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Severe hearing impairment

MedGen UID:
846511
Concept ID:
C3874334
Finding
Synonym: Severe hearing loss
SNOMED CT: Severe hearing loss (3561000119106)
 
HPO: HP:0012714

Definition

A severe form of hearing impairment. [from HPO]

Term Hierarchy

Professional guidelines

PubMed

Saki N, Bayat A, Hoseinabadi R, Nikakhlagh S, Karimi M, Dashti R
Int J Pediatr Otorhinolaryngol 2017 Jun;97:89-92. Epub 2017 Mar 31 doi: 10.1016/j.ijporl.2017.03.038. PMID: 28483258
Braun T, Hempel JM, Berghaus A
Dtsch Arztebl Int 2014 Feb 7;111(6):92-8. doi: 10.3238/arztebl.2014.0092. PMID: 24622605Free PMC Article
Oudesluys-Murphy AM, van Straaten HL, Bholasingh R, van Zanten GA
Eur J Pediatr 1996 Jun;155(6):429-35. doi: 10.1007/BF01955176. PMID: 8789756

Recent clinical studies

Etiology

Wu F, Zhou C
Am J Alzheimers Dis Other Demen 2024 Jan-Dec;39:15333175241227318. doi: 10.1177/15333175241227318. PMID: 38198589Free PMC Article
Shen X, Yu H, Chen K, Xue Q, Lu J, Xie Z
J Clin Anesth 2023 Dec;91:111254. Epub 2023 Sep 8 doi: 10.1016/j.jclinane.2023.111254. PMID: 37689025
Foster JI, Williams KL, Timmer BHB, Brauer SG
Trends Hear 2022 Jan-Dec;26:23312165221144155. doi: 10.1177/23312165221144155. PMID: 36524292Free PMC Article
Kim SY, Kim HJ, Park EK, Joe J, Sim S, Choi HG
PLoS One 2017;12(6):e0179973. Epub 2017 Jun 22 doi: 10.1371/journal.pone.0179973. PMID: 28640916Free PMC Article
Oudesluys-Murphy AM, van Straaten HL, Bholasingh R, van Zanten GA
Eur J Pediatr 1996 Jun;155(6):429-35. doi: 10.1007/BF01955176. PMID: 8789756

Diagnosis

Foster JI, Williams KL, Timmer BHB, Brauer SG
Trends Hear 2022 Jan-Dec;26:23312165221144155. doi: 10.1177/23312165221144155. PMID: 36524292Free PMC Article
Kim SY, Lee CH, Min C, Yoo DM, Choi HG
Curr Issues Mol Biol 2021 May 18;43(1):142-152. doi: 10.3390/cimb43010012. PMID: 34070082Free PMC Article
Keats BJ, Corey DP
Am J Med Genet 1999 Sep 24;89(3):158-66. PMID: 10704190
Oudesluys-Murphy AM, van Straaten HL, Bholasingh R, van Zanten GA
Eur J Pediatr 1996 Jun;155(6):429-35. doi: 10.1007/BF01955176. PMID: 8789756
Jones MC
Clin Pediatr (Phila) 1970 Jun;9(6):338-41. doi: 10.1177/000992287000900610. PMID: 5419443

Therapy

Jiang F, Dong Q, Wu S, Liu X, Dayimu A, Liu Y, Ji H, Wang L, Liu T, Li N, Li X, Fu P, Jing Q, Zhou C, Li H, Xu L, Chen S, Wang H
BMC Med 2024 Nov 7;22(1):518. doi: 10.1186/s12916-024-03748-7. PMID: 39506811Free PMC Article
Kim SY, Lee CH, Min C, Yoo DM, Choi HG
Curr Issues Mol Biol 2021 May 18;43(1):142-152. doi: 10.3390/cimb43010012. PMID: 34070082Free PMC Article
Solheim J, Hickson L
Int J Audiol 2017 Jul;56(7):472-479. Epub 2017 Mar 23 doi: 10.1080/14992027.2017.1303201. PMID: 28332420
NIH Consens Statement 1995 May 15-17;13(2):1-30. PMID: 8595436
Ito J, Takagi A, Kawano M, Honjo I
Acta Otolaryngol 1995 Jul;115(4):493-6. doi: 10.3109/00016489509139354. PMID: 7572123

Prognosis

Banks R, Greene BR, Morrow I, Ciesla M, Woolever D, Tobyne S, Gomes-Osman J, Jannati A, Showalter J, Bates D, Pascual-Leone A
Sci Rep 2024 Sep 10;14(1):21157. doi: 10.1038/s41598-024-67539-z. PMID: 39256446Free PMC Article
Shen X, Yu H, Chen K, Xue Q, Lu J, Xie Z
J Clin Anesth 2023 Dec;91:111254. Epub 2023 Sep 8 doi: 10.1016/j.jclinane.2023.111254. PMID: 37689025
Kim SY, Lim JS, Kong IG, Choi HG
Sci Rep 2018 Oct 15;8(1):15266. doi: 10.1038/s41598-018-33325-x. PMID: 30323320Free PMC Article
Kemperman MH, Koch SM, Kumar S, Huygen PL, Joosten FB, Cremers CW
Int J Audiol 2004 Oct;43(9):523-32. doi: 10.1080/14992020400050067. PMID: 15726843
Oudesluys-Murphy AM, van Straaten HL, Bholasingh R, van Zanten GA
Eur J Pediatr 1996 Jun;155(6):429-35. doi: 10.1007/BF01955176. PMID: 8789756

Clinical prediction guides

Shen X, Yu H, Chen K, Xue Q, Lu J, Xie Z
J Clin Anesth 2023 Dec;91:111254. Epub 2023 Sep 8 doi: 10.1016/j.jclinane.2023.111254. PMID: 37689025
Foster JI, Williams KL, Timmer BHB, Brauer SG
Trends Hear 2022 Jan-Dec;26:23312165221144155. doi: 10.1177/23312165221144155. PMID: 36524292Free PMC Article
de Kleijn JL, van Kalmthout LWM, van der Vossen MJB, Vonck BMD, Topsakal V, Bruijnzeel H
JAMA Otolaryngol Head Neck Surg 2018 Jul 1;144(7):630-638. doi: 10.1001/jamaoto.2018.0652. PMID: 29800000
Dufresne D, Dagenais L, Shevell MI; REPACQ Consortium
Pediatr Neurol 2014 Nov;51(5):641-4. Epub 2014 Jul 19 doi: 10.1016/j.pediatrneurol.2014.07.005. PMID: 25194720
Eisenberg LS
Ear Hear 2007 Dec;28(6):766-72. doi: 10.1097/AUD.0b013e318157f01f. PMID: 17982364

Recent systematic reviews

Foster JI, Williams KL, Timmer BHB, Brauer SG
Trends Hear 2022 Jan-Dec;26:23312165221144155. doi: 10.1177/23312165221144155. PMID: 36524292Free PMC Article
de Kleijn JL, van Kalmthout LWM, van der Vossen MJB, Vonck BMD, Topsakal V, Bruijnzeel H
JAMA Otolaryngol Head Neck Surg 2018 Jul 1;144(7):630-638. doi: 10.1001/jamaoto.2018.0652. PMID: 29800000

Supplemental Content

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    Clinical resources

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