 doi: 10.1016/j.jns.2021.117422. PMID: 33832773
Heritable and non-heritable uncommon causes of stroke.
Bersano A, Kraemer M, Burlina A, Mancuso M, Finsterer J, Sacco S, Salvarani C, Caputi L, Chabriat H, Oberstein SL, Federico A, Lasserve ET, Hunt D, Dichgans M, Arnold M, Debette S, Markus HS
J Neurol 2021 Aug;268(8):2780-2807. Epub 2020 Apr 21 doi: 10.1007/s00415-020-09836-x. PMID: 32318851

Therapy

European Stroke Organisation (ESO) Guidelines on Moyamoya angiopathy Endorsed by Vascular European Reference Network (VASCERN).
Bersano A, Khan N, Fuentes B, Acerbi F, Canavero I, Tournier-Lasserve E, Vajcoczy P, Zedde ML, Hussain S, Lémeret S, Kraemer M, Herve D
Eur Stroke J 2023 Mar;8(1):55-84. Epub 2023 Feb 2 doi: 10.1177/23969873221144089. PMID: 37021176Free PMC Article
Microembolic signals and antiplatelet therapy in Moyamoya angiopathy.
Pompsch M, Veltkamp R, Diehl RR, Kraemer M
J Neurol 2022 Dec;269(12):6605-6612. Epub 2022 Aug 24 doi: 10.1007/s00415-022-11323-4. PMID: 36002693
Primary central nervous system vasculitis - An update on diagnosis, differential diagnosis and treatment.
Kraemer M, Berlit P
J Neurol Sci 2021 May 15;424:117422. Epub 2021 Mar 27 doi: 10.1016/j.jns.2021.117422. PMID: 33832773
Moyamoya angiopathy unmasking systemic lupus erythematosus.
Das S, Dubey S, Pandit A, Ray BK
BMJ Case Rep 2021 Jan 27;14(1) doi: 10.1136/bcr-2020-239307. PMID: 33504534Free PMC Article
Spicy foods triggering clinical symptoms in Moyamoya angiopathy.
Dubey S, Ghosh R, Chatterjee S, Dubey MJ, Ray BK, DAS S, Chatterjee A, Lahiri D, Kraemer M
J Neurosurg Sci 2021 Feb;65(1):85-88. Epub 2020 Jun 17 doi: 10.23736/S0390-5616.20.05030-4. PMID: 32550609

Prognosis

Angiopoietin-2 associates with poor prognosis in Moyamoya angiopathy.
Gorla G, Potenza A, Carrozzini T, Pollaci G, Acerbi F, Vetrano IG, Ferroli P, Canavero I, Rifino N, Bersano A, Gatti L
Ann Clin Transl Neurol 2024 Jun;11(6):1590-1603. Epub 2024 Apr 24 doi: 10.1002/acn3.52076. PMID: 38655722Free PMC Article
Thalassemia and Moyamoya Syndrome: Epidemiology and long-term outcome.
Das S, Ray BK, Pandit A, Ghosh R, Chakraborty AP, Dubey S
Eur J Paediatr Neurol 2022 Nov;41:63-70. Epub 2022 Oct 17 doi: 10.1016/j.ejpn.2022.10.002. PMID: 36368232
Neuroimaging in Moyamoya angiopathy: Updated review.
Filimonova E, Ovsiannikov K, Rzaev J
Clin Neurol Neurosurg 2022 Nov;222:107471. Epub 2022 Oct 15 doi: 10.1016/j.clineuro.2022.107471. PMID: 36265242
Limb-shaking TIA in Moyamoya angiopathy.
Das S, Ghosh R, Dubey S, Pandit A, Ray BK, Kraemer M
Clin Neurol Neurosurg 2021 Aug;207:106783. Epub 2021 Jun 27 doi: 10.1016/j.clineuro.2021.106783. PMID: 34225004
Moyamoya angiopathy - Is there a Western phenotype?
Hever P, Alamri A, Tolias C
Br J Neurosurg 2015;29(6):765-71. Epub 2015 Oct 16 doi: 10.3109/02688697.2015.1096902. PMID: 26473792

Clinical prediction guides

The genetic landscape and clinical implication of pediatric Moyamoya angiopathy in an international cohort.
Zanoni P, Steindl K, Sticht H, Oneda B, Joset P, Ivanovski I, Horn AHC, Cabello EM, Laube J, Zweier M, Baumer A, Rauch A, Khan N
Eur J Hum Genet 2023 Jul;31(7):784-792. Epub 2023 Apr 4 doi: 10.1038/s41431-023-01320-0. PMID: 37012328Free PMC Article
Thalassemia and Moyamoya Syndrome: Epidemiology and long-term outcome.
Das S, Ray BK, Pandit A, Ghosh R, Chakraborty AP, Dubey S
Eur J Paediatr Neurol 2022 Nov;41:63-70. Epub 2022 Oct 17 doi: 10.1016/j.ejpn.2022.10.002. PMID: 36368232
Neuroimaging in Moyamoya angiopathy: Updated review.
Filimonova E, Ovsiannikov K, Rzaev J
Clin Neurol Neurosurg 2022 Nov;222:107471. Epub 2022 Oct 15 doi: 10.1016/j.clineuro.2022.107471. PMID: 36265242
Limb-shaking TIA in Moyamoya angiopathy.
Das S, Ghosh R, Dubey S, Pandit A, Ray BK, Kraemer M
Clin Neurol Neurosurg 2021 Aug;207:106783. Epub 2021 Jun 27 doi: 10.1016/j.clineuro.2021.106783. PMID: 34225004
Primary central nervous system vasculitis - An update on diagnosis, differential diagnosis and treatment.
Kraemer M, Berlit P
J Neurol Sci 2021 May 15;424:117422. Epub 2021 Mar 27 doi: 10.1016/j.jns.2021.117422. PMID: 33832773

Recent systematic reviews

The mechanobiological theory: a unifying hypothesis on the pathogenesis of moyamoya disease based on a systematic review.
Sudhir BJ, Keelara AG, Venkat EH, Kazumata K, Sundararaman A
Neurosurg Focus 2021 Sep;51(3):E6. doi: 10.3171/2021.6.FOCUS21281. PMID: 34469862

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