Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Review
. 1997 Apr;55(4):972-7.

[Creutzfeldt-Jakob disease(CJD) and Gerstmann-Sträussler-Scheinker syndrome(GSS)]

[Article in Japanese]
F Udaka  1 , M Fujisawa, M Kameyama
Affiliations
  • PMID: 9103904
Review

[Creutzfeldt-Jakob disease(CJD) and Gerstmann-Sträussler-Scheinker syndrome(GSS)]

[Article in Japanese]
F Udaka et al. Nihon Rinsho. 1997 Apr.

Abstract

Prion diseases are now a focus of attention since the diseases are known to disseminate beyond expectation. They are various types of Gerstmann-Sträussler-Scheinker syndrome(GSS), fatal familial insomnia, iatrogenic Creutzfeldt-Jakob disease(CJD), and variant CJD which suspected to have disseminated from bovine spongiform encephalopathy. Abnormal prion protein deposits as amyloid structure in the brain of the patients with these diseases. Mutation of the prion protein gene exists in a part of these diseases. Depending on their kind, patients represent a variety of clinical and neuropathological manifestations. They can be clinically divided into two general groups of the CJD type and the GSS type. For clinical diagnosis of the GSS type prion diseases, analysis of prion protein gene is useful.

PubMed Disclaimer

Similar articles

See all similar articles

LinkOut - more resources