The Middle-East connection of Wolman Disease
- PMID: 12070591
The Middle-East connection of Wolman Disease
Abstract
The clinical, laboratory and cytological features of 2 Bahraini infants with Wolman's disease are described. While one of the cases showed the classical diagnostic features, the other case exhibited a few atypical features such as lack of adrenal calcification and unusual morphology of vacuolated marrow macrophages. Literature review shows that this disorder may not be rare in this region.
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