U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Multiple epiphyseal dysplasia and pseudoachondroplasia

MedGen UID:
1842169
Concept ID:
C5681609
Disease or Syndrome
Orphanet: ORPHA93429

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMultiple epiphyseal dysplasia and pseudoachondroplasia

Professional guidelines

Recent clinical studies

Etiology

El-Lababidi N, Zikánová M, Baxová A, Nosková L, Leiská A, Lambert L, Honzík T, Zeman J
Prague Med Rep 2020;121(3):153-162. doi: 10.14712/23362936.2020.14. PMID: 33030144
Muensterer OJ, Berdon WE, Lachman RS, Done SL
Pediatr Radiol 2012 Apr;42(4):475-80. Epub 2012 Mar 18 doi: 10.1007/s00247-012-2364-8. PMID: 22426567
Kennedy J, Jackson G, Ramsden S, Taylor J, Newman W, Wright MJ, Donnai D, Elles R, Briggs MD
Eur J Hum Genet 2005 May;13(5):547-55. doi: 10.1038/sj.ejhg.5201374. PMID: 15756302Free PMC Article
McKeand J, Rotta J, Hecht JT
Am J Med Genet 1996 May 17;63(2):406-10. doi: 10.1002/(SICI)1096-8628(19960517)63:2<406::AID-AJMG16>3.0.CO;2-O. PMID: 8725795
Horton WA, Hall JG, Scott CI, Pyeritz RE, Rimoin DL
Am J Dis Child 1982 Apr;136(4):316-9. doi: 10.1001/archpedi.1982.03970400034010. PMID: 6803579

Diagnosis

Matsumoto H, Hori T, Mori M, Sasai H, Ohnishi H
Pediatr Int 2024 Jan-Dec;66(1):e15799. doi: 10.1111/ped.15799. PMID: 39087399
Kennedy J, Jackson G, Ramsden S, Taylor J, Newman W, Wright MJ, Donnai D, Elles R, Briggs MD
Eur J Hum Genet 2005 May;13(5):547-55. doi: 10.1038/sj.ejhg.5201374. PMID: 15756302Free PMC Article
Briggs MD, Chapman KL
Hum Mutat 2002 May;19(5):465-78. doi: 10.1002/humu.10066. PMID: 11968079
Unger S, Hecht JT
Am J Med Genet 2001 Winter;106(4):244-50. PMID: 11891674
Khungar A, Mahajan P, Gupte G, Vasundhara M, Kher A, Bharucha BA
J Postgrad Med 1993 Apr-Jun;39(2):91-3. PMID: 8169872

Therapy

Guo BB, Jin JY, Yuan ZZ, Zeng L, Xiang R
Biomed Res Int 2021;2021:6678531. Epub 2021 Mar 8 doi: 10.1155/2021/6678531. PMID: 33748277Free PMC Article
Raggio CL, Yonko EA, Khan SI, Carter EM, Citron KP, Bostrom MPG, Figgie MP
J Arthroplasty 2020 Aug;35(8):1993-2001. Epub 2020 Apr 9 doi: 10.1016/j.arth.2020.04.007. PMID: 32386881
Pesenti S, Iobst CA, Launay F
Orthop Traumatol Surg Res 2017 Sep;103(5):761-764. Epub 2017 Apr 17 doi: 10.1016/j.otsr.2017.03.015. PMID: 28428035
Wilczynska M, Ching T
BMJ Case Rep 2011 Oct 11;2011 doi: 10.1136/bcr.08.2011.4667. PMID: 22675014Free PMC Article
Kanazawa H, Tanaka H, Inoue M, Yamanaka Y, Namba N, Seino Y
J Bone Miner Metab 2003;21(5):307-10. doi: 10.1007/s00774-003-0425-7. PMID: 12928832

Prognosis

Posey KL, Coustry F, Hecht JT
Matrix Biol 2018 Oct;71-72:161-173. Epub 2018 Mar 9 doi: 10.1016/j.matbio.2018.02.023. PMID: 29530484Free PMC Article
Oh KJ, Yoon JR, Yang JH
Knee 2013 Jan;20(1):45-8. Epub 2012 Nov 22 doi: 10.1016/j.knee.2012.10.012. PMID: 23177661
Posey KL, Hecht JT
Curr Drug Targets 2008 Oct;9(10):869-77. doi: 10.2174/138945008785909293. PMID: 18855621
Sasaki T, Yagi T, Monji J, Yasuda K, Kanno Y
J Pediatr Orthop 1986 Jan-Feb;6(1):61-5. PMID: 3941183
Stanescu V, Stanescu R, Maroteaux P
J Bone Joint Surg Am 1984 Jul;66(6):817-36. doi: 10.2106/00004623-198466060-00002. PMID: 6376516

Clinical prediction guides

Andrzejewski A, Péjin Z, Finidori G, Badina A, Glorion C, Wicart P
J Pediatr Orthop 2021 Feb 1;41(2):e135-e140. doi: 10.1097/BPO.0000000000001708. PMID: 33165262
Tariq M, Khan TN, Lundin L, Jameel M, Lönnerholm T, Baig SM, Dahl N, Klar J
Clin Genet 2018 Jan;93(1):182-186. Epub 2017 Nov 21 doi: 10.1111/cge.13091. PMID: 28685811
Posey KL, Veerisetty AC, Liu P, Wang HR, Poindexter BJ, Bick R, Alcorn JL, Hecht JT
Am J Pathol 2009 Oct;175(4):1555-63. Epub 2009 Sep 17 doi: 10.2353/ajpath.2009.090184. PMID: 19762713Free PMC Article
Hecht JT, Francomano CA, Briggs MD, Deere M, Conner B, Horton WA, Warman M, Cohn DH, Blanton SH
Genomics 1993 Dec;18(3):661-6. doi: 10.1016/s0888-7543(05)80370-2. PMID: 8307577
Stöss H, Pesch HJ, Spranger J
Prog Clin Biol Res 1982;104:379-83. PMID: 7163282

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...