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Pulmonary valve stenosis

MedGen UID:
18768
Concept ID:
C0034089
Disease or Syndrome
Synonyms: Pulmonary Valve Stenoses; Pulmonary Valve Stenosis; Pulmonic Stenoses, Valvular; Pulmonic Stenosis, Valvular; Stenoses, Pulmonary Valve; Stenosis, Pulmonary Valve; Valvular Pulmonic Stenoses; Valvular Pulmonic Stenosis
SNOMED CT: PVS - Pulmonary valve stenosis (56786000); PS - Pulmonary valve stenosis (56786000); Pulmonic valve stenosis (56786000); Pulmonary valve stenosis (56786000)
 
Monarch Initiative: MONDO:0006936

Definition

The pathologic narrowing of the orifice of the pulmonary valve. This lesion restricts blood outflow from the right ventricle to the pulmonary artery. When the trileaflet valve is fused into an imperforate membrane, the blockage is complete. [from MONDO]

Professional guidelines

PubMed

Marchini F, Meossi S, Passarini G, Campo G, Pavasini R
Vasc Health Risk Manag 2023;19:379-390. Epub 2023 Jun 30 doi: 10.2147/VHRM.S380240. PMID: 37416511Free PMC Article
Linglart L, Gelb BD
Am J Med Genet C Semin Med Genet 2020 Mar;184(1):73-80. Epub 2020 Feb 5 doi: 10.1002/ajmg.c.31765. PMID: 32022400Free PMC Article
Ruckdeschel E, Kim YY
Heart 2019 Mar;105(5):414-422. Epub 2018 Oct 18 doi: 10.1136/heartjnl-2017-312743. PMID: 30337335

Curated

UK NICE Guideline NG208, Heart valve disease presenting in adults: investigation and management, 2021

Recent clinical studies

Etiology

Wei X, Zhao ZG, Zhong XM, Feng Y
Eur Heart J Cardiovasc Imaging 2022 Nov 17;23(12):e545. doi: 10.1093/ehjci/jeac187. PMID: 36093625
Hatt D, Syngal P, White M, Warrier R
Clin Pediatr (Phila) 2018 Jun;57(7):871-873. Epub 2017 Oct 25 doi: 10.1177/0009922817737085. PMID: 29067824
Swamy P, Bharadwaj A, Varadarajan P, Pai RG
Echocardiography 2015 Jan;32 Suppl 2:S148-56. Epub 2014 May 29 doi: 10.1111/echo.12437. PMID: 24888422
Odenwald T, Taylor AM
Expert Rev Cardiovasc Ther 2011 Nov;9(11):1445-57. doi: 10.1586/erc.11.150. PMID: 22059793
Baumgartner H, Hung J, Bermejo J, Chambers JB, Evangelista A, Griffin BP, Iung B, Otto CM, Pellikka PA, Quiñones M; EAE/ASE
Eur J Echocardiogr 2009 Jan;10(1):1-25. Epub 2008 Dec 8 doi: 10.1093/ejechocard/jen303. PMID: 19065003

Diagnosis

Kovacs S, Scansen BA, Stern JA
Vet Clin North Am Small Anim Pract 2023 Nov;53(6):1379-1391. Epub 2023 Jul 7 doi: 10.1016/j.cvsm.2023.05.014. PMID: 37423844
Marchini F, Meossi S, Passarini G, Campo G, Pavasini R
Vasc Health Risk Manag 2023;19:379-390. Epub 2023 Jun 30 doi: 10.2147/VHRM.S380240. PMID: 37416511Free PMC Article
Katekaru-Tokeshi DI, Jiménez-Santos M
Rev Esp Cardiol (Engl Ed) 2021 Jul;74(7):624. Epub 2021 Jan 14 doi: 10.1016/j.rec.2020.10.017. PMID: 33454243
Ruckdeschel E, Kim YY
Heart 2019 Mar;105(5):414-422. Epub 2018 Oct 18 doi: 10.1136/heartjnl-2017-312743. PMID: 30337335
Massoure PL, Latremouille C, Lamblin G, Leca F
Cardiovasc J Afr 2012 Jul 12;23(6):e19-20. doi: 10.5830/CVJA-2012-011. PMID: 22832481

Therapy

Kwiatkowski DM, Hanley FL, Krawczeski CD
Pediatr Crit Care Med 2016 Aug;17(8 Suppl 1):S323-9. doi: 10.1097/PCC.0000000000000818. PMID: 27490618
Chung R, Taylor AM
Circ Cardiovasc Imaging 2014 Jan;7(1):182-9. doi: 10.1161/CIRCIMAGING.113.000826. PMID: 24449547
Hill G
Congenit Heart Dis 2013 Mar-Apr;8(2):174-7. Epub 2013 Mar 1 doi: 10.1111/chd.12042. PMID: 23448360
Baumgartner H, Hung J, Bermejo J, Chambers JB, Evangelista A, Griffin BP, Iung B, Otto CM, Pellikka PA, Quiñones M; EAE/ASE
Eur J Echocardiogr 2009 Jan;10(1):1-25. Epub 2008 Dec 8 doi: 10.1093/ejechocard/jen303. PMID: 19065003
Block PC, Bonhoeffer P
Curr Cardiol Rep 2005 Mar;7(2):108-13. doi: 10.1007/s11886-005-0022-6. PMID: 15717957

Prognosis

Rao PS
Indian J Pediatr 2024 Jan;91(1):1-2. Epub 2023 Oct 9 doi: 10.1007/s12098-023-04874-5. PMID: 37806996
Wei X, Zhao ZG, Zhong XM, Feng Y
Eur Heart J Cardiovasc Imaging 2022 Nov 17;23(12):e545. doi: 10.1093/ehjci/jeac187. PMID: 36093625
Cuypers JA, Witsenburg M, van der Linde D, Roos-Hesselink JW
Heart 2013 Mar;99(5):339-47. Epub 2013 Jan 8 doi: 10.1136/heartjnl-2012-301964. PMID: 23303481
Block PC, Bonhoeffer P
Curr Cardiol Rep 2005 Mar;7(2):108-13. doi: 10.1007/s11886-005-0022-6. PMID: 15717957
Latson LA
J Interv Cardiol 2001 Jun;14(3):345-50. doi: 10.1111/j.1540-8183.2001.tb00343.x. PMID: 12053395

Clinical prediction guides

Chung R, Taylor AM
Circ Cardiovasc Imaging 2014 Jan;7(1):182-9. doi: 10.1161/CIRCIMAGING.113.000826. PMID: 24449547
Hill G
Congenit Heart Dis 2013 Mar-Apr;8(2):174-7. Epub 2013 Mar 1 doi: 10.1111/chd.12042. PMID: 23448360
Massoure PL, Latremouille C, Lamblin G, Leca F
Cardiovasc J Afr 2012 Jul 12;23(6):e19-20. doi: 10.5830/CVJA-2012-011. PMID: 22832481
Lepri F, De Luca A, Stella L, Rossi C, Baldassarre G, Pantaleoni F, Cordeddu V, Williams BJ, Dentici ML, Caputo V, Venanzi S, Bonaguro M, Kavamura I, Faienza MF, Pilotta A, Stanzial F, Faravelli F, Gabrielli O, Marino B, Neri G, Silengo MC, Ferrero GB, Torrrente I, Selicorni A, Mazzanti L, Digilio MC, Zampino G, Dallapiccola B, Gelb BD, Tartaglia M
Hum Mutat 2011 Jul;32(7):760-72. Epub 2011 Apr 28 doi: 10.1002/humu.21492. PMID: 21387466Free PMC Article
Arnold JR, Ghahramani AR, Hernandez FA, Sommer LS
Chest 1971 Sep;60(3):229-32. doi: 10.1378/chest.60.3.229. PMID: 5093254

Recent systematic reviews

Salmeri N, Seidenari A, Cavoretto PI, Papale M, Candiani M, Farina A
Ultrasound Obstet Gynecol 2024 Sep;64(3):294-307. doi: 10.1002/uog.27659. PMID: 38629488
Rao PS
Indian Heart J 2024 Mar-Apr;76(2):86-93. Epub 2023 Dec 24 doi: 10.1016/j.ihj.2023.12.007. PMID: 38147974Free PMC Article
Diniz AMB, Manso PH, Santos MV, Rodrigues AJ, Sbragia L
Braz J Cardiovasc Surg 2023 May 4;38(3):398-404. doi: 10.21470/1678-9741-2022-0273. PMID: 36592074Free PMC Article
Ravindra K, Chanana N, Mor S
Sci Total Environ 2021 Apr 15;765:142772. Epub 2020 Oct 7 doi: 10.1016/j.scitotenv.2020.142772. PMID: 33183823
Cai GJ, Sun XX, Zhang L, Hong Q
Am J Obstet Gynecol 2014 Aug;211(2):91-117. Epub 2014 Mar 14 doi: 10.1016/j.ajog.2014.03.028. PMID: 24631708

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
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    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Curated

    • NICE, 2021
      UK NICE Guideline NG208, Heart valve disease presenting in adults: investigation and management, 2021

    Consumer resources

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