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MICROPHTHALMIA, SYNDROMIC 15(MCOPS15)

MedGen UID:
1674836
Concept ID:
C5193017
Disease or Syndrome
Synonym: MCOPS15
 
OMIM®: 610083; 615145

Professional guidelines

PubMed

Russo M, Palmeri S, Zucconi A, Vagge A, Arioni C
Ital J Pediatr 2025 Mar 5;51(1):65. doi: 10.1186/s13052-025-01882-3. PMID: 40038803Free PMC Article
Das D, Modaboyina S, Raj S, Agrawal S, Bajaj MS
Indian J Ophthalmol 2022 Jul;70(7):2559-2563. doi: 10.4103/ijo.IJO_2627_21. PMID: 35791156Free PMC Article
Taha Najim R, Topa A, Jugård Y, Casslén B, Odersjö M, Andersson Grönlund M
Acta Ophthalmol 2020 Dec;98(8):848-858. Epub 2020 May 21 doi: 10.1111/aos.14427. PMID: 32436650

Recent clinical studies

Etiology

Das D, Modaboyina S, Raj S, Agrawal S, Bajaj MS
Indian J Ophthalmol 2022 Jul;70(7):2559-2563. doi: 10.4103/ijo.IJO_2627_21. PMID: 35791156Free PMC Article
Smith PS, West H, Whitworth J, Castle B, Sansbury FH, Warren AY, Woodward ER, Tischkowitz M, Maher ER
Genes Chromosomes Cancer 2021 Jan;60(1):5-16. Epub 2020 Sep 19 doi: 10.1002/gcc.22893. PMID: 32830346
Toussi A, Mans N, Welborn J, Kiuru M
J Cutan Pathol 2020 Jul;47(7):606-616. Epub 2020 May 11 doi: 10.1111/cup.13689. PMID: 32249949Free PMC Article
Iordanidou V, De Potter P
Am J Ophthalmol 2004 Sep;138(3):425-9. doi: 10.1016/j.ajo.2004.04.062. PMID: 15364225
Read AP, Newton VE
J Med Genet 1997 Aug;34(8):656-65. doi: 10.1136/jmg.34.8.656. PMID: 9279758Free PMC Article

Diagnosis

Smith PS, West H, Whitworth J, Castle B, Sansbury FH, Warren AY, Woodward ER, Tischkowitz M, Maher ER
Genes Chromosomes Cancer 2021 Jan;60(1):5-16. Epub 2020 Sep 19 doi: 10.1002/gcc.22893. PMID: 32830346
Jankauskienė A, Koczkowska M, Bjerre A, Bernaciak J, Schaefer F, Lipska-Ziętkiewicz BS
BMC Nephrol 2016 Mar 21;17:32. doi: 10.1186/s12882-016-0246-2. PMID: 27000031Free PMC Article
Davoody A, Chen IP, Nanda R, Uribe F, Reichenberger EJ
Cleft Palate Craniofac J 2012 Sep;49(5):e55-60. Epub 2011 Jul 8 doi: 10.1597/10-256. PMID: 21740180Free PMC Article
Iordanidou V, De Potter P
Am J Ophthalmol 2004 Sep;138(3):425-9. doi: 10.1016/j.ajo.2004.04.062. PMID: 15364225
Warburg M
Birth Defects Orig Artic Ser 1971 Mar;7(3):117-24. PMID: 5006136

Therapy

Reece AS, Hulse GK
BMC Pharmacol Toxicol 2020 Nov 12;21(1):75. doi: 10.1186/s40360-020-00450-1. PMID: 33183341Free PMC Article
Tocharoenchok T, Sriyoschati S, Tongcharoen P, Tantiwongkosri K, Subtaweesin T
Asian Cardiovasc Thorac Ann 2016 Jun;24(5):428-34. Epub 2016 Apr 19 doi: 10.1177/0218492316645749. PMID: 27095702
Crider KS, Cleves MA, Reefhuis J, Berry RJ, Hobbs CA, Hu DJ
Arch Pediatr Adolesc Med 2009 Nov;163(11):978-85. doi: 10.1001/archpediatrics.2009.188. PMID: 19884587
Müllner-Eidenböck A, Amon M, Moser E, Klebermass N
Ophthalmology 2004 May;111(5):906-13. doi: 10.1016/j.ophtha.2003.07.019. PMID: 15121367
Lesnoni G, Rossi T, Nistri A, Boccassini B
Eur J Ophthalmol 1999 Oct-Dec;9(4):315-8. doi: 10.1177/112067219900900411. PMID: 10651198

Prognosis

Marakhonov AV, Voskresenskaya AA, Ballesta MJ, Konovalov FA, Vasilyeva TA, Blanco-Kelly F, Pozdeyeva NA, Kadyshev VV, López-González V, Guillen E, Ayuso C, Zinchenko RA, Corton M
Orphanet J Rare Dis 2020 Aug 13;15(1):207. doi: 10.1186/s13023-020-01484-8. PMID: 32791987Free PMC Article
Taha Najim R, Topa A, Jugård Y, Casslén B, Odersjö M, Andersson Grönlund M
Acta Ophthalmol 2020 Dec;98(8):848-858. Epub 2020 May 21 doi: 10.1111/aos.14427. PMID: 32436650
Brenner L, Burke K, Leduc CA, Guha S, Guo J, Chung WK
Genet Test Mol Biomarkers 2011 Jul-Aug;15(7-8):525-9. Epub 2011 Mar 27 doi: 10.1089/gtmb.2010.0277. PMID: 21438779
Schneider A, Bardakjian TM, Zhou J, Hughes N, Keep R, Dorsainville D, Kherani F, Katowitz J, Schimmenti LA, Hummel M, Fitzpatrick DR, Young TL
Am J Med Genet A 2008 Nov 1;146A(21):2794-8. doi: 10.1002/ajmg.a.32384. PMID: 18831064Free PMC Article
Read AP, Newton VE
J Med Genet 1997 Aug;34(8):656-65. doi: 10.1136/jmg.34.8.656. PMID: 9279758Free PMC Article

Clinical prediction guides

Mai CT, Isenburg JL, Canfield MA, Meyer RE, Correa A, Alverson CJ, Lupo PJ, Riehle-Colarusso T, Cho SJ, Aggarwal D, Kirby RS; National Birth Defects Prevention Network
Birth Defects Res 2019 Nov 1;111(18):1420-1435. Epub 2019 Oct 3 doi: 10.1002/bdr2.1589. PMID: 31580536Free PMC Article
García-Rabasco A, De-Unamuno B, Martínez F, Febrer-Bosch I, Alegre-de-Miquel V
Pediatr Dermatol 2013 Nov-Dec;30(6):e230-1. Epub 2012 May 21 doi: 10.1111/j.1525-1470.2012.01735.x. PMID: 22612277
Brenner L, Burke K, Leduc CA, Guha S, Guo J, Chung WK
Genet Test Mol Biomarkers 2011 Jul-Aug;15(7-8):525-9. Epub 2011 Mar 27 doi: 10.1089/gtmb.2010.0277. PMID: 21438779
Schneider A, Bardakjian TM, Zhou J, Hughes N, Keep R, Dorsainville D, Kherani F, Katowitz J, Schimmenti LA, Hummel M, Fitzpatrick DR, Young TL
Am J Med Genet A 2008 Nov 1;146A(21):2794-8. doi: 10.1002/ajmg.a.32384. PMID: 18831064Free PMC Article
Read AP, Newton VE
J Med Genet 1997 Aug;34(8):656-65. doi: 10.1136/jmg.34.8.656. PMID: 9279758Free PMC Article

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