Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Review
. 2013 Apr;43(4):454-9.
doi: 10.1007/s00247-012-2479-y. Epub 2012 Aug 29.

Imaging findings in megacystis-microcolon-intestinal hypoperistalsis syndrome

Marianne M Ballisty  1 , Kiery A Braithwaite, Bahig M Shehata, Paula N Dickson
Affiliations
Review

Imaging findings in megacystis-microcolon-intestinal hypoperistalsis syndrome

Marianne M Ballisty et al. Pediatr Radiol. 2013 Apr.

Abstract

Megacystis-microcolon-intestinal hypoperistalsis syndrome (MMIHS) is a rare and frequently lethal form of severe functional intestinal obstruction more commonly found in girls. Imaging features characteristic of this disease include a large dilated bladder, microcolon and intestinal dysmotility. Additional imaging findings may include intestinal malrotation, hydronephrosis and vesicoureteral reflux. It is usually fatal in the first year of life. Because presenting clinical and imaging features can mimic other causes of neonatal bowel obstruction, we compiled examples of this disorder to help the pediatric radiologist recognize imaging findings associated with MMIHS and aid in the development of a long-term management plan and in counseling the family regarding implications of this disorder. We reviewed recent and historical literature relevant to MMIHS and present the imaging and clinical features of four patients with MMIHS treated at our institution as examples of this uncommon disorder.

PubMed Disclaimer

Similar articles

See all similar articles

Cited by

References

    1. Urology. 2009 Sep;74(3):592-4 - PubMed
    1. Hum Pathol. 2008 Jun;39(6):970-4 - PubMed
    1. AJR Am J Roentgenol. 1976 May;126(5):957-64 - PubMed
    1. Radiology. 1980 Sep;136(3):649-50 - PubMed
    1. J Pediatr Surg. 2003 May;38(5):749-55 - PubMed

Supplementary concepts