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Review
. 2000 Jun;120(3):399-405.
doi: 10.1046/j.1365-2249.2000.01142.x.

X-linked immunodeficiency with hyper-IgM (XHIM)

Affiliations
Review

X-linked immunodeficiency with hyper-IgM (XHIM)

L D Notarangelo et al. Clin Exp Immunol. 2000 Jun.
No abstract available

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Figures

Fig. 1
Fig. 1
Chest x-ray of 7 month XHIM boy presenting with Pneumocystis carinii pneumonia.
Fig. 2
Fig. 2
Distribution of mutations along the human CD40L gene in patients with XHIM (data from the CD40Lbase). Different types of mutations are identified by different symbols.
Fig. 3
Fig. 3
Trichrome stain of liver from CD154 knockout mouse after 3 months infection by Cryptosporidium parvum. Abnormalities include necrosis, fibrosis and acute or chronic cholangitis.

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