The factors influencing visual development in blepharophimosis-ptosis-epicanthus inversus syndrome
- PMID: 17022162
- DOI: 10.3928/01913913-20060901-03
The factors influencing visual development in blepharophimosis-ptosis-epicanthus inversus syndrome
Abstract
Purpose: To investigate the factors influencing visual development in blepharophimosis-ptosis-epicanthus inversus syndrome.
Materials and methods: The study population comprised 20 patients with blepharophimosis-ptosis-epicanthus inversus syndrome who were referred for an oculoplastic opinion. The ocular examination included measurement of Snellen visual acuity, cycloplegic refraction, ocular movements and alignment, and the presence of amblyopia. Patients were treated with spectacle correction, occlusion therapy, strabismus surgery, and oculoplastic surgery if necessary. Minimum follow-up was 2 years.
Results: Nine (45%) patients had amblyopia; 5 (25%) of these patients had unilateral amblyopia and 4 (20%) had bilateral amblyopia. Six (67%) patients with amblyopia had a significant coexisting strabismus. A significant strabismus was present in 11 (55%) patients; 6 (55%) of these patients had unilateral or bilateral amblyopia. Patients with strabismus were more likely to have amblyopia than those without. A total of 14 (70%) patients had refractive error; 6 (43%) of these patients had amblyopia.
Conclusions: Patients with blepharophimosis-ptosis-epicanthus inversus syndrome had a high rate of amblyopia, especially bilateral amblyopia. Patients with strabismus were more likely to have amblyopia than those without. Patients also had a high incidence of refractive errors.
Similar articles
-
The incidence of strabismus and refractive error in patients with blepharophimosis, ptosis and epicanthus inversus syndrome (BPES).Strabismus. 2003 Sep;11(3):173-7. doi: 10.1076/stra.11.3.173.16645. Strabismus. 2003. PMID: 14710475
-
Clinical, radiologic, and genetic features in blepharophimosis, ptosis, and epicanthus inversus syndrome in the Indian population.Invest Ophthalmol Vis Sci. 2013 Apr 26;54(4):2985-91. doi: 10.1167/iovs.13-11794. Invest Ophthalmol Vis Sci. 2013. PMID: 23513057
-
Blepharophimosis: a recommendation for early surgery in patients with severe ptosis.Clin Exp Ophthalmol. 2003 Apr;31(2):138-42. doi: 10.1046/j.1442-9071.2003.00621.x. Clin Exp Ophthalmol. 2003. PMID: 12648048
-
Blepharophimosis-ptosis-epicanthus inversus syndrome (BPES).Acta Ophthalmol Scand. 1996 Feb;74(1):45-7. doi: 10.1111/j.1600-0420.1996.tb00680.x. Acta Ophthalmol Scand. 1996. PMID: 8689480 Review.
-
[Blepharophimosis, epicanthus inversus, and ptosis syndrome(BPES)].Ryoikibetsu Shokogun Shirizu. 2000;(30 Pt 5):274-6. Ryoikibetsu Shokogun Shirizu. 2000. PMID: 11057226 Review. Japanese. No abstract available.
Cited by
-
[Blepharophimosis syndrome: a special form of congenital ptosis].Pan Afr Med J. 2015 Mar 23;20:282. doi: 10.11604/pamj.2015.20.282.5584. eCollection 2015. Pan Afr Med J. 2015. PMID: 26161205 Free PMC article. French.
-
[Effectiveness of upper eyelid rotation flap via blepharoplasty incision for correction of mild to moderate epicanthus].Zhongguo Xiu Fu Chong Jian Wai Ke Za Zhi. 2019 Feb 15;33(2):203-206. doi: 10.7507/1002-1892.201805097. Zhongguo Xiu Fu Chong Jian Wai Ke Za Zhi. 2019. PMID: 30739416 Free PMC article. Chinese.
MeSH terms
LinkOut - more resources
Full Text Sources
Medical
