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Joubert syndrome 29(JBTS29)

MedGen UID:
1625238
Concept ID:
C4539715
Disease or Syndrome
Synonyms: JBTS29; JOUBERT SYNDROME 29
 
Monarch Initiative: MONDO:0800372
OMIM®: 616183; 617562

Professional guidelines

PubMed

Juan Z, Cuixia G, Yuanjie C, Yan L, Ling Y, Tiejuan Z, Li W, Jijing H, Guohui Z, Yousheng Y, Qingqing W, Lijuan S
Eur J Med Res 2024 Jul 31;29(1):397. doi: 10.1186/s40001-024-01993-3. PMID: 39085968Free PMC Article

Recent clinical studies

Etiology

Juan Z, Cuixia G, Yuanjie C, Yan L, Ling Y, Tiejuan Z, Li W, Jijing H, Guohui Z, Yousheng Y, Qingqing W, Lijuan S
Eur J Med Res 2024 Jul 31;29(1):397. doi: 10.1186/s40001-024-01993-3. PMID: 39085968Free PMC Article
Ying L, Hui W, FuQian, Nan Z, Yeping J, Lan M
BMC Pediatr 2022 Jul 20;22(1):433. doi: 10.1186/s12887-022-03496-8. PMID: 35858853Free PMC Article
Kagan KO, Dufke A, Gembruch U
Curr Opin Obstet Gynecol 2017 Apr;29(2):85-94. doi: 10.1097/GCO.0000000000000348. PMID: 28151755
Salman MS, Masood S, Azad M, Chodirker BN
Can J Neurol Sci 2014 Jan;41(1):29-36. doi: 10.1017/s031716710001622x. PMID: 24384334
Saraiva JM, Baraitser M
Am J Med Genet 1992 Jul 1;43(4):726-31. doi: 10.1002/ajmg.1320430415. PMID: 1341417

Diagnosis

Crawford D, Dearmun A
Nurs Child Young People 2017 Jun 12;29(5):15. doi: 10.7748/ncyp.29.5.15.s19. PMID: 28604212
Kagan KO, Dufke A, Gembruch U
Curr Opin Obstet Gynecol 2017 Apr;29(2):85-94. doi: 10.1097/GCO.0000000000000348. PMID: 28151755
Bulgheroni S, D'Arrigo S, Signorini S, Briguglio M, Di Sabato ML, Casarano M, Mancini F, Romani M, Alfieri P, Battini R, Zoppello M, Tortorella G, Bertini E, Leuzzi V, Valente EM, Riva D
Am J Med Genet A 2016 Dec;170(12):3115-3124. Epub 2016 Aug 17 doi: 10.1002/ajmg.a.37938. PMID: 27530364
Bader I, Decker E, Mayr JA, Lunzer V, Koch J, Boltshauser E, Sperl W, Pietsch P, Ertl-Wagner B, Bolz H, Bergmann C, Rittinger O
Eur J Med Genet 2016 Aug;59(8):386-91. Epub 2016 Jul 1 doi: 10.1016/j.ejmg.2016.06.007. PMID: 27377014
Saraiva JM, Baraitser M
Am J Med Genet 1992 Jul 1;43(4):726-31. doi: 10.1002/ajmg.1320430415. PMID: 1341417

Therapy

Saleem SN, Zaki MS
AJNR Am J Neuroradiol 2010 Mar;31(3):424-9. Epub 2009 Nov 26 doi: 10.3174/ajnr.A1867. PMID: 19942698Free PMC Article

Prognosis

Chen C, Gao J, Lv Q, Xu C, Xia Y, Du A
BMC Med Genomics 2021 Oct 9;14(1):242. doi: 10.1186/s12920-021-01089-5. PMID: 34627237Free PMC Article
Nuovo S, Fuiano L, Micalizzi A, Battini R, Bertini E, Borgatti R, Caridi G, D'Arrigo S, Fazzi E, Fischetto R, Ghiggeri GM, Giordano L, Leuzzi V, Romaniello R, Signorini S, Stringini G, Zanni G, Romani M, Valente EM, Emma F
Nephrol Dial Transplant 2020 Jul 1;35(7):1195-1202. doi: 10.1093/ndt/gfy333. PMID: 30403813Free PMC Article
Soliman NA, Hildebrandt F, Otto EA, Nabhan MM, Allen SJ, Badr AM, Sheba M, Fadda S, Gawdat G, El-Kiky H
Saudi J Kidney Dis Transpl 2012 Sep;23(5):1090-8. doi: 10.4103/1319-2442.100968. PMID: 22982934Free PMC Article
Hakami WS, Majeed-Saidan MA
Saudi Med J 2011 Nov;32(11):1137-42. PMID: 22057601
Saraiva JM, Baraitser M
Am J Med Genet 1992 Jul 1;43(4):726-31. doi: 10.1002/ajmg.1320430415. PMID: 1341417

Clinical prediction guides

Chen C, Gao J, Lv Q, Xu C, Xia Y, Du A
BMC Med Genomics 2021 Oct 9;14(1):242. doi: 10.1186/s12920-021-01089-5. PMID: 34627237Free PMC Article
Nuovo S, Fuiano L, Micalizzi A, Battini R, Bertini E, Borgatti R, Caridi G, D'Arrigo S, Fazzi E, Fischetto R, Ghiggeri GM, Giordano L, Leuzzi V, Romaniello R, Signorini S, Stringini G, Zanni G, Romani M, Valente EM, Emma F
Nephrol Dial Transplant 2020 Jul 1;35(7):1195-1202. doi: 10.1093/ndt/gfy333. PMID: 30403813Free PMC Article
Dehghani M, Mojarad M, Ghayoor Karimiani E, Vahidi Mehrjardi MY, Sahebalzamani A, Ashrafzadeh F, Beiraghi Toosi M, Eslahi A, Ahangari N, Yassini SM, Hassanbeigi A, Rasti A, Kalantar SM, Maroofian R
Public Health Genomics 2017;20(3):188-193. Epub 2017 Jul 19 doi: 10.1159/000477560. PMID: 28719906
Soliman NA, Hildebrandt F, Otto EA, Nabhan MM, Allen SJ, Badr AM, Sheba M, Fadda S, Gawdat G, El-Kiky H
Saudi J Kidney Dis Transpl 2012 Sep;23(5):1090-8. doi: 10.4103/1319-2442.100968. PMID: 22982934Free PMC Article

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